Hemochromatosis: ICD 9M Code: 275.0 Hemochromatosis 1 .Excess Iron Overload In The Body: 2. Forms: A. Congenital B.

Acquired Iron Overload: C. Transfusions: eg: Sickle Cell Anemia Requiring Blood Transfusions D. Increased Oral Iron Intake: Bantu Siderosis E. Chronic Atransferrinemia F. Porphyria Cutanea Tarda G. Other Causes 3. Clinical Features: A. Hepatomegaly B. Diabetes Mellitus C. Bronze Pigmentation of the skin D. Late Cirrhosis 4. Death May Result From Cardiac Death Or Cirrhosis 5. Hereditary Hemochromatosis: A. Can be Diagnosed Long Before Irreversible Liver Damage Occurs Screening Involves: A. High Levels Of Serum Fe B. High Levels Of Serum transferring C. Exclusion Of Secondary Causes Of Iron Overload D. Liver Biopsy 6. The Natural Course Of Disease Can Be Altered By The Use Of 1. Phlebotomy 2. Iron Chelators: eg: Deferroxamine 7. Patients Diagnosed With Hereditary Hemochromatosis. Before The Precirrhotic Stage Can Have A Normal Life Expectancy