CIE-9 Códico Neuropediatrico

Codificacin en Neurologa Peditrica (CIE-9) Coding in Neuropediatrics (ICD-9)
Disponible en: www.neurologia.com/cie-9
Clasificacin por patologas Classification of disorders
Clasificacin alfabtica Alphabetical classification

A. Garca-Prez Grupo de Trabajo de Codificacin en Neurologa Peditrica
Codificacin en Neurologa Peditrica (CIE-9) Coding in Neuropediatrics (ICD-9)

Disponible en: www.neurologia.com/cie-9
Editorial Editorial Introduccin Introduction Clasificacin por patologas Classification of disorders 1. 2. Neurologa perinatal y fetal Fetal and perinatal neurology Malformaciones del sistema nervioso central. Malformaciones craneales. Hidrocefalia. Malformations of the central nervous system. Cranial malformations. Hydrocephalus Sndromes malformativos. Trastornos cromosmicos y genmicos. Malformative syndromes. Chromosomal and genomic disorders Sndromes neurocutneos. Neurocutaneous syndromes Parlisis cerebral. Ataxia. Trastornos del movimiento. Cerebral palsy. Ataxia. Movement disorders
5 7 19 21
22
3.
25
4. 5.
28 29
6.
Retrasos y trastornos del desarrollo, del aprendizaje y de la conducta. Developmental and behavioral disorders. Learning disabilities Epilepsia. Trastornos paroxsticos no epilpticos. Patologa del sueo. Epilepsy. Nonepileptic paroxysmal disorders. Sleep disorders. Cefaleas Headaches and related disorders Patologa infecciosa e inflamatoria Infectious and inflammatory disorders Patologa vascular Vascular disorders Patologa traumtica, txica y yatrognica. Coma Traumatic, toxic and iatrogenic disorders. Coma Patologa tumoral Tumour pathology
32
7.
35 39 40 42 43 47
8. 9. 10. 11. 12.I
12.II Clasificacin morfolgica de los tumores del sistema nervioso Morphology of nervous system neoplasms 13. Errores congnitos del metabolismo con repercusin neurolgica Inborn errors of metabolism with neurological repercussions
49
52
14. 15. 16. 17. 18. 19. 20. 21.
Enfermedades neurodegenerativas. Leucodistrofias Neurodegenerative diseases. Leukodystrophies Otoneurologa. Neurooftalmologa Otoneurology. Neuro-ophthalmology Patologa vertebral y de la mdula espinal Vertebral column and spinal cord disorders Enfermedades neuromusculares Neuromuscular diseases Otros Others Procedimientos diagnsticos Diagnostic procedures Procedimientos teraputicos Therapeutic procedures Motivos de consulta Reasons for medical consultation
55 56 60 62 66 67 71 74 81
Clasificacin alfabtica Alphabetical classification (Spanish)
Editorial
La codificacin en neurologa peditrica: un buen indicador de la calidad asistencial

Jaime Campos Castell
Servicio de Neurologa Peditrica. Hospital Clnico San Carlos. Madrid, Espaa
Cuando se han cumplido ya 40 aos del inicio de la actividad asistencial neurolgica en la edad infantil, podemos apreciar que se ha consolidado como una especialidad que, al margen de la discusin de su ubicacin sub, supra o quiz mejor paralela a sus ramas truncales madre neurolgicas y peditricas, posee un fin preciso cual es mejorar la calidad de vida de los pacientes afectados por procesos del sistema nervioso central y perifrico en esta etapa de la vida que cronolgicamente abarca desde la edad fetal hasta la adolescencia. En la actualidad podemos encontrar en toda Espaa unidades, secciones y servicios que cumplen de manera eficaz esta prctica clnica y, paralelamente, realizan una actividad cientfica refrendada por su participacin en reuniones nacionales e internacionales y la publicacin de sus trabajos en revistas de prestigio con su correspondiente factor de impacto y en libros que sirven de base para el aprendizaje de las nuevas generaciones. Un grupo de estos neurlogos peditricos, situados generacionalmente en promociones relativamente jvenes y an recientes, ha llevado a cabo un trabajo de codificacin basado en la CIE-9, lo que constituye un trabajo laudable, y me ha pedido un pequeo prlogo a este ejemplo claro del vigor, antes sealado, que la neurologa peditrica nos ofrece. Con orgullo de pertenecer a este grupo he aceptado ser su prologuista. Qu importancia tiene la codificacin para la prctica de nuestra especialidad?. Como seala el ttulo escogido, una adecuada codificacin de los procesos diagnsticos que manejamos en la prctica diaria no slo es un sistema de informacin homologable, sino que permite la comunicacin informatizada entre nosotros y con otros profesionales de la salud, al tiempo que constituye un indicador de la calidad asistencial [1,2] al permitir evaluar el porcentaje de diagnsticos y cdigos establecidos segn el sistema elegido, y de manera indirecta, aunque no menos importante, determina la toma de decisiones y acciones que permiten un adecuado sistema de gestin al potenciar las estrategias diagnsticas y teraputicas (GRD y costes de procesos). La codificacin de enfermedades supone bsicamente un proceso por el cual la informacin se convierte en smbolos para ser comunicada con la
Editorial La codificacin en neurologa peditrica: un buen indicador de la calidad asistencial
aplicacin de las reglas de un cdigo. Precisa, para que sea eficiente como base de datos, que los diagnsticos estn detallados como grupo general del cual pueden desprenderse otros subgrupos ms especficos; es importante que quede reflejada la etiologa si es conocida, y que permita solucionar el problema planteado al valorar procesos diagnsticos no determinados o poco precisos. La actual clasificacin CIE-9 (ICD-9-CM), no considera un gran nmero de procesos neuropeditricos de base bioqumica y/o gentica y muchas definiciones son inadecuadas, poco claras o incluso usan un lenguaje traducido poco actual. Otras especialidades de la pediatra tambin han sealado problemas en su uso prctico [3]. En algunos centros, hasta un 67% de diagnsticos no se codifican o se codifican incorrectamente, y de ellos el 37% se atribuye a los pediatras [4]. Por esto es encomiable el trabajo de este grupo de neuropediatras, dirigidos por la Dra. Asuncin Garca Prez, que desde hace aos viene presentando resultados preliminares y que a partir del VII Congreso de la Sociedad Espaola de Neurologa Peditrica (Murcia, 2006), junto con otros entusiastas voluntarios constituidos en grupo de trabajo, ofrecen hoy los resultados de su versin adaptada del CIE-9 en neurologa peditrica. Mi ms cordial enhorabuena a todos ellos, con mi gratitud.
Bibliografa
1. Mihovilovic C, Vallejos R. Codificacin de enfermedades: un indicativo de calidad. Rev Ped Elec [on line] 2005; 3: 11-24. 2. Pestana-Delgado R, Llanos-Zavalaga LF, Cabello-Morales E, Lecca-Garca L. Concordancia entre el diagnstico mdico y la codificacin de informtica, considerando el CIE-10, en la consulta externa de pediatra del Hospital Nacional Cayetano Heredia, Lima-Per. Rev Med Hered 2000; 4: 239-45. 3. Grupo de Trabajo de Codificacin Diagnstica de la Sociedad de Urgencias de Pediatra de la AEP. Codificacin diagnstica en urgencias de pediatra. An Esp Pediatr 2000; 3: 261-72. 4. Prins H, Bller H, Zwetsloot-Schonk B. Redesign of diagnostic coding in Pediatrics: from form-based to discharge letter linked. Perspect Health Inf Manag 2004; 1: 10.
Introduccin
Codificacin en neurologa peditrica basada en la CIE-9, 5. ed. (2006)

A. Garca-Prez a, M.A. Martnez-Granero a, A. Verd-Prez b, P. de Castro-de Castro c, C. Garzo c, M. Vzquez-Lpez c, A. Martnez-Bermejo d, R. Simn-de las Heras e, B. MartnezMenndez f, V. San Antonio-Arce g, T. de Santos-Moreno h, M.L. Carrasco-Marina i, M.R. Cazorla-Calleja j
a Fundacin Hospital Alcorcn. Madrid. b Hospital Virgen de la Salud. Toledo. c Hospital Gregorio Maran. Madrid. d Hospital La Paz. Madrid. e Hospital 12 de Octubre. Madrid. f Hospital Universitario de Getafe. Madrid. g Hospital Clnico San Carlos. Madrid. h Fundacin Jimnez Daz. i Hospital Severo Ochoa. Legans, Madrid. j Hospital de Fuenlabrada. Madrid.
Correspondencia: Neuropediatra: Dra Asuncin Garca Prez. Neuropediatra. Servicio de Pediatra. Fundacin Hospital Alcorcn. Madrid. agarcia@fhalcorcon.es E-mail: agarcia@fhalcorcon.es Agradecimientos. A J.A. Vaquero Mateo, de la Fundacin Hospital Alcorcn, Microsoft Office Specialist Master Instructor, por su contribucin a la digitalizacin de la codificacin en neurologa peditrica y la elaboracin de la base de datos.
Objetivo. Anlisis y adaptacin consensuada de la codificacin de la CIE-9, a los motivos de consulta, diagnsticos y procedimientos en neurologa peditrica. Materiales y mtodos. Se seleccionan los motivos de consulta, diagnsticos y procedimientos ms frecuentes en neuropediatra y se les asigna el cdigo ms apropiado de la CIE-9-MC (5. ed.) segn las normas de codificacin de dicho sistema. Se han agrupado las patologas por secciones, las cuales se han adjudicado a los distintos miembros del grupo de trabajo (13 neurlogos peditricos de 10 hospitales de Madrid capital y rea perifrica). Resultados. Se han asignado cdigos de la CIE-9-MC (5. ed.) a 158 motivos de consulta, 886 diagnsticos, 73 procedimientos diagnsticos y 53 procedimientos teraputicos. Siempre se ha intentado buscar el cdigo de la CIE-9 ms apropiado para los distintos diagnsticos. No se han inventado cdigos, aunque el grupo de trabajo se ha tomado algunas libertades de interpretacin que respetan la filosofa general de la CIE-9-CM y que se describen en el texto.
Introduccin Codificacin en neurologa peditrica basada en la CIE-9, 5. ed. (2006)
Conclusin. La creacin de esta adaptacin de la CIE-9 potenciar la codificacin diagnstica en los servicios de neurologa peditrica, dotndolos adems de una herramienta til para la elaboracin de bases de datos que permitan el anlisis retrospectivo de la informacin, y compartirla entre los distintos centros.
Introduccin
La codificacin surge como necesidad de poseer un lenguaje homologado que permita una comunicacin lo ms inequvoca posible entre profesionales de la salud. Facilita el tratamiento de la informacin clnica, la elaboracin de bases de datos, y posibilita as el estudiar, interpretar y compartir esta informacin. Adems, la poltica de calidad asistencial requiere la informatizacin de diagnsticos y procedimientos para facilitar la toma de decisiones a los gestores sanitarios (GRD y costes por procesos). En el VII Congreso de la Sociedad Espaola de Neurologa Peditrica (SENP, 2006) se constituy el grupo de trabajo (GT) de codificacin en neurologa peditrica basada en la CIE-9, con el acuerdo de la Junta Directiva, a propuesta de la Seccin de Neurologa Peditrica de la Fundacin Hospital Alcorcn y a partir de lo comunicado sobre el tema en la II Reunin Ibrica de Neuropediatra (2005). Los integrantes del GT han sido neurlogos peditricos de nueve hospitales de Madrid: Fundacin Hospital Alcorcn, Gregorio Maran, La Paz, 12 de Octubre, Hospital Clnico, Fundacin Jimnez Daz, Hospital de Legans, Hospital de Getafe, Hospital de Fuenlabrada, adems del Hospital Virgen de la Salud de Toledo. La CIE-9, versin en castellano del ICD-9-CM (International Classification of Diseases-9th revision-Clinical Modification), es el sistema de codificacin internacionalmente utilizado y aceptado por la comunidad cientfica internacional y las autoridades sanitarias. Tiene limitaciones en neurologa peditrica por: El gran nmero de diagnsticos actuales en neurologa peditrica con base bioqumica y gentica que la CIE no considera. La CIE utiliza una nomenclatura arcaica y traducciones inexactas. La CIE no se adecua a las clasificaciones diagnsticas recientes de la patologa neurolgica infantil. Por todo ello se ha considerado til e importante que el colectivo de neurlogos peditricos perfilase los cdigos de la CIE-9 correspondientes a los diagnsticos y procedimientos que se manejan actualmente, asegurando y facilitando as su asignacin. Se presenta la sistemtica seguida por el GT y los cdigos elegidos con la descripcin diagnstica o de procedimiento a los que se asignan.
Materiales y mtodos
Se recogen los diagnsticos y procedimientos ms frecuentes en neurologa peditrica y se les asigna el cdigo ms apropiado de la CIE-9 (5. ed.). Para ello se han agrupado las patologas por secciones, y las diferentes secciones se han adjudicado a los distintos miembros del GT (13 neuropediatras de 10 hospitales de Madrid capital y zona perifrica). Se han codificado tambin los motivos de consulta, por el inters de conocer la patologa que nos es referida (valor clnico, asignacin de recursos), y los procedimientos diagnsticos y teraputicos, dada la importancia que stos pueden tener en los costes por proceso, adems de lo tiles que pueden resultar a efectos de estudios epidemiolgicos. Se solicit la colaboracin de los servicios de documentacin de los diferentes hospitales. Los cdigos elegidos se sometieron a consenso del GT y finalmente el coordinador del grupo revis y elimin los diagnsticos duplicados en distintas secciones y modific mnimamente alguna descripcin diagnstica con objeto de utilizar una nomenclatura ms actualizada. Las secciones consideradas han sido: 1. Neurologa perinatal y fetal. 2. Malformaciones del sistema nervioso central. Malformaciones craneales. Hidrocefalia. 3. Sndromes malformativos. Trastornos cromosmicos y genmicos. 4. Sndromes neurocutneos. 5. Parlisis cerebral. Ataxia. Trastornos del movimiento. 6. Retrasos y trastornos del desarrollo, del aprendizaje y de la conducta. 7. Epilepsia. Trastornos paroxsticos no epilpticos. Patologa del sueo. 8. Cefaleas. 9. Patologa infecciosa e inflamatoria. 10. Patologa vascular. 11. Patologa traumtica, txica y yatrognica. Coma. 12.I. Patologa tumoral 12.II. Clasificacin morfolgica de los tumores del sistema nervioso. 13. Errores congnitos del metabolismo con repercusin neurolgica. 14. Enfermedades neurodegenerativas. Leucodistrofias. 15. Otoneurologa. Neurooftalmologa. 16. Patologa vertebral y de la mdula espinal. 17. Enfermedades neuromusculares. 18. Otros. 19. Procedimientos diagnsticos. 20. Procedimientos teraputicos. 21. Motivos de consulta.
En estas secciones se han recogido los diagnsticos neurolgicos infantiles segn las clasificaciones o propuestas de clasificacin actuales, por ejemplo: International Classification of Headache Disorders (2. ed., 2004), Report of the ILAE Task Force on Classification and Terminology (Engel J. Epilepsia 2001), y Vademecum Metabolicum (Zschocke/Hoffmann, 2001). La estructura de los cdigos de la CIE-9-MC es de tres dgitos para el rango de categora, cuatro dgitos para el de subcategora, y cinco dgitos para el rango de subclasificacin. Por ejemplo: 345, epilepsia parcial; 345.4, epilepsia parcialcon deterioro de conocimiento; 345.40, epilepsia parcialcon deterioro de conocimiento con epilepsia tratable. Siempre se ha intentado buscar el cdigo donde mejor encajasen los distintos diagnsticos. El GT no ha inventado cdigos, aunque se ha tomado algunas libertades que respetan la filosofa general de la CIE-9-CM: Los cuartos dgitos 8, correspondientes a otras patologas especficas de esa categora que no tienen entrada directa, y .9, que la CIE asigna a patologa de esa categora sin especificar, se han utilizado para patologas sin otros posibles cdigos o entradas directas. Se han respetado las entradas directas de la CIE-9 para algunos diagnsticos, aunque encajasen mejor en otras subcategoras que acogan patologas similares, o bien cuando en las nuevas clasificaciones etiolgicas ocuparan otras categoras. Por ejemplo: 759.8, entrada directa para Prader-Willi, y 758.33, para Angelman (delecin 15q1113) correspondiente a otras deleciones autosmicas. Ambas deberan tener la misma categora o subcategora, pero se ha respetado la CIE y asignado el cdigo que mejor encuadrara a la patologa que no tena entrada directa en la CIE. Cuando se dispona de pocos cdigos para adjudicar a amplias clasificaciones diagnsticas, se han intentado agrupar los diagnsticos bajo algn cdigo prximo (por ejemplo: 345.0 para ausencias, ausencias infantiles, ausencias mioclnicas, ausencias juveniles). Adems, se han utilizado el cuarto o quinto dgitos con sentido diferente y ms actualizado, ya que a veces las subcategoras y subclasificaciones de la CIE no tenan sentido alguno. Por ejemplo, de la CIE-9, 4. dgito: 345.4, epilepsia parcial con deterioro de conocimiento; 345.5, epilepsia parcial sin mencin a perdida conciencia. El CIE-9 5. dgito se usa en estas subcategoras para: 0, sin mencin de epilepsia no tratable; 1, con epilepsia no tratable. Se ha adaptado de la siguiente manera: a) 345.40 para epilepsia parcial sintomtica y 345.41 para epilepsia parcial criptognica, b) 345.50 para epilepsia parcial idioptica y 345.51 para epilepsia parcial familiar. Cuando no se ha encontrado una entrada directa para un diagnstico interesante, se le ha adjudicado algn cdigo disponible que estuviera
10
relacionado. Por ejemplo: 784.0, cefalea secundaria correspondiente en la CIE-9 a cefalea. Se supone que al codificar este diagnstico se aadirn otros cdigos correspondientes al origen de la cefalea, como neoplasia maligna cerebelo. Adems, en el caso de patologa tumoral habra que codificar por la localizacin tumoral y por el tipo histolgico. Se ha utilizado la barra / para mayor especificacin: 771.89 / 052, infeccin congnita / por varicela. Los distintos diagnsticos slo estn contemplados en una nica seccin de patologas aunque pudieran pertenecer a varias. La versin digitalizada en Excel de esta codificacin permite hacer la bsqueda rpida del diagnstico introduciendo aproximaciones al descriptor. Se ha tenido en cuenta a la hora de asignar cdigos que stos son la base de la gestin de los GRD (grupos relacionados por diagnstico), que asocian a los cdigos el consumo de recursos (costes), de manera que la adaptacin realizada nunca supusiera una modificacin sustancial de los pesos especficos y costes por proceso. Se ha introducido, adems del cdigo CIE-9, un cdigo de especificacin para individualizar diagnsticos diferentes que compartan un mismo cdigo CIE-9. De esta manera, respetando el cdigo CIE-9 se han separado para nuestro uso personal las diferentes patologas, y as poder manejarlas ms fcilmente. Este cdigo de especificacin es alfanumrico: S/E (sin especificacin) o bien del 01 al 99, y est asignado por orden alfabtico a los diagnsticos que compartan el mismo cdigo CIE-9. La seccin Otros contiene diagnsticos que no se han podido incluir en otras secciones, como normalidad neurolgica, nio adoptado, circunstancias psicosociales adversas Finalmente, se han revisado los cdigos finales y se han comparado con los que maneja el sistema SIERE (Sistema de Informacin sobre Enfermedades Raras en Espaol) para comprobar que encajasen.
Resultados
Se han asignado cdigos de la CIE-9-MC (5. ed.) a 158 motivos de consulta, 886 diagnsticos, 73 procedimientos diagnsticos y 53 procedimientos teraputicos. Todos ellos se exponen a continuacin en diferentes tablas.
Cmo codificar
La CIE-9-MC recomienda escoger el cdigo diagnstico ms concreto y con mayor nmero de dgitos posibles:
11
Escoger inicialmente una de las secciones diagnsticas que aparecen en el listado y buscar el diagnstico en l. En caso de no hallarlo, buscarlo en las otras secciones que tambin pudieran acogerlo. Los diagnsticos slo estn contemplados en una nica seccin de patologas, aunque pudieran pertenecer a varias. La versin digitalizada en Excel de esta codificacin permite hacer la bsqueda rpida del diagnstico introduciendo en el buscador una aproximacin al descriptor. Si no es posible un diagnstico concreto, ir a uno ms genrico. Al diagnstico inicial se pueden aadir otros diagnsticos que describan mejor y de forma ms completa el cuadro (por ejemplo, cefalea secundaria y neoplasia maligna cerebelo e hidrocefalia obstructiva). Cuanto mejor codificado est cada caso, mayor informacin disponible para manejar. Se puede codificar por un lado el motivo de consulta, y por otro, el diagnstico final, los cuales pueden coincidir en ocasiones. Tambin se puede codificar los procedimientos diagnsticos y teraputicos, dada la importancia que stos pueden tener en los costes por proceso, adems de lo tiles que pueden resultar a efectos de estudios epidemiolgicos.
Conclusiones
Esta adaptacin de la CIE-9 facilitar y potenciar la codificacin diagnstica en los servicios de neurologa peditrica. Permite adems una codificacin consistente y uniforme de los diagnsticos neuropeditricos con un sistema internacionalmente aceptado. Es una herramienta til para la gestin y la investigacin epidemiolgica y clnica en los servicios de neurologa peditrica y facilita la elaboracin de bases de datos con criterios comunes que permitan, analizar y compartir la informacin, y realizar estudios multicntricos epidemiolgicos, clnicos, teraputicos, etc.
Bibliografa
1. Grupo de Trabajo de Codificacin Diagnstica de la Sociedad de Urgencias de Pediatra de la Asociacin Espaola de Pediatra. Codificacin diagnstica en urgencias de pediatra. An Esp Pediatr 2000; 53: 261-72. 2. Clasificacin Internacional de Enfermedades. 9. revisin. Modificacin clnica. CIE-9. MC. 5. ed. Madrid: Ministerio de Sanidad y Consumo; 2006.
12
Introduction
Coding in Neuropediatrics based on the ICD-9, 5th ed. (2006)

A. Garca-Prez a, M.A. Martnez-Granero a, A. Verd-Prez b, P. de Castro-de Castro c, C. Garzo c, M. Vzquez-Lpez c, A. Martnez-Bermejo d, R. Simn-de las Heras e, B. MartnezMenndez f, V. San Antonio-Arce g, T. de Santos-Moreno h, M.L. Carrasco-Marina i, M.R. Cazorla-Calleja j
a Fundacin Hospital Alcorcn. Madrid. b Hospital Virgen de la Salud. Toledo. c Hospital Gregorio Maran. Madrid. d Hospital La Paz. Madrid. e Hospital 12 de Octubre. Madrid. f Hospital Universitario de Getafe. Madrid. g Hospital Clnico San Carlos. Madrid. h Fundacin Jimnez Daz. i Hospital Severo Ochoa. Legans, Madrid. j Hospital de Fuenlabrada. Madrid.
Corresponding author: Neuropediatrics Unit: Dra Asuncin Garca Prez. Neuropediatra. Servicio de Pediatra. Fundacin Hospital Alcorcn. Madrid. agarcia@fhalcorcon.es E-mail: agarcia@fhalcorcon.es Acknowledgement. To J.A. Vaquero Mateo of the Fundacin Hospital Alcorcn, Microsoft Office Specialist Master Instructor, for his contribution to the database development process.
Aim. To analyze ICD-9 coding and adapt it, on a consensus basis, to reasons for medical consultation, diagnoses and procedures in child neurology. Materials and methods. The most frequent reasons for medical consultation, diagnoses and procedures in neuropediatrics were selected and assigned the most appropriate International Classification of Diseases, 9th Revision, Clinical Modification (5th ed.) (ICD-9-CM) codes in accordance with this systems coding rules. Disorders were grouped by sections, and allocated to the various members of the working group (13 child neurologists from 10 hospitals in Madrid and environs). Results. ICD-9-CM codes were assigned to: 158 reasons for medical consultation; 886 diagnoses; 73 diagnostic procedures; and 53 therapeutic procedures. In every case, the most appropriate ICD-9 code was sought for the respective diagnosis. No codes were invented but the working group did take certain liberties with interpretation, which nevertheless showed respect for general ICD-9-CM philosophy and are described in full in the text.
13
Introduction Coding in Neuropediatrics based on the ICD-9, 5th ed. (2006)
Conclusion. The creation of this ICD-9 adaptation will not only enhance diagnostic coding in child neurology departments, but will also provide them with a useful tool for setting up databases to enable information to be retrospectively analyzed and shared by the different health centers.
Introduction
Coding arises in response to the need for a standardized language that will allow for the most unequivocal communication possible among health professionals. It facilitates the handling and management of clinical information and the setting-up of databases, which will in turn enable such information to be studied, interpreted and shared. Furthermore, health-care quality policy renders it essential for diagnoses and procedures to be computerized so as to simplify decision-making by health administrators (diagnostic related groups and costs per procedure). At the 7th Congress of the Spanish Child Neurology Society Sociedad Espaola de Neurologa Peditrica (SENP) 2006, the Board of Governors consented to a working group (WG) being set up to code child neurology on the basis of the ICD-9, following a proposal to this effect tabled by the Child Neurology Department of the Alcorcn Foundation Hospital and a communication on the topic delivered at the 2nd Iberian Neuropediatrics Meeting Reunin Ibrica de Neuropediatra (2005). The WG members were child neurologists drawn from 9 hospitals in Madrid, namely, the Alcorcn Foundation, Gregorio Maran, La Paz, 12 de Octubre, Clinical, Jimnez Diaz Foundation, Legans, Getafe and Fuenlabrada Hospitals, plus the Virgen de la Salud Hospital in Toledo. The ICD-9, the Spanish version of the International Classification of Diseases, 9th Revision, Clinical Modification (5th ed.) (ICD-9-CM), is the internationally used coding system accepted by the international scientific community and health authorities. Insofar as child neurology is concerned, this classification has limitations because: A great number of currently used biochemical and genetic-based child neurology diagnoses are not envisaged by the ICD. The ICD relies on archaic nomenclature and inaccurate translations. The ICD makes no provision for recent diagnostic classifications of child neurological disorders. As a consequence, it was judged both useful and important for the child-neurologist fraternity to identify ICD-9 codes that corresponded to diagnoses and procedures currently in use, and ensure that these could be duly assigned. This paper outlines the systematic approach followed by the WG, as well as the codes selected for allocation to the respective diagnostic descriptions or procedures.
14
Materials and methods

The most frequent diagnoses and procedures in child neurology were compiled and the most appropriate ICD-9 code assigned to each. To this end, disorders were grouped by section, and the different sections were then allocated to the various members of the WG (13 child neurologists from 10 hospitals in Madrid and environs). We also coded: Reasons for medical consultation, in view of the interest attached to knowing the disorder which is referred to us (clinical value, allocation of resources, etc.); and Diagnostic and therapeutic procedures, in view of the importance that these can have for costs per procedure, and their potential usefulness for epidemiological study purposes. The collaboration of the records departments of the respective hospitals was sought. Codes were chosen subject to agreement by the WG, and the coordinating group then reviewed and eliminated any diagnoses that were duplicated in the different sections and minimally amended some diagnostic descriptions in order to incorporate terminology that was more up-to-date. The sections considered were: 1. Fetal and perinatal neurology. 2. Malformations of the central nervous system. Cranial malformations. Hydrocephalus. 3. Malformative syndromes. Chromosomal and genomic disorders. 4. Neurocutaneous syndromes. 5. Cerebral palsy. Ataxia. Movement disorders. 6. Developmental and behavioral disorders. Learning disabilities. 7. Epilepsy. Nonepileptic paroxysmal disorders. Sleep disorders. 8. Headaches and related disorders. 9. Infectious and inflammatory disorders. 10. Vascular disorders. 11. Traumatic, toxic and iatrogenic disorders. Coma. 12.I. Tumour pathology 12.II. Morphology of nervous system neoplasms. 13. Inborn errors of metabolism with neurological repercussions. 14. Neurodegenerative diseases. Leukodystrophies. 15. Otoneurology. Neuro-ophthalmology. 16. Vertebral column and spinal cord disorders. 17. Neuromuscular diseases. 18. Others. 19. Diagnostic procedures. 20. Therapeutic procedures. 21. Reasons for medical consultation.
15
In the above sections, child neurological diagnoses were listed in line with current or proposed classifications, such as The International Classification of Headache Disorders (2nd ed., 2004), Report of the ILAE Task Force on Classification and Terminology (Engel J. Epilepsia 2001), and Vademecum Metabolicum (Zschocke/ Hoffmann, 2001). The ICD-9-CM code structure consists of a 3-digit rubric for category, a 4-digit rubric for subcategory, and a 5-digit rubric for subclassification, e.g.: 345, partial epilepsy; 345.4, partial epilepsy, with impairment of consciousness; and 345.40, partial epilepsy, with impairment of consciousness, without intractable epilepsy. In all cases, an effort was made to find the code that provided the best fit for the respective diagnoses. No codes were invented by the WG, but it did take certain liberties which nevertheless showed respect for general ICD-9-CM philosophy: The fourth digits, .8 corresponding to other specified disorders belonging to this category which have no direct entry, and .9, which the ICD assigns to unspecified disorder belonging to this category, were used for disorders having no other possible codes or direct index entries. Direct ICD-9 entries for some diagnoses were respected, even though they would have fitted better into other subcategories which covered similar disorders, or would have come under other categories in the new etiological classifications, e.g., 759.81 direct ICD-9 entry for Prader-Willi syndrome, and for Angelman syndrome (deletion 15q11-13) 758.33, corresponding to other autosomal deletions. While both should rightly have the same category or subcategory, the ICD was nevertheless respected and the code assigned that best covered the disorder which had no direct entry in the ICD. In cases where there were few codes to assign to wide-ranging diagnostic classifications, we endeavored to group the diagnoses under some closely related code (e.g., 345.0 for absences, childhood absences, myoclonic absences and juvenile absences). Furthermore, the 4th or 5th digit was used with a different and more current meaning, since at times the ICD subcategories and subclassifications make no sense whatsoever, e.g. ICD-9 4th digit: 345.4, partial epilepsy with impairment of consciousness; 345.5, partial epilepsy without mention of impairment of consciousness. The ICD-9 5th digit subclassification is used in these subcategories for: 0, without mention of intractable epilepsy; 1, with intractable epilepsy. This was adapted as follows: i) 345.40 for partial symptomatic epilepsy and 345.41 for partial cryptogenic epilepsy; and ii) 345.50 for partial idiopathic epilepsy and 345.51 for partial familial epilepsy In cases where no direct entry could be found for an interesting diagnosis, this was assigned an available code that was in some way related, e.g., 784.0 secondary headache corresponding in the ICD-9 to headache. It is to be
16
assumed that, when such a diagnosis is coded, other codes relating to the origin of the headache, e.g., malignant neoplasm of cerebellum would be added. Furthermore, in the case of tumour pathology, coding by tumour site and histological type would be required. A forward slash (/) was used for more detailed specification, e.g., 771.89 / 052, congenital infection / due to varicella. Different diagnoses are shown under only one disorder section despite the fact that they might pertain to several such sections. The digitized Excel version of this coding enables users to make a quick search of diagnoses, by entering broad search terms and synonyms of the descriptor. When it came to allocating codes, account was taken of the fact that these form the basis for managing the diagnostic related groups (DRG) which link codes to use of resources (costs). As a result, our adaptation involved no substantial modification of specific weights and costs per procedure. Apart from the ICD-9 code, a specification code was introduced in order to individualize different diagnoses which shared the same ICD-9 code. While ensuring that the ICD-9 code was respected in all cases, the different disorders were thus separated for our personal use and rendered easier to handle. This specification code which is alphanumerical, N/S (not specified), or numbered from 01 to 99 was assigned to diagnoses sharing the same ICD-9 code in alphabetical order. The section entitled Others contains a few diagnostic codes which may not be easily included in any of the other sections, i.e.: neurologically normal child, adverse social and environmental situations, adopted child, etc. Lastly, the final codes were reviewed and compared against those used by the Spanish Rare Disease Information System Sistema de Informacin sobre Enfermedades Raras en Espaol (SIERE) to check that they indeed fit.
Results
ICD-9-CM codes were allocated to: 158 reasons for medical consultation; 886 diagnoses; 73 diagnostic procedures; and 53 therapeutic procedures. All are listed below in tables.
How to code
The ICD-9-CM recommends choosing the most specific diagnostic code, with the greatest number of digits possible: Initially, choose one of the diagnostic sections that appear on the list, and
17
Introduccin Coding in Neuropediatrics based on the ICD-9, 5th ed. (2006)
search for the diagnosis. In the event of not finding it, search through other sections that could also cover it. Diagnoses are shown under only one disorder section despite the fact that they might pertain to several such sections The digitized Excel version of this coding enables users to make a quick diagnostic search, by entering a term similar to or synonymous with the descriptor into the search engine. If a specific diagnosis is not possible, proceed to a more generic diagnosis. Other diagnoses that better describe the clinical profile (e.g., secondary headache and malignant neoplasm of cerebellum and obstructive hydrocephalus) can be added to the initial diagnosis. The better a case is coded, the more information becomes available for its management. One can code the reason for consultation on the one hand, and the final diagnosis on the other: these may sometimes coincide. Diagnostic and therapeutic procedures can likewise be coded, in view of the importance that these can have vis--vis costs per procedure, and their potential usefulness for epidemiological study purposes.
Conclusions
This adaptation of the ICD-9 will facilitate and enhance diagnostic coding in child neurology departments. Moreover, it allows for consistent, standardized coding of child neurological diagnoses based on an internationally accepted system. It is a useful tool for epidemiological and clinical management and research in child neurology departments, and enables databases with common criteria to be set up, something that will in turn make it possible for information to be analyzed and shared, and epidemiological, clinical and therapeutic multicentre studies to be conducted.
References
1. Grupo de Trabajo de Codificacin Diagnstica de la Sociedad de Urgencias de Pediatra de la Asociacin Espaola de Pediatra. Codificacin diagnstica en urgencias de pediatra. An Esp Pediatr 2000; 53: 261-72. 2. Clasificacin Internacional de Enfermedades. 9. revisin. Modificacin clnica. CIE-9. MC. 5. ed. Madrid: Ministerio de Sanidad y Consumo; 2006.
18
Clasificacin por patologas Classification of disorders
1. Neurologa fetal y perinatal 1. Fetal and perinatal neurology
CIE-9/ ICD-9 243 763.5 763.9 764.9 765.0 765.1 766.1 766.22 767.0 767.0 767.1 767.2 767.3 767.4 767.5 767.6 767.7 767.9 768.4 768.5 768.9 770.81 771.0
CE/ SC S/E S/E S/E S/E S/E S/E S/E S/E 01 02 S/E S/E S/E S/E S/E S/E S/E S/E S/E S/E S/E S/E S/E
Diagnstico
Diagnose
Hipotiroidismo neonatal Efecto de la analgesia y anestesia maternas sobre el feto/RN
Congenital hypothyroidism Maternal anesthesia and analgesia affecting fetus or newborn
Afectacin del RN por complicaciones parto Complication of labour and delivery affecting fetus or newborn Crecimiento intrauterino retardado Inmaduridad extrema, gran prematuro Prematuridad (otra) Fetal growth retardation Immature or extremely premature Preterm (other)
Recin nacido de peso elevado para la edad Exceptionally large baby relating to long gestacional gestation Postmadurez Hemorragia cerebral al nacimiento Hemorragia subdural al nacimiento Traumatismo del cuero cabelludo en el nacimiento Fractura de clavcula al nacimiento Traumatismo del esqueleto en el nacimiento (otros) Traumatismo de la columna vertebral y de la mdula espinal en el nacimiento Traumatismo del plexo braquial al nacimiento Traumatismos de pares craneales y nervios perifricos al nacimiento (otros) Traumatismo obsttrico al nacimiento Prolonged gestation of infant Cerebral hemorrhage due to birth trauma Subdural hemorrhage due to birth trauma Scalp injury due to birth trauma Fracture of clavicle due to birth trauma Other injuries to skeleton due to birth trauma Spine and spinal cord injury due to birth trauma Brachial plexus injury due to birth trauma Other cranial and peripheral nerve injuries due to birth trauma Other birth trauma
Traumatismo del nervio facial al nacimiento Facial nerve injury due to birth trauma
Sufrimiento fetal, prdida de bienestar fetal Fetal distress, loss of fetal well-being Asfixia grave al nacer (con repercusin neurolgica). EHI Asfixia al nacer Apnea del neonato Rubola congnita Birth asphyxia with neurological impact. Hypoxic-ischemic encephalopathy Birth asphyxia Apnea of newborn Congenital rubella infection
21
1. Neurologa fetal y perinatal 1. Fetal and perinatal neurology
CIE-9/ ICD-9 771.1 771.2
CE/ SC S/E S/E
Diagnstico
Diagnose
Citomegalovirus congnito Infeccin congnita (incluye toxoplasmosis congnita) Varicela congnita Ttanos neonatal VIH de transmisin vertical Transfusin fetomaterna o fetofetal
Congenital cytomegalovirus infection Other congenital infections specific to the perinatal period including congenital toxoplasmosis Congenital chickenpox Tetanus neonatorum Human immunodeficiency virus infection (HIV), vertical transmission Feto-fetal or fetal-maternal transfusion syndrome
771.2/052 S/E 771.3 771.89/ 042 772.0 772.1 772.2 772.9 774.7 775.2 S/E S/E S/E S/E S/E S/E S/E S/E
Hemorragia intraventricular fetal y neonatal Intraventricular hemorrhage of fetus or perinatal newborn Hemorragia subaracnoidea perinatal Hemorragia fetal y neonatal sin especificacin Kernicterus Miastenia grave neonatal (transitoria neonatal, asociada a alteraciones autoinmunes) Tirotoxicosis neonatal Hipocalcemia e hipomagnesemia del recin nacido Hipoglucemia neonatal Excitabilidad neuromuscular del RN y lactante Depresin neurolgica neonatal Efecto sobre el feto o RN de la administracin materna de frmacos Sndrome de abstinencia a drogas Leucomalacia periventricular Hipotona central neonatal Subarachnoid hemorrhage of newborn Unspecified hemorrhage of newborn Kernicterus of fetus or newborn (any etiology) Neonatal myasthenia gravis (transient and autoimmune caused) Neonatal thyrotoxicosis Hypocalcemia, hypomagnesemia of newborn Neonatal hypoglycemia Neurological irritability in newborn Cerebral depression in fetus or newborn Maternal drug reactions and intoxications specific to newborn Drug withdrawal syndrome in newborn Periventricular leukomalacia Central hypotonia present in the perinatal period
775.3 775.4 775.6 779.1 779.2 779.4 779.5 779.7 779.89
S/E S/E S/E S/E S/E S/E S/E S/E S/E
22
2. Malformaciones del SNC. Malformaciones craneales. Hidrocefalia 2. Malformations of CNS. Cranial malformations. Hydrocephalus
CIE-9/ ICD-9 278.2 331.3 331.4 348.0 348.0 740.0 740.1 742.0 742.1 742.2 742.2 742.2 742.2 742.2 742.2 742.2 742.2 742.2 742.2 742.3 742.4 742.4 742.4 742.4 742.8 754.0
CE/ SC S/E S/E S/E 01 02 S/E S/E S/E S/E 01 02 03 04 05 06 07 08 09 10 S/E 01 02 03 05 S/E 01
Diagnstico
Diagnose
Hipervitaminosis A Hidrocefalia comunicante Hidrocefalia obstructiva (no comunicante) Quistes cerebrales Quiste porenceflico (adquirido) Anencfalo Craneorraquisquisis Encefalocele Microcefalia Agenesia del cuerpo calloso Displasias o hipoplasias o agenesias de parte del cerebro Displasia septoptica Esquisencefalia Hemimegalencefalia Heterotopias Hipoplasia cerebelosa Holoprosencefalia Lisencefalia Microgirias Hidrocefalia congnita Atrofia cerebral Hidranencefalia Porencefalia (congnita o verdadera) Anomalas cerebrales (otras) Hidrocefalia externa, higroma cerebral o aumento de espacios subaracnoideos Asimetra craneal (facial) o plagiocefalia postural
Hypervitaminosis (vitamin A) Communicating hydrocephalus Obstructive hydrocephalus (noncommunicating) Cerebral cysts Porencephalic cyst (acquired) Anencephalus Craniorrachischisis Encephalocele Microcephaly Callosal agenesis Dysplasia or hypoplasia or agenesis of part of brain Septo-optic dysplasia Schizencephaly Hemimegalencephaly Neuronal heterotopias Cerebellar hypoplasia Holoprosencephaly Lissencephaly Microgyria Congenital hydrocephalus Cerebral atrophy Hydranencephaly Porencephaly (congenital) Anomalies of brain (others) External hydrocephalus, cerebral hygroma or enlargement subarachnoid spaces Asymmetry of face or postural plagiocephaly
23
2. Malformaciones del SNC. Malformaciones craneales. Hidrocefalia 2. Malformations of CNS. Cranial malformations. Hydrocephalus
CIE-9/ ICD-9 754.0 754.1 756.0 756.0 756.0 756.0
CE/ SC 02 S/E 01 02 03 04
Diagnstico
Diagnose
Dolicocefalia Tortcolis congnita Craneosinstosis Crouzon Macrocefalia Malformacin craneofacial
Dolichocephaly Congenital torticollis Craniosynostosis Crouzon syndrome Macrocephaly Craniofacial malformation
24
3. Sndromes malformativos. Trastornos cromosmicos y genmicos 3. Malformative syndromes. Chromosomal and genomic disorders
CIE-9/ ICD-9 253.0 270.8 279.11 755.52 755.55 755.59 755.59 756.0 756.0 756.2 756.4 756.5 756.83 756.89 756.89 758.0 758.1 758.2 758.3 758.31 758.32 758.33 758.33 758.33
CE/ SC S/E 05 S/E S/E S/E 01 02 05 06 S/E 01 S/E S/E 01 02 S/E S/E S/E S/E S/E S/E 01 02 03
Diagnstico
Diagnose
Gigantismo, sndrome de hipercrecimiento (Sotos, Weaver...) Lowe DiGeorge Sprengel. Elevacin congnita de la escpula Apert o acrocefalosindactilia Anomalas congnitas del miembro superior (otras) Disstosis cleidocraneal Hallerman-Streiff Treacher-Collins Costilla cervical Acondroplasia y otras condrodistrofias Displasia sea con afectacin neurolgica Ehlers-Danlos Acortamiento congnito de tendn Amiotrofia congnita Down: trisoma 21 Patau: trisoma 13 Edwards: trisoma 18
Gigantism, overgrowth syndromes (Sotos, Weaver, etc.) Lowe syndrome DiGeorge syndrome Sprengel malformation (congenital elevation of scapula) Apert syndrome, acrocephalosyndactyly Congenital anomalies of upper limb (any type) Cleidocranial dysostosis Hallerman-Streiff syndrome Treacher-Collins syndrome Cervical rib Achondroplasia and other chondrodystrophies Skeletal dysplasia with neurological manifestations Ehlers-Danlos syndrome Congenital shortening of tendon Amyotrophia congenita Down syndrome, trisomy 21 Patau syndrome, trisomy 13 Edwards syndrome, trisomy 18
Sndromes por delecin autosmica, Autosomal deletion syndromes, microdeleciones, deleciones subtelomricas microdeletions, subtelomeric deletions Cri du Chat: delecin 5p Velocardiofacial: delecin 22q11.2 Angelman: delecin 15q11-q13 materna Microdeleciones (otras) Miller-Dieker: delecin 17p13.3 Cri du Chat syndrome, deletion 5p Velo-cardio-facial syndrome, deletion 22q11.2 Angelman syndrome, deletion 15q11-q13 maternal Microdeletions (others) Miller-Dieker syndrome, deletion 17p13.3
25
CIE-9/ ICD-9 758.33 758.33 758.39 758.39 758.4 758.5
CE/ SC 04 05 01 02 S/E S/E
Diagnstico
Diagnose
Smith-Magenis: delecin 17p11.2 Williams: delecin: 7q11.23 Delecin 18p/q Deleciones autosmicas (otras) Traslocacin autosmica balanceada en individuo normal Cromosomopatas autosmicas numricas, estructurales o monognicas (cromosoma 20 anillo, trisoma 9...) Turner Klinefelter
Smith-Magenis syndrome, deletion 17p11.2 Williams syndrome, deletion 7q11.23 Deletion 18p/q Autosomal deletions (others) Balanced autosomal translocation in normal individual Autosomic chromosomopaties: numeric, structural or monogenic (ring chromosome 20, trisomy 9...) Turner syndrome Klinefelter syndrome
758.6 758.7 758.81 759.81 759.82 759.83 759.89 759.89 759.89 759.89 759.89 759.89 759.89 759.89 759.89 759.89 759.89 759.89 759.89
S/E S/E S/E S/N S/E S/E 01 02 03 04 05 06 07 08 09 10 11 12 13
Cromosomopatas gonosmicas, numricas, Gonosomic chromosomopaties: numeric, estructurales o monognicas (otras) structurals or monogenics (others) Prader-Willi Marfan X frgil CHARGE Cockayne Coffin-Lowry Cohen Cornelia de Lange Dubowitz Freeman-Sheldon Gorlin Johanson-Blizard Kabuki Laurence-Moon-Biedl Marshall-Smith MASA Prader-Willi syndrome Marfan syndrome Fragile X syndrome CHARGE association Cockayne syndrome Coffin-Lowry syndrome Cohen syndrome Cornelia de Lange syndrome Dubowitz syndrome Freeman-Sheldon syndrome Gorlin syndrome Johanson-Blizard syndrome Kabuki syndrome Laurence-Moon-Biedl syndrome Marshall-Smith syndrome MASA syndrome
26
CIE-9/ ICD-9 759.89 759.89 759.89 759.89 759.89 759.89 759.89 759.89
CE/ SC 14 15 16 17 18 19 20 21
Diagnstico
Diagnose
Noonan Pallister-Hall Rubinstein-Taybi Schinzel-Giedion Silver-Russell Smith-Lemli-Opitz Weaver Sndromes malformativos conocidos que afectan a mltiples rganos o sistemas (otros) Sndrome malformativo no etiquetado Sndrome alcohlico fetal
Noonan syndrome Pallister-Hall syndrome Rubinstein-Taybi syndrome Schinzel-Giedion syndrome Silver-Russell syndrome Smith-Lemli-Opitz syndrome Weaver syndrome Known malformative syndromes affecting multiple organs or systems (others) Malformative syndrome, unspecified Fetal alcohol syndrome
759.9
760.71
S/E S/E
27
4. Sndromes neurocutneos 4. Neurocutaneous syndromes
CIE-9/ ICD-9 216.8 237.71 237.72 259.8 288.2 702.8 709.09 756.4 756.89 757.1 757.1 757.33 757.33 757.39 757.39 757.8 759.5 759.6 759.6 759.89
CE/ SC S/E S/E S/E S/E S/E S/E S/E 02 03 01 02 01 02 01 02 S/E S/E 01 02
24
Diagnstico
Diagnose
Nevo pigmentado (epidrmico lineal, Jadasshon, melanosis neurocutnea) Neurofibromatosis tipo 1 (NF1) Neurofibromatosis tipo 2 (NF2) Progeria Chediak-Higashi Nevo lineal sebceo Lentiginosis-sordera-cardiopata Maffucci Waardenburg Neuroictiosis Sjgren-Larsson (ictiosis congnita) Hipomelanosis de Ito/incontinencia pigmenti Xerodermia pigmentosa Cockayne-Weber (epidermlisis bullosa) Proteus Neurocutneos (otros sndromes) Esclerosis tuberosa Sturge-Weber Von Hippel-Lindau Klippel-Trenaunay
Pigmented nevus (linear epidermal nevus, neurocutaneous melanosis) Neurofibromatosis, type 1 Neurofibromatosis, type 2 Progeria Chediak-Higashi syndrome Linear nevus sebaceous of Jadassohn Lentigines-deafness-cardiomyopathy (Leopard) Maffucci syndrome (enchondromatosis, Olliers disease) Waardenburg syndrome Neuroichthyosis Sjgren-Larsson (congenital ichthyosis) Ito hypomelanosis, incontinentia pigmenti Xeroderma pigmentosum Cockayne-Weber (epidermolysis bullosa) Proteus syndrome, Proteus-like syndrome Neurocutaneous syndromes (others) Tuberous sclerosis Sturge-Weber syndrome Von Hippel-Lindau syndrome Klippel-Trenaunay syndrome
28
5. Parlisis cerebral infantil. Ataxia. Trastornos del movimiento 5. Cerebral palsy. Ataxia. Movement disorders
CIE-9/ ICD-9 272.5 275.1 275.40 307.2 307.21 307.22 307.23 307.3 307.3
CE/ SC 02 S/E S/E S/E S/E S/E S/E 01 02
Diagnstico
Diagnose
Neuroacantocitosis Wilson Calcificacin de ncleos basales cerebrales Tics Tics transitorios Tics crnicos Gilles de la Tourette Estereotipias Spasmus nutans, movimientos repetitivos rtmicos (body rocking, head banging, bobble head) Autoestimulacin (masturbacin del lactante) Parkinson Parkinsonismo secundario Degeneracin estriatongrica Degeneracin olivopontocerebelosa Hallervorden-Spatz (deficiencia de pantotenato cinasa) Temblor esencial Temblor esencial larngeo Temblor esencial palatino Temblor familiar Temblor por frmacos Mioclonas benignas del lactante Mioclonas no epilpticas Mioclono benigno neonatal del sueo Mioclono esencial familiar Mioclono negativo
Neuroacanthocytosis Wilson disease Basal ganglia calcifications Tics Transient tics Chronic tics Tourette syndrome Stereotypies Spasmus nutans, rhythmic movements (body rocking, head banging, bobble head, jactatio capitis) Self-stimulation, infant masturbation Parkinson disease Secondary parkinsonism Striatopallidal disease Olivopontocerebellar atrophy Hallervorden-Spatz disease, pantothenate kinase associated neurodegeneration (PKAN) Benign essential tremor Essential laryngeal tremor Essential palatal tremor Familial tremor Drug induced tremor Benign myoclonus of early infancy Non-epileptic myoclonus Benign neonatal sleep myoclonus Essential myoclonus Negative myoclonus
307.9 332.0 332.1 333.0 333.0 333.0
S/E S/E S/E 01 02 03
333.1 333.1 333.1 333.1 333.1 333.2 333.2 333.2 333.2 333.2
01 02 03 04 05 01 02 03 04 05
29
CIE-9/ ICD-9 333.4 333.5 333.5 333.5 333.5 333.5 333.6 333.7 333.7 333.7 333.7 333.8 333.81 333.82 333.82 333.83 333.83 333.84 333.89 333.90 333.90 333.90 333.91 333.92 333.93
CE/ SC S/E 01 02 03 04 05 S/E 01 02 03 04 S/E S/E 01 02 01 02 S/E S/E 01 02 03 S/E S/E S/E
Diagnstico
Diagnose
Huntington Corea inducida por frmacos Corea familiar benigna Coreas (otras): corea y SAFL, lupus, vasculitis Coreoatetosis paroxstica cinesiognica PCI coreoatetoide Distona de torsin idioptica
Huntington disease Drug induced chorea Benign hereditary chorea Chorea (any etiology): antiphospholipid syndrome, lupus, vasculitis Paroxysmal kinesigenic choreoathetosis Choreoathetotic cerebral palsy Idiopathic torsion dystonia
Distona secundaria a ECM: alteracin de NT, Dystonia, secondary to neurometabolic pterinas, dficit de creatina cerebral diseases Distona sintomtica Distona por frmacos Distona de inicio tardo Distona focal sin especificar Blefarospasmo Distona orofacial y disfona Discinesia tarda Tortcolis espasmdica Tortcolis paroxistica benigna Espasmo del escribiente Distona paroxstica familiar Distona transitoria: distona paroxstica transitoria del lactante Sandifer Supraversin paroxstica benigna de la mirada Rgido acintico-hiperekplexia (sndrome) Neurolptico maligno (sndrome) Escalofros, sobresaltos (shuddering, jitteriness) Symptomatic dystonia Drug induced dystonia Late onset dystonia Focal or segmental dystonia Blepharospasm Orofacial dyskinesia Tardive dyskinesia Spasmodic torticollis Benign paroxysmal torticollis Writers cramp Familial paroxysmal dystonia Transient idiopathic dystonia Sandifer syndrome Paroxysmal tonic upgaze Hyperekplexia, startle disease Neuroleptic malignant syndrome Shuddering attacks, jitteriness
30
CIE-9/ ICD-9 333.99 342.8 343 343.0 343.1 343.2 343.4 343.8 343.8 379.59 392.0 781.3 781.93
CE/ SC S/E S/E S/E S/E S/E S/E S/E 01 02 S/E S/E S/E S/E
Diagnstico
Diagnose
Trastornos del movimiento (otros): piernas inquietas Hemipleja alternante PCI PCI dipljica PCI hemipartica espstica PCI tetrapartica espstica Hemipleja adquirida (excluye la PCI hemipljica) PCI distnica, mixta espstico-distnica PCI atxica o ataxia cerebelosa congnita (Marinesco-Sjgren) Opsoclono-mioclono o sndrome de Kinsbourne Corea reumtica de Sydenham Ataxia aguda Tortcolis ocular
Movement disorders (others: restless legs syndrome) Alternating hemiplegia of childhood Cerebral palsy Spastic diplegia, cerebral palsy Spastic hemiplegia, cerebral palsy Spastic tetraplegia, cerebral palsy Hemiparesis/hemiplegia (acquired; excludes hemiplegic cerebral palsy) Dyskinetic cerebral palsy Ataxic cerebral palsy (includes MarinescoSjgren syndrome) Opsoclonus-myoclonus syndrome, Kinsbourne syndrome Sydenham chorea, rheumatic chorea Acute cerebellar ataxia Torticollis, in ocular disease
31
6. Retrasos y trastornos del desarrollo, del aprendizaje y de la conducta 6. Developmental and behavioral disorders. Learning disabilities
CIE-9/ ICD-9 299.0 299.1 299.8 299.9 300.11 300.2 300.81 301.3 307.0 307.1 307.51 307.52 307.6 309.3 310.2 312.20 312.9 313.0 313.2 313.23 313.3 313.81 313.9
CE/ SC S/E S/E S/E S/E S/E S/E S/E S/E S/E S/E S/E S/E S/E S/E S/E S/E S/E S/E S/E S/E S/E S/E S/E
Diagnstico
Diagnose
Autismo Trastorno desintegrativo infantil Asperger Trastorno generalizado del desarrollo no especificado
Autism Childhood disintegrative disorder Asperger syndrome Pervasive developmental disorder not otherwise specified
Conversin o trastorno conversivo: parlisis, Conversion disorder: palsy, blindness, sordera, ceguera deafness Fobia o trastorno fbico Somatizacin (dolencias mltiples) Agresividad Tartamudeo Anorexia nerviosa Bulimia Pica Enuresis primaria o secundaria (no orgnica) Trastorno de la conducta (secundario, trastorno de adaptacin) Sndrome postraumtico (posconmocin cerebral) Disocial (trastorno) Trastorno de la conducta (en la infancia) Ansiedad (trastorno) Timidez y retraimiento social Mutismo electivo Socializacin (problemas) Oposicionista desafiante (trastorno) Trastorno emocional (distimia en la infancia) Phobic disorder Somatization disorder, somatoform disorder (unexplained complaints) Aggressiveness Stuttering, stammering Anorexia nervosa Bulimia (eating disorder) Pica (eating disorder) Enuresis (primary) (secondary) of nonorganic origin Adjustment disorder, adjustment reaction Postconcussive syndrome Conduct disorder, dissocial personality disorder Behavior disorder (disruptive behavioral disorder) Anxiety disorder Shyness Selective mutism Social and interpersonal problems Oppositional defiant disorder Emotional disorder (dysthymia in childhood)
32
CIE-9/ ICD-9 314.0 314.9 315.0 315.1 315.3 315.31 315.31 315.32 315.4 315.8 315.9 316 317 318.0 318.1 318.2 319 319 330.8 358.8 728.2 780.93 783.42
CE/ SC S/E S/E S/E S/E S/E 01 02 S/E S/E S/E S/E S/E S/E S/E S/E S/E 01 02 04 S/E S/E S/E S/E
Diagnstico
Diagnose
Trastorno por dficit atencin con/sin hiperactividad Hipercinesia/inatencin no especificada o de otras causas Dislexia Discalculia Lenguaje (TEL) Retraso simple del lenguaje Disfasia expresiva Disfasia mixta: comprensiva y expresiva Trastorno del desarrollo de la coordinacin Trastorno de orientacin visuoespacial Trastorno del aprendizaje Afectacin psquica acompaante a otras enfermedades sistmicas Retraso mental ligero (CI 70-51) Retraso mental moderado (CI 36-50) Retraso mental grave (CI 35-21) Retraso mental profundo (CI < 20) Retraso sin especificacin Retraso mental lmite (CI 71-80) Rett Hipotona benigna del lactante Debilidad muscular y atrofia muscular Amnesia (retrgrada) y prdida de memoria Retraso psicomotor
Attention deficit hyperactivity disorder Hyperactivity or inattention not otherwise specified Dyslexia Dyscalculia Specific language impairment Speech delay Expressive language disorder Mixed receptive-expressive language disorder Developmental coordination disorder Visual-spatial and perception disorder Learning disabilities Psychic factors associated with diseases classified elsewhere Mild mental retardation (IQ 70-51) Moderate mental retardation (IQ 36-50) Severe mental retardation (IQ 35-21) Profound mental retardation (IQ < 20) Mental retardation, not otherwise specified Borderline cognitive impairment (IQ 71-80) Rett syndrome Benign congenital hypotonia Muscular wasting or atrophy not elsewhere classified Amnesia, memory loss Delayed psychomotor development
33
CIE-9/ ICD-9 784.3 784.4 784.5 784.69 787.6 788.36 995.59
CE/ SC S/E S/E S/E S/E S/E S/E S/E
Diagnstico
Diagnose
Afasia adquirida (Landau-Kleffner, afasia postraumtica o lesional) Alteraciones de la voz: disfona, ronquera, hipernasalidad Disartrias Gerstmann Encopresis Enuresis nocturna Hipoestimulacin
Acquired childhood aphasia (LandauKleffner, following brain lesion) Voice disturbance: dysphonia, hypernasality, hoarseness Dysarthria, slurred speech Gerstmann developmental syndrome Encopresis Nocturnal enuresis Child neglect
34
7. Epilepsia. Trastornos paroxsticos no epilpticos. Patologa del sueo 7. Epilepsy. Non-epileptic paroxistic disorders. Sleep disorders
CIE-9/ ICD-9 255.6 306.8 307.45 307.46 307.47 337.0 345.0 345.0 345.0 345.0 345.1 345.1 345.1 345.2 345.3 345.3 345.4 345.40 345.40 345.41 345.41 345.41 345.41 345.5
CE/ SC S/E S/E S/E S/E S/E S/E 01 02 03 04 01 02 03 S/E 01 03 S/E 01 02 01 02 03 04 S/E
Diagnstico
Diagnose
Feocromocitoma Bruxismo Alteraciones del ritmo circadiano (ciclo vigilia-sueo) Sonambulismo, terrores nocturnos Pesadillas, parasomnias Sncope del seno carotdeo Ausencias atpicas Ausencias infantiles Ausencias mioclnicas Ausencias juveniles Epilepsia generalizada primaria convulsiva Epilepsia generalizada convulsiva sintomtica o criptognica Epilepsia con crisis tonicoclnicas del despertar Estatus epilptico no convulsivo Estatus epilptico convulsivo Estatus mioclnico Epilepsia focal/parcial sintomtica y criptognica Epilepsia focal/parcial secundaria a displasias, tberes, hamartomas Epilepsia del lbulo temporal mesial con o sin esclerosis hipocampal Crisis parciales migratorias de la infancia temprana Epilepsia del lbulo frontal Epilepsia del lbulo occipital no idioptica Hemipleja-hemiconvulsin (sndrome)
Pheochromocytoma Bruxism Sleep-wake cycle alteration, circadian rhythm disorders Somnambulism, night terrors Nightmare Carotid sinus syncope Atypical absences Childhood absence epilepsy Myoclonic absences Juvenile absence epilepsy Convulsive generalized epilepsy Symptomatic or cryptogenic generalized convulsive epilepsy Epilepsy with generalized tonic-clonic on awake Non-convulsive epileptic status Convulsive epileptic status Myoclonic epileptic status Symptomatic and cryptogenic focal epilepsy Epilepsy associated to cortical dysplasia, neurocutaneous disorders, hamartoma...) Mesial temporal lobe epilepsy with or without hippocampal sclerosis Migrating partial seizures of early infancy Frontal lobe epilepsy Nonidiopathic occipital epilepsy Hemiconvulsion-hemiplegia syndrome
Epilepsia focal o parcial idioptica o familiar Focal idiopathic and familial epilepsy with/ con/sin generalizacin secundaria without secondary generalization
35
CIE-9/ ICD-9 345.50 345.50 345.50 345.50
CE/ SC 01 02 03 04
Diagnstico
Diagnose
Convulsiones infantiles benignas no familiares (Watanabe) Epilepsia parcial benigna centrotemporal Epilepsia parcial benigna atpica
Benign infantile seizures nonfamilial Benign childhood epilepsy with centrotemporal spikes Atypical benign childhood epilepsy
Epilepsia occipital idioptica temprana (tipo Early-onset benign childhood occipital Panayiotopoulos) y tarda (tipo Gastaut) epilepsy (Panayiotopoulos type) and late-onset childhood occipital epilepsy (Gastaut type) Convulsiones infantiles benignas familiares (Vigevano) Epilepsia focal familiar con focos variables Epilepsia frontal nocturna autosmica dominante Epilepsia familiar del lbulo temporal West tpico, atpico y variantes Epilepsia parcial continua: tipo I (Kojevnikov) y tipo II (Rasmussen) Epilepsias y sndromes especficos sin cdigo propio Epilepsia mioclnico asttica Epilepsia mioclnica benigna de la infancia Epilepsia mioclnica juvenil Epilepsias mioclnicas progresivas: Unverricht-Lundborg, Lafora, ceroidolipofuscinosis Epilepsia mioclnica grave (Dravet) Lennox-Gastaut Landau-Kleffner EPOCS Benign familial infantile seizures Familial focal epilepsy with variable foci Autosomal dominant nocturnal frontal lobe epilepsy Familial temporal lobe epilepsy West syndrome (typical, atypical and variants) Epilepsia partialis continua (Kozhevnikov and Rasmussen type) Other epilepsies and epileptic syndromes not otherwise specified Epilepsy with myoclonic astatic seizures Benign myoclonic epilepsy in infancy Juvenile myoclonic epilepsy Progressive myoclonic epilepsies: UnverrichtLundborg disease, Lafora disease, neuronal ceroid lipofuscinosis, sialidosis, MERRF, other types Severe myoclonic epilepsy in infancy (Dravet syndrome) Lennox-Gastaut syndrome Landau-Kleffner syndrome Epilepsy with continous spike-waves during slow-wave sleep (CSWS)
345.51 345.51 345.51 345.51 345.6 345.7 345.8 345.80 345.80 345.80 345.81
01 02 03 04 S/E S/E S/E 01 02 03 01
345.81 345.81 345.81 345.81
02 03 04 05
36
CIE-9/ ICD-9 345.9 345.90 345.90 345.90 345.90 345.90 345.90 345.91
CE/ SC S/E 01 02 03 04 05 06 S/E
Diagnstico
Diagnose
Epilepsia no especificada si focal o generalizada Epilepsia del sobresalto Epilepsia fotosensible o visual sensitiva Epilepsia fotosensible idioptica del lbulo occipital Epilepsia generalizada con crisis febriles plus Epilepsia primaria de la lectura Epilepsias reflejas Crisis secundarias a: ECM, celiaqua, infecciones peri/posnatales, TCE, enfermedad gentica o cuadro malformativo conocido Narcolepsia-catapleja Muerte cerebral Hipotensin ortosttica Convulsiones neonatales familiares y no familiares benignas Convulsiones neonatales sintomticas por EHI, hipoglucemia, hipocalcemia, ECM Encefalopata epilptica infantil precoz Encefalopata mioclnica temprana/precoz Convulsiones neonatales (otras) Espasmos del sollozo Sncope (incluye sncope febril) Convulsin febril y estatus febril Crisis nica o grupo de crisis aisladas o raramente repetitivas Crisis inducidas por frmacos o drogas Crisis inmediatas a traumatismo
Nondetermined focal or generalized epilepsy Startle epilepsy Other visual sensitive epilepsies Idiopathic photosensitive occipital lobe epilepsy Generalized epilepsies with febrile seizures plus Primary reading epilepsy Reflex epilepsies Seizures in inborn errors of metabolism, coeliac disease, chromosomal abnormalities and cerebral malformations Narcolepsy-cataplexy Brain-death Ortostathic hypotension Benign familial and nonfamilial neonatal seizures Symptomatic neonatal seizures (hypoglicemia, IHE, hypocalcemia...) Early-infantile epileptic encephalopathy with suppression-bursts (Ohtahara syndrome) Early myoclonic encephalopathy Neonatal seizures (other types, not specified) Breathholding spells Syncope (includes febrile syncope) Febrile seizures and febrile status Single seizure or isolated clusters of seizures Drug or other chemically induced seizures Immediate and early posttraumatic seizures
347 348.8 458.0 779.0 779.0 779.0 779.0 779.0 780.2 780.2 780.31 780.39 780.39 780.39
S/E S/E S/E 01 02 03 04 05 01 02 S/E 01 02 03
37
CIE-9/ ICD-9 780.39
CE/ SC 04
Diagnstico
Diagnose
Crisis por accidente cerebral agudo (hipxico, hemorrgico, inflamatorio, nfeccioso...) Crisis por gastroenteritis Crisis por hipertensin endocraneal (hidrocefalia, tumores) Trastornos convulsivos no epilpticos (hiperekplexia, pseudocrisis, sncope convulsivo) Insomnio o perturbaciones del sueo Insomnio con apnea Hipersomnia, no especificado Alteraciones del ciclo vigilia-sueo Distona paroxstica nocturna Mioclonas de sueo Escalofros por fiebre EEG anormal
Symptomatic neonatal seizures (hypoglicemia, IHE, hypocalcemia...) Benign infantile convulsions associated with mild gastroenteritis Seizures in intracranial hypertension (hydrocephalus, tumors) Paroxysmal nonepileptic events (hiperekplexia, pseudoseizures, convulsive syncope) Insomnia and sleep disorders Insomnia with nocturnal apnea Hypersomnia, unspecified Disruptions of 24 hour sleep wake cycle, unspecified Nocturnal paroxismal dystonia Nocturnal myoclonus Shuddering associated to fever Abnormal EEG
780.39 780.39 780.39
05 06 07
780.5 780.51 780.54 780.55 780.59 780.59 780.6 794.02
S/E S/E S/E S/E 01 02 S/E S/E
38
8. Cefaleas 8. Headaches and related disorders
CIE-9/ ICD-9 307.80 307.81 307.81 346 346.0 346.1 346.2 346.2 346.2 346.2 346.2 346.8 346.8 346.9 348.2 349.0 350.1 352.1 536.2 784.0 784.0
CE/ SC S/E 01 02 S/E S/E S/E 01 02 03 04 05 01 02 S/E S/E S/E S/E S/E S/E 01
02
Diagnstico
Diagnose
Cefaleas de origen psiquitrico Cefalea crnica diaria Cefalea tensional Migraa Migraa con aura Migraa sin aura Migraa abdominal Migraa basilar Migraa en racimos Cefalea histamnica Migraa retiniana Migraa hemipljica familiar Migraa oftalmopljica Complicaciones de la migraa Hipertensin intracraneal benigna o pseudotumor cerebri Cefalea pospuncin Neuralgia del trigmino Neuralgia del glosofarngeo Vmitos cclicos Cefalea Cefalea secundaria
Psychogenic pain (headache) Chronic daily headache Tension headache Migraine Migraine with aura Migraine without aura Migraine, abdominal Migraine, basilar type Cluster headache Histamine cephalalgia Migraine, retinal Migraine, hemiplegic familiar Migraine, ophtalmoplegic Complication of migraine Pseudotumor cerebri / Benign intracranial hypertension Headache, post-lumbar puncture Trigeminal neuralgia Glossopharyngeal neuralgia Vomiting (cyclic, recurrent) Headache Secondary headache
39
9. Patologa infecciosa e inflamatoria 9. Infectious and inflammatory disorders
CIE-9/ ICD-9 013.0 013.2 023.8 042 045.10 046.1 046.2 046.8 047.9 049.9 052.0 052.7 054.3 055.0 071 083.9 084.9 088.81 090.4 130.0 320.9 321.8 322
Diagnstico
Diagnose
Meningitis tuberculosa Tuberculoma cerebral Neurobrucelosis Sida (aadir 049.9) Poliomielitis aguda Creutzfeldt-Jakob Panencefalitis esclerosante subaguda Infeccin del SNC por virus lentos Meningitis vrica no especificada Encefalitis vrica (MNI, parotiditis, rubola, CMV) Encefalitis posvaricela Cerebelitis posvaricelosa Encefalitis herptica Encefalitis postsarampin Rabia Encefalopata por Rickettsia Encefalopata en malaria Lyme (neuroborreliosis) Neurosfilis Meningoencefalitis por toxoplasma adquirida
Tuberculous meningitis Cerebral tuberculoma Neurobrucellosis HIV (add 049.9 AIDS encephalopathy) Paralytic poliomyelitis Creutzfeldt-Jakob disease Subacute sclerosing panencephalitis (SSPE) Other specified slow virus infection of central nervous system Non-determined viral meningitis Viral encephalitis (Epstein-Barr, mumps, rubella, CMV) Varicella encephalitis Varicella cerebellar ataxia Herpes virus encephalitis Measles encephalitis Rabies Rickettsial encephalitis Cerebral malaria Lyme disease (borreliosis) Neurosyphilis Toxoplasmic encephalitis
Meningitis bacteriana y meningoencefalitis Bacterial meningitis o meningoencephalitis bacteriana Meningitis por otros organismos: hongos, parsitos Other organisms meningitis: fungal, parasitic meningitis
Meningitis inespecfica: reaccin menngea Non-infectious meningitis: malignancies, qumica, secundaria a foco infeccioso, o LOE toxic, drug-induced, migraine with intracraneal, migraa con pleocitosis pleocytosis
40
9. Patologa infecciosa e inflamatoria 9. Infectious and inflammatory disorders
CIE-9/ ICD-9 323.4
CE/ SC S/E
Diagnstico
Diagnose
Encefalitis infecciosas (otras): cisticercosis, hidatidosis SNC, otros parsitos Encefalitis posvacunacin Encefalitis postinfecciosa Encefalomielitis aguda diseminada Leucoencefalitis hemorrgica aguda Encefalitis: paraneoplsicas, procesos autoinmunes, neurosarcoidosis Mielitis postinfecciosa, paraneoplsica, en procesos autoinmunes Absceso cerebral y cerebeloso Absceso y empiema espinal Empiema subdural, extradural Angetis, flebitis, tromboflebitis sptica de senos venosos intracraneales Celulitis orbitaria
Other infectious encephalitis: neurocysticercosis, cerebral echinococcosis, other parasitic infestation Post-immunization encephalitis Postinfectious encephalitis Acute disseminated encephalomyelitis (ADEM) Acute haemorrhagic leukoencephalitis Postinfectious, paraneoplastic or autoimmune encephalitis (neurosarcoidosis) Postinfectious, paraneoplastic or autoimmune myelitis Cerebral or cerebellar abscess Spinal abscess or empyema Subdural or extradural empyema Infectious arteritis or phlebitis (includes septic thrombophlebitis of cerebral venous sinuses) Orbital cellulitis
323.5 323.6 323.6 323.6 323.8 323.8 324.0 324.1 324.9 325
S/E 01 02 03 01 02 S/E S/E S/E S/E
376.01 383.02
S/E
S/E
Absceso extradural de la punta del peasco Infectious of apex of petrous bone o sndrome de Gradenigo (Gradenigos syndrome)
41
10. Patologa vascular 10. Vascular disorders
CIE-9/ ICD-9 430 431 431 432.0 432.1 433 434 435 437.1 437.3 437.4 437.5 437.6 437.8 443.21 443.24 747.81
CE/ SC S/E 01 02 S/E S/E S/E S/E S/E S/E S/E S/E S/E S/E S/E S/E S/E S/E
Diagnstico
Diagnose
Hemorragia subaracnoidea Hemorragia intraparenquimatosa Hemorragia ventricular Hemorragia epidural no traumtica Hemorragia subdural no traumtica
Subarachnoid hemorrhage Parenchymal hemorrhage Intraventricular hemorrhage Non-traumatic extradural hemorrhage Non-traumatic subdural hemorrhage
Oclusin de la arterial precerebral (cartida, Precerebral arterial occlusion (carotid, basilar, basilar, vertebral) vertebral) Oclusin de la arteria cerebral (embolia, trombosis) Isquemia cerebral transitoria Isquemia cerebral crnica. Insuficiencia cerebrovascular Aneurisma arterial intracraneal Vasculitis y arteritis cerebrales Moyamoya Trombosis de seno venoso intracraneal (incluye trombosis del seno cavernoso) Fstulas intracraneales: carotidocavernosa, dural Diseccin carotdea Diseccin de la arteria vertebral Malformacin arteriovenosa, aneurismas venosos (vena de Galeno) y fstulas congnitas cerebrales Malformacin arteriovenosa espinal o hemangioma espinal Cerebral arterial occlusion (embolism, thrombosis) Transient cerebral ischemia Chronic cerebral ischemia. Cerebrovascular insufficiency Intracranial arterial aneurysms Cerebral vasculitis, cerebral arteritis Moya-moya disease Sino-venous thrombosis (includes cavernous sinus thrombosis) Intracranial fistulas (carotid-cavernous, dural) Carotid artery dissection Vertebral artery dissection Arteriovenous malformation, venous aneurysm (includes veinof Galen malformation and other congenital fistulas) Spinal arteriovenous and hemangioma malformations
747.82
S/E
42
11. Patologa traumtica, txica y yatrognica. Coma 11. Traumatic, toxic and iatrogenic disorders. Coma
CIE-9/ ICD-9 250.3 251.0 292.12 292.2 293.0 305.0 331.81 341.9 344.81 345.3 348.31
CE/ SC S/E S/E S/E S/E S/E S/E S/E 01 S/E 02 01
Diagnstico
Diagnose
Coma diabtico cetoacidtico Coma hipoglucmico Alucinacin inducida por drogas Intoxicacin por droga de abuso Sndrome confusional agudo Intoxicacin alcohlica Reye (sndrome) Lesin axonal difusa Locked-in (enclaustramiento o estado similar) Coma poscrtico (tras crisis epilptica) Encefalopata metablica (ECM, alteraciones hidroelectrolticas, diabetes...) Encefalopata sptica (asociada a cualquier infeccin) Herniacin cerebral (cualquier sndrome por herniacin) Edema cerebral (de cualquier etiologa) Derivacin ventricular (complicacin) Rinorrea de LCR Coma txico (accidental, drogas de abuso, frmacos...) Otorrea de LCR Encefalopata hipertensiva (incluye encefalopata posterior reversible) Coma heptico (encefalopata heptica) Coma urmico Coma Alteracin transitoria de la conciencia Estado vegetativo persistente
Diabetic coma (with ketoacidosis) Hypoglycemic coma Hallucinosis drug-induced Drug intoxication Acute confusional state Alcoholic intoxication/abuse Reyes syndrome Diffuse axonal injury Locked-in state Epileptic coma (after seizure) Metabolic encephalopathy (inborn metabolic errors, water-electrolyte disorders, diabetes...) Septic encephalopathy (caused by any infection) Brain (stem) herniation Cerebral edema (any etiology) Ventriculoperitoneal shunt (complication) Rhinorrhea of cerebrospinal fluid Coma caused by poisoning (accident, drug abuse, biological or chemical substances, etc.) / Toxic encephalopathy Otorrhea of cerebrospinal fluid Hypertensive encephalopathy (posterior reversible encephalopathy syndrome) Hepatic coma (hepatic encephalopathy) Uremic coma Coma Transient alteration of awareness Persistent vegetative state
348.31 348.4 348.5 349.1 349.81 349.82
02 02 S/E S/E S/E S/E
388.61 437.2 572.2 588.89 780.01 780.02 780.03
S/E S/E S/E S/E S/E S/E S/E
43
CIE-9/ ICD-9 780.09 780.1 798.0 800.0 800.5 801.0 801.7
Diagnstico
Diagnose
Obnubilacin, somnolencia, estupor Alucinacin Muerte sbita del lactante Fractura de bveda craneal cerrada Fractura de bveda craneal abierta Fractura de base craneal cerrada (incluye techo de la rbita) Fractura de base craneal abierta con hemorragia subaracnoidea, subdural, extradural Fractura vertebral sin lesin medular Fractura vertebral con lesin medular Conmocin cerebral Conmocin cerebral con prdida de conocimiento transitoria (TCE) Conmocin cerebral con coma prolongado con recuperacin (TCE)
Drowsiness, unconsciousness, somnolence, stupor Hallucination Sudden infant death syndrome Skull fracture, closed Skull fracture, open Closed fracture of base of skull (orbital ceiling included) Skull open fracture with subarachnoid, subdural, and extradural hemorrhage Vertebral fracture without spinal cord damage Vertebral fracture with spinal cord damage Cerebral concussion Cerebral concussion with transitory loss of consciousness (brain injury) Cerebral concussion with prolonged coma and recovery
805.8 806.8 850.0 850.1 850.3 850.4 850.5 851.0 851.4 851.8 852.0 852.2 852.4 853.0 950.0
S/E S/E S/E S/E S/E S/E S/E S/E S/E S/E S/E S/E S/E S/E S/E
Conmocin cerebral con coma profundo sin Cerebral concussion with deep coma without recuperacin (TCE) recovery Coma traumtico Contusin cerebral cortical Contusin cerebelosa (o de pednculos cerebrales) Contusin cerebral de otras estructuras (meninges) Hemorragia subaracnoidea traumtica Hematoma subdural traumtico Hematoma epidural traumtico Hematoma parenquimatoso traumtico (incluye HIV) Nervio ptico (lesin traumtica) Traumatic coma Cerebral cortical concussion Cerebellar concussion Cerebral concussion of other structures (meninges) Traumatic subarachnoid hemorrhage Traumatic subdural hematoma Traumatic epidural hematoma Traumatic parenchymatous hematoma (intraventricular hemorrhage included) Optic nerve (traumatic injury)
44
CIE-9/ ICD-9 950.9 951.8 952.0 952.1 952.2 952.3 952.4 953.9 955.9 956.9 959.01 962.9
CE/ SC S/E S/E S/E S/E S/E S/E S/E S/E S/E S/E S/E S/E
Diagnstico
Diagnose
Ceguera cortical traumtica Nervio craneal (lesin traumtica)
Traumatic cortical blindness Cranial nerve (traumatic injury)
Mdula espinal cervical (lesin traumtica) Cervical spinal cord (traumatic injury) Mdula espinal torcica (lesin traumtica) Thoracic spinal cord (traumatic injury) Mdula espinal lumbar (lesin traumtica) Mdula espinal sacra (lesin traumtica) Cola de caballo (lesin traumtica) Plexo o raz (lesin traumtica) Nervio perifrico de miembro superior o cintura escapular (lesin traumtica) Nervio perifrico de miembro inferior o cintura plvica (lesin traumtica) TCE Sobredosis (accidental o no) de corticoides u otras hormonas y sustitutos sintticos Lumbar spinal cord (traumatic injury) Sacral spinal cord (traumatic injury) Cauda equina (traumatic injury) Spinal plexus or nerve roots (traumatic injury) Peripheral nerve of upper limb or shoulder girdle (traumatic injury) Peripheral nerve of lower limb or pelvic girdle (traumatic injury) Traumatic head injury Overdose (accidental or not) of corticosteroids, other hormones or synthetic substitutes
965.9 966.1 966.2 966.3
S/E S/E S/E S/E
Sobredosis (accidental o no) de analgsicos Overdose (accidental or not) of analgesics (opiceos, AINE) (opioids, antirheumatics) Sobredosis (accidental o no) de fenitona Sobredosis (accidental o no) de etosuximida Overdose (accidental or not) of phenytoin Overdose (accidental or not) of ethosuximide
Sobredosis (accidental o no) de cualquier Overdose (accidental or not) of any anticonvulsionante (excepto fenitona, antiepileptic drug (except phenytoin, etosuximida, barbitricos, benzodiacepinas) ethosuximide, barbiturates) Sobredosis (accidental o no) de barbitricos Overdose (accidental or not) of barbiturates Sobredosis (accidental o no) de benzodiacepinas Sobredosis (accidental o no) de psicoestimulantes (metilfenidato, anfetaminas) Sobredosis (accidental o no) de psicotrpicos Overdose (accidental or not) of benzodiazepines Overdose (accidental or not) of central nervous system stimulants (methylphenidate, amphetamines) Overdose (accidental or not) of psychotropic agents
967.0 969.4 969.7
S/E S/E S/E
969.9
S/E
45
CIE-9/ ICD-9 977.9 984 985 986 988.9 989 989.5 990 992.5 995.50 995.53 995.55 996.2 997.01 997.09
CE/ SC S/E S/E S/E S/E S/E S/E S/E S/E S/E S/E S/E S/E S/E S/E S/E
Diagnstico
Diagnose
Intoxicacin por frmacos Intoxicacin por plomo y sus compuestos Intoxicacin por metales Intoxicacin por monxido de carbono Intoxicacin por alimentos (hongos, plantas) Intoxicacin por insecticida, pesticidas, venenos Efecto txico de: mordedura de serpientes, araas, etc. Radiacin. Efectos de la misma no especificados Golpe de calor Malos tratos infantiles Violacin a menores Zarandeado (sndrome del nio) Derivacin ventricular (complicacin mecnica) Dao cerebral secundario a procedimiento quirrgico o mdico (lesin anxica) Dao cerebral secundario a procedimiento quirrgico o mdico (hemorragia o infarto) Puncin lumbar (complicacin secundaria) Degeneracin cerebral secundaria a quimioterepia antineoplsica (con o sin radioterapia) Efecto adverso de un frmaco (administrado de forma apropiada y dosis correctas)
Poisoning by medicinal and biological substances Lead and lead compound poisoning Heavy metal poisoning Carbon monoxide poisoning Food poisoning (mushrooms, plants, fish, shellfish) Insecticide, pesticide poisoning Bite of snakes, spiders, etc., toxic effect Effects of radiation Heatstroke / Sunstroke Child abuse, unspecified Child sexual abuse Shaken infant syndrome Ventriculoperitoneal shunt malfunction Nervous system lesion caused by surgical or medical procedure Nervous system lesion caused by surgical or medical procedure (cerebrovascular infarction or hemorrhage) Lumbar puncture (secondary complication) Cerebral degeneration caused by chemotherapy (with or without radiotherapy) Adverse effect of biological, correct substance properly administered
E879.4 E933.1
S/E S/E
E947.9
S/E
46
12-I. Patologa tumoral 12-I. Tumor pathology
CIE-9/ ICD-9 191.0
CE/ SC S/E
Diagnstico
Diagnose
Neoplasia maligna del cerebro, excepto lbulos y ventrculos (ganglios basales)
Malignant neoplasia of cerebrum, except lobes and ventricles (basal ganglia/cerebral cortex/corpus striatum/globus pallidus/ hypothalamus/thalamus) Malignant neoplasia of frontal lobe Malignant neoplasia of temporal lobe Malignant neoplasia of parietal lobe Malignant neoplasia of occipital lobe Malignant neoplasia of ventricles Malignant neoplasia of cerebellum Malignant neoplasia of brain stem Malignant neoplasia of other parts of brain (corpus callosum/tapetum, malignant neoplasm of contiguous or overlapping sites of brain) Malignant neoplasia of brain, unspecified Malignant neoplasia of cranial nerves Malignant neoplasia of cerebral meninges Malignant neoplasia of spinal cord Malignant neoplasia of spinal meninges Malignant neoplasia of other specified sites of nervous system (malignant neoplasm of contiguous or overlapping sites of other parts of nervous system) Malignant neoplasia of nervous system, part unspecified Malignant neoplasia of other endocrine glands and related structures Malignant neoplasia of pituitary gland, craniopharyngeal duct Malignant neoplasia of pineal gland
191.1 191.2 191.3 191.4 191.5 191.6 191.7 191.8
S/E S/E S/E S/E S/E S/E S/E S/E
Neoplasia maligna del lbulo frontal Neoplasia maligna del lbulo temporal Neoplasia maligna del lbulo parietal Neoplasia maligna del lbulo occipital Neoplasia maligna de los ventrculos Neoplasia maligna del cerebelo Neoplasia maligna del tronco cerebral Neoplasia maligna de otras partes del cerebro en contigidad, cuerpo calloso
191.9 192.0 192.1 192.2 192.3 192.8
S/E S/E S/E S/E S/E S/E
Neoplasia maligna del cerebro Neoplasia maligna de los nervios craneales Neoplasia maligna de las meninges cerebrales Neoplasia maligna de la mdula espinal Neoplasia maligna de las meninges espinales Neoplasia maligna de otros sitios especificados del sistema nervioso (en contigidad) Neoplasia maligna del sistema nervioso central Neoplasia maligna de otras glndulas endocrinas y estructuras relacionadas Neoplasia maligna de la glndula pituitaria y conducto craneofarngeo Neoplasia maligna de la glndula pineal
192.9 194 194.3 194.4
S/E S/E S/E S/E
47
12-I. Patologa tumoral 12-I. Tumor pathology
CIE-9/ ICD-9 198.3 198.4 225.0 225.1 225.2 225.3 225.4 225.8
CE/ SC S/E S/E S/E S/E S/E S/E S/E S/E
Diagnstico
Diagnose
Neoplasia maligna secundaria en cerebro y mdula espinal Neoplasia maligna secundaria en otras partes del sistema nervioso (meninges) Neoplasia benigna del encfalo Neoplasia benigna de los nervios craneales Neoplasia benigna de las meninges cerebrales Neoplasia benigna de la mdula espinal Neoplasia benigna de las meninges espinales Neoplasia benigna en otros sitios especificados del sistema nervioso (de contigidad) Neoplasia benigna del sistema nervioso central Neoplasia benigna de otras glndulas endocrinas y estructuras relacionadas Neoplasia benigna de la glndula pituitaria y conducto craneofarngeo Neoplasia benigna de la glndula pineal Neoplasia de evolucin incierta de la glndula pituitaria y conducto craneofarngeo Neoplasia de evolucin incierta de la glndula pineal Neoplasia de evolucin incierta del cerebro y mdula espinal Neoplasia de evolucin incierta de las meninges Neoplasia de evolucin incierta de otras partes no especificadas del sistema nervioso Quiste coloide del III ventrculo
Secondary malignant neoplasia of brain and spinal cord Secondary malignant neoplasia of other parts of nervous system (meninges) Benign neoplasia of brain Benign neoplasia of cranial nerves Benign neoplasia of cerebral meninges Benign neoplasia of spinal cord Benign neoplasia of spinal meninges Benign neoplasia of other specified sites of nervous system Benign neoplasia of nervous system, part unspecified Benign neoplasia of other endocrine glands and related structures Benign neoplasia of pituitary gland and craniopharyngeal duct (pouch) Benign neoplasm of pineal gland Neoplasia of uncertain behavior of pituitary gland and craniopharyngeal duct Neoplasia of uncertain behavior of pineal gland Neoplasia of uncertain behavior of brain and spinal cord Neoplasia of uncertain behavior of meninges Neoplasia of uncertain behavior of other and unspecified parts of nervous system Neoplasia of uncertain behavior of cholloid cyst of third ventricle
225.9 227 227.3 227.4 237.0
S/E S/E S/E S/E S/E
237.1 237.5 237.6 237.9
S/E S/E S/E S/E
742.4
04
48
12-II. Clasificacin morfolgica de los tumores del sistema nervioso 12-II. Morphology of nervous system neoplasms
CIE-9/ ICD-9
CE/ SC
Diagnstico
Diagnose
M8000/6 S/E M8140/0 S/E M8680/1 S/E M8720/3 S/E M8728/0 S/E M8728/1 S/E M8728/3 S/E M8850/0 S/E M9064/3 S/E M9070/3 S/E M9071/3 S/E M9080/0 S/E M9080/1 S/E M9080/3 S/E M9084/0 S/E M9084/3 S/E M9085/3 S/E M9100/3 S/E M9120/0 S/E M9121/0 S/E M9122/0 S/E M9141/0 S/E M9150/1 S/E M9160/0 S/E M9161/1 S/E M9170/0 S/E M9350/1 S/E
Metstasis Adenoma Paraganglioma Melanoma maligno Melanocitosis difusa Melanocitoma Melanomatosis menngea Lipoma Germinoma Carcinoma embrionario Tumor del seno endodrmico Teratoma benigno Teratoma Teratoma maligno Quiste dermoide Quiste dermoide con transformacin maligna Tumores germinales mixtos Coriocarcinoma Hemangioma Hemangioma cavernoso Hemangioma venoso Angioqueratoma Hemangiopericitoma Angiofibroma Hemangioblastoma Linfangioma Craneofaringioma
Neoplasm, metastatic Adenoma Paraganglioma filum terminale Malignant melanoma Diffuse melanocytosis Meningeal melanocytoma Meningeal melanomatosis Lipoma Germinoma Embryonal carcinoma Yolk sac tumour Teratoma, benign Teratoma Teratoma, malignant Dermoid cyst Dermoid cyst with malignant transformation Mixed germ cell tumour Choriocarcinoma Haemangioma Cavernous haemangioma Venous haemangioma Angiokeratoma Haemangiopericytoma Angiofibroma Haemangioblastoma Lymphangioma Craniopharyngioma
49
CIE-9/ ICD-9
CE/ SC
Diagnstico
Diagnose
M9360/1 S/E M9361/1 S/E M9362/3 S/E M9370/3 S/E M9380/3 S/E M9381/3 S/E M9382/3 S/E M9383/1 S/E M9384/1 S/E M9390/0 S/E M9390/3 S/E M9391/3 S/E M9392/3 S/E M9393/3 S/E M9394/1 S/E M9400/3 S/E M9401/3 S/E M9412/1 S/E M9413/0 S/E M9421/1 S/E M9424/3 S/E M9430/3 S/E M9440/3 S/E M9444/1 S/E M9450/3 S/E M9451/3 S/E
Pinealoma Pineocitoma Pineoblastoma Cordoma Glioma maligno Gliomatosis cerebri Glioma mixto Subependimoma Astrocitoma subependimario de clulas gigantes Papiloma del plexo coroideo Carcinoma del plexo coroideo Ependimoma Ependimoma anaplsico Ependimoma papilar Ependimoma mixopapilar Astrocitoma Astrocitoma anaplsico Astrocitoma/ganglioglioma desmoplsico infantil Tumor neuroepitelial disembrioplsico Astrocitoma piloctico Xantoastrocitoma pleomrfico Astroblastoma Glioblastoma Glioma cordoide Oligodendroglioma Oligodendroglioma anaplsico
Pinealoma Pineocytoma Pineoblastoma Chordoma Glioma, malignant Gliomatosis cerebri Mixed glioma Subependymoma Subependymal giant cell astrocytoma Choroid plexus papilloma Choroid plexus carcinoma Ependymoma Ependymoma, anaplastic Papillary ependymoma Myxopapillary ependymoma Astrocytoma Astrocytoma, anaplastic Desmoplastic infantile astrocytoma Dysembryoplastic neuroepithelial tumour Pilocytic astrocytoma Pleomorphic xanthroastrocytoma Astroblastoma Glioblastoma Chordoid glioma Oligodendroglioma Oligodendroglioma, anaplastic
50
CIE-9/ ICD-9
CE/ SC
Diagnstico
Diagnose
M9470/3 S/E M9473/3 S/E M9490/0 S/E M9490/3 S/E M9492/0 S/E M9493/0 S/E M9500/3 S/E M9501/3 S/E M9505/1 S/E M9505/3 S/E M9506/1 S/E M9508/3 S/E M9510/3 S/E M9522/3 S/E M9523/3 S/E M9530/0 S/E M9540/0 S/E M9540/3 S/E M9550/0 S/E M9560/0 S/E M9571/0 S/E M9590/3 S/E M9720/3 S/E M9930/3 S/E
Meduloblastoma Tumor neuroectodrmico primitivo Ganglioneuroma Ganglioneuroblastoma Gangliocitoma Gangliocitoma displstico del cerebelo (Lhermitte-Duclos) Neuroblastoma Meduloepitelioma Ganglioglioma Ganglioglioma anaplsico Neurocitoma central Tumor teratoide/rabdoide atpico Retinoblastoma Neuroblastoma olfatorio (estesioneuroblastoma) Neuroepitelioma olfatorio Meningioma Neurofibroma Neurofibrosarcoma o tumor maligno de vaina de nervio perifrico Neurofibroma plexiforme Schwanomma/neurinoma Perineurioma Linfoma maligno Histiocitosis maligna Sarcoma mieloide (granuloctico)
Medulloblastoma Primitive neuroectodermal tumour Ganglioneuroma Ganglioneuroblastoma Gangliocytoma Dysplastic gangliocytoma of cerebellum (Lhermitte-Duclos) Neuroblastoma Medulloepithelioma Ganglioglioma Ganglioglioma, anaplastic Central neurocytoma Atypical teratoid/rhabdoid tumour Retinoblastoma Olfactory neuroblastoma Olfactory neuroepithelioma Meningioma Neurofibroma Malignant peripheral nerve sheath tumour Plexiform neurofibroma Neurilemmoma, schwannoma Perineurioma Malignant lymphoma Malignant histiocytosis Myeloid sarcoma
51
13. Errores congnitos del metabolismo con repercusin neurolgica 13. Inborn errors of metabolism with neurological repercussions
CIE-9/ ICD-9 266.2 266.2 266.2 266.9 270.0 270.1 270.2
CE/ SC 01 02 03 S/E S/E S/E 01
Diagnstico
Diagnose
Folato cerebral y cido folnico (dficit) Biotina (trastorno del metabolismo) Vitamina B12 (trastorno del metabolismo) Piridoxina (dependencia) Aminoacidopata (alteracin del transporte): Hartnup, cistinosis, otros Fenilcetonuria Tirosinemia, alteraciones del triptfano (ECM de aminocidos aromticos excepto fenilalanina) Aciduria metilmalnica Jarabe de arce (ECM de aminocidos de cadena ramificada) Metionina sintasa (dficit) Metiltetrahidrofolatorreductasa (dficit MTHFR) Sulfito oxidasa (dficit) Homocistinuria (ECM de aminocidos sulfurados) Histidinemia Ciclo de la urea (trastorno): sndrome HHH (hiperamonemia, hiperornitinemia, homocitrulinuria), aciduria argininosuccnica Aciduria glutrica tipo I Hiperglicinemia no cetsica Carnosinemia Glutatin sintetasa (dficit) Creatina cerebral (dficit) Hiperprolinemia
Folic acid and folinic acid (cerebral deficiency) Biotine (inborn error of metabolism of) Vitamin B12 (inborn error of metabolism of) Piridoxine dependency syndrome Disorders of aminoacid transport: Hartnup disease, cystinosis, etc. Phenilketonuria Hypertyrosinemia, other inborn errors of the metabolism of aromatic aminoacids (except phenylalanine) Methylmalonic acidemia Maple urine syrup disease (and other inborn errors of the metabolism of branched-chain aminoacids) Methionine synthase deficiency Methylenetetrahydrofolate reductase deficiency Sulfite oxidase deficiency Homocystinuria (and other inborn errors of sulfur-containing aminoacids) Histidinemia Urea cycle disorder: HHH syndrome, argininosuccinic aciduria, etc.
270.3 270.3
01 02
270.4 270.4 270.4 270.4 270.5 270.6
01 02 03 04 S/E S/E
270.7 270.7 270.8 270.8 270.8 270.8
01 02 01 02 03 04
Glutaric aciduria, type I Non-ketotic hyperglycinemia Carnosinemia Glutathione synthetase deficiency Creatine deficiency, cerebral Hyperprolinemia
52
CIE-9/ ICD-9 270.9 270.9 270.9 271.0 271.1 271.2 271.8 271.8 271.9 271.9 272.5 272.7 272.8 277.1 277.2
CE/ SC 01 02 03 S/E S/E S/E 01 02 01 02 01 S/E S/E S/E S/E
Diagnstico
Diagnose
Aciduria orgnica: isovalrica, propinica y Organic aciduria: isovaleric, propionic, and otras (2-OH-glutarica, 3-metiglutacnica...) others not specified otherwise Canavan o degeneracin esponjosa del cerebro Deficiencia mltiple de carboxilasas (MCAD) Glucogenosis Galactosemia Canavan disease (aspartate acylase deficiency) Multiple carboxylases deficiency (MCAD) Glycogenosis Galactosemia
Fructosa 1,6 difosfato (dficit) o intolerancia Hereditary fructose intolerance (fructose 1,6 hereditaria a la fructosa diphosphatase deficiency) Piruvato carboxilasa y piruvato deshidrogenasa (dficit) Oligosacaridosis (manosidosis, fucosidosis, aspartilglucosaminuria) Glicoprotenas deficientes en carbohidratos Carbohidratos (glicerocinasa), trastorno del metabolismo A-beta-lipoproteinemia familiar (BassenKornzweig), hipobetalipoproteinemia Mucolipidosis I, II, III, IV (sialidosis, I-cell) Farber Porfirias (trastorno del metabolismo) Purinas y pirimidinas (trastorno del metabolismo): Lesch-Nyhan, dficit de adenilsuccinatoliasa, dficit de adenosina deaminasa, sndrome de deplecin de nucletidos, etc. Mucopolisacaridosis Biotinidasa (dficit) Carnitina (trastorno del metabolismo) Aciduria glutrica tipo II Carnitil palmitoil transferasa (dficit CPT) Pyruvate dehydrogenase, pyruvate carboxylase deficiencies Oligosaccharidoses (mannosidosis, fucosidosis, aspartylglycosaminuria) Glycosylation, congenital disorders Carbohydrates, congenital disorder of metabolism Abetalipoproteinemia (Bassen-Kornzweig disease), hypobetalipoproteinemia Mucolipidoses I, II, III, IV (sialidoses, I cell disease, etc.) Farber disease Porphyrias Purines and pirimidines, metabolic disorders: Lesch-Nyhan disease, adenylosuccinate lyase deficiency, etc.
277.5 277.6 277.82 277.85 277.85
S/E S/E S/E 01 02
Mucopolysaccharidosis Biotinidase deficiency Carnitine, disorder of metabolism Glutaric aciduria, type II Carnitine palmitoyl transferase deficiency
53
CIE-9/ ICD-9 277.85 277.86 277.87 277.87
CE/ SC 03 S/E 01 02
Diagnstico
Diagnose
Beta-oxidacin de los cidos grasos (trastorno del metabolismo) Peroxisomales (enfermedades) Cetlisis (defecto) Mitocondrial (trastorno del metabolismo): cadena respiratoria, citopatasmitocondriales Sulfatasa (dficit) Neurotransmisores (trastorno del metabolismo) Ceroidolipofuscinosis Galactosialidosis Gangliosidosis GM1 y GM2 (Tay-Sachs, Sandhoff) Lipidosis clsicas con afectacin cerebral: Niemann-Pick A, B, C, Gaucher, Fabry, etc. Lipidosis con afectacin cerebral (otras): Smith-Lemli-Opitz, aciduria mevalnica, Tangier, xantomatosis cerebrocutnea Error innato metablico (sospecha) Adrenoleucodistrofia (Schilder) Refsum Menkes (trastornos del metabolismo del cobre)
Beta-oxidation of fatty acids, congenital disorder Peroxisomal diseases (except adrenoleukodistrophy) Ketolisis, congenital deficiency Mitochondrial metabolism disorder: respiratory chain, any mitochondrial cytopathy Sulfatase deficiency Neurotransmitters, disorders of metabolism Ceroid lipofuscinosis, neuronal Galactosialidosis GM1 and GM2 gangliosidosis (Tay-Sachs and Sandhof diseases, etc.) Classic cerebral lipidoses: Niemann-Pick A, B, C, Gaucher, Fabry, etc. Cerebral lipidoses, not specified otherwise (i.e. Smith-Lemli-Opitz, mevalonic aciduria, cerebrotendinous xanthomatosis...) Inborn error of metabolism, suspected Adrenoleukodistrophy Refsum disease Menkes disease
277.89 277.89 330.1 330.1 330.1 330.2 330.2
01 02 01 02 03 01 02
330.3 341.1 356.3 759.89
S/E S/E S/E 25
54
14. Enfermedades neurodegenerativas. Leucodistrofias 14. Neurodegenerative diseases. Leukodystrophies
CIE-9/ ICD-9 046.3 330.0
CE/ SC S/E S/E
Diagnstico
Diagnose
Leucoencefalopata multifocal progresiva
Progressive multifocal leukoencephalopathy
Leucodistrofias: Krabbe, Alexander, Leukodystrophy: Krabbe, Alexander, Pelizaeus-Merzbacher, van der Knaap, LDM, Pelizaeus-Merzbacher, globoid cell, van der Aicardi-Goutires Knaap, metachromatic, Aicardi-Goutires Alpers Distrofia neuroaxonal infantil (Schindler) Leigh Degeneracin o regresin neurolgica de etiologa desconocida Degeneracin cerebral por enfermedad cerebrovascular, neoplasia, hidrocefalia, deficiencia vitamnica o nutricional Ataxia de Friedreich Ataxia con atrofia cerebelosa o degeneracin cerebelosa primaria Alpers disease Neuroaxonal dystrophy (Schindler disease) Leighs disease Cerebral degenerative disease in childhood Cerebral degeneration in cerebrovascular disease, neoplastic disease, hydrocephalus, vitamin or nutritional deficiency Friedreichs ataxia Primary cerebellar degeneration or ataxia with cerebellar atrophy
330.8 330.8 330.8 330.9 331.7
1 2 3 S/E S/E
334.0 334.2 334.4
S/E S/E S/E
Ataxia asociada a ECM, encefalopata Cerebellar ataxia in inborn error of degenerativa, encefalopatas epilpticas metabolism, degenerative disease, epileptic encephalopathy Ataxias cerebelosas autosmicas dominantes, ligadas al sexo Ataxia con incoordinacin oculoceflica Ataxia peridica hereditaria Ataxia telangiectasia Degeneracin espinocerebelosa Inclusiones intraneuronales (enfermedad) Esclerosis mltiple Neuromielitis ptica Mielinosis central pontina Desmielinizacin no especificada del SNC Cerebellar ataxia, autosomal recessive, dominant, X-linked (includes Joubert and other similar disorders) Cerebellar ataxia with oculomotor apraxia Episodic ataxia Ataxia telangiectasia, ataxia telangiectasialike disorder Spinocerebellar ataxia/degeneration Intraneuronal inclusions disease Multiple sclerosis Neuromyelitis optica Central pontine myelinosis Demyelinating disease of central nervous system, unspecified
334.8
334.8 334.8 334.8 334.9 335.8 340 341.0 341.8 341.9
2 3 4 S/E S/E S/E S/E S/E 2
55
15. Otoneurologa. Neurooftalmologa 15. Otoneurology. Neuro-ophthalmology
CIE-9/ ICD-9 130.2 270.2 337.9 360.44 362.21 362.72
CE/ SC S/E 2 S/E S/E S/E S/E
Diagnstico
Diagnose
Coriorretinitis por toxoplasma Albinismo Horner Leucocoria Retinopata del prematuro Retinopata en otros trastornos: Refsum, A-beta-lipoproteinemia Retinitis pigmentosa Hemorragia retiniana Vogt-Koyanagi-Harada Uvetis Catarata infantil Alteraciones de refraccin y acomodacin Ambliopa y defectos refractivos Perturbacin visual subjetiva (macro-micropsias, fotofobia) Diplopa Defectos del campo visual Alteracin de la visin cromtica Ceguera nocturna o nictalopa Perturbacin visual, incluye visin borrosa Ceguera y baja visin (no incluye defectos refractivos) Anillo de Kayser-Fleischer Depsitos corneanos asociados con trastornos metablicos (otros)
Chorioretinitis due to toxoplasmosis Albinism Horner syndrome Leukokoria Retrolental fibroplasia / Retinopathy of prematurity Retinal dystrophy in other systemic disorders and syndromes: Refsum, abetalipoproteinemia Pigmentary retinal dystrophy Retinal hemorrhage Vogt-Koyanagi-Harada syndrome Unspecified iridocyclitis/uveitis Infantile cataract Disorders of refraction and accommodation Amblyopia Subjective visual disturbances: macropsia, micropsia, metamorphopsia Diplopia Visual field defects Color vision deficiencies Night blindness Other visual disturbances, blurred vision included Impairment level not further specified (blindness and low vision included, disorders of refraction not included) Kayser-Fleischer ring Other corneal deposits associated with metabolic disorders
362.74 362.81 364.24 364.3 366.0 367.0 368.0 368.1 368.2 368.4 368.5 368.6 368.8 369.00
S/E S/E S/E S/E S/E S/E S/E S/E S/E S/E S/E S/E S/E S/E
371.14 371.15 374.3
S/E S/E S/E
Ptosis del prpado, excluye ptosis congnita Ptosis of eyelid, congenital ptosis not included
56
CIE-9/ ICD-9 374.46 377.00 377.1 377.16 377.2 377.21 377.23 377.24 377.3 377.31 377.32 377.6 377.7 377.75 378.0 378.1 378.5 378.55 378.71 378.72 378.81 378.86 378.9
Diagnstico
Diagnose
Blefarofimosis Papiledema Atrofia ptica Atrofia ptica hereditaria, incluye atrofia ptica de Leber y hereditaria dominante Anomalas de disco ptico, incluye coloboma del disco ptico (congnito) Drusas del disco ptico Coloboma del disco ptico (adquirido) Pseudopapiledema Neuritis ptica Papilitis Neuritis ptica retrobulbar Vas pticas, afectacin Corteza visual, afectacin Ceguera cortical Endotropa Exotropa Estrabismo paraltico
Blepharophimosis Papilledema Optic atrophy Hereditary optic atrophy, dominant hereditary and Lebers optic atrophy included Other disorders of optic disc, congenital coloboma included Drusen of optic disc Coloboma of optic disc (acquired) Pseudopapilledema Optic neuritis, meningococcal neuritis not included Optic papillitis Retrobulbar optic neuritis (acute) Disorders of other visual pathways Disorders of visual cortex (agnosia and hallutination not included) Cortical blindness Esotropia, intermittent esotropia not included Exotropia, intermittent exotropia not included Paralytic strabismus
Oftalmopleja externa (incluye sndrome de External ophthalmoplegia (includes TolosaTolosa-Hunt) Hunt syndrome) Duane Oftalmopleja externa progresiva Parlisis conjugada de la mirada (incluye Parinaud) Oftalmopleja internuclear Duanes syndrome Progressive external ophthalmoplegia Palsy of conjugate gaze (Parinaud syndrome and others) Internuclear ophthalmoplegia
Motilidad ocular alterada (excluye nistagmo Unspecified disorder of eye movements, y movimientos irregulares de ojos) nystagmus and other irregular eyes movements not included
57
CIE-9/ ICD-9 379.4 379.51 379.58
CE/ SC S/E S/E S/E
Diagnstico
Diagnose
Anisocoria y otros problemas pupilares (adquiridos) Nistagmo congnito Apraxia oculomotora, incluye sndrome de Cogan Mnire Vrtigo perifrico Vrtigo paroxstico benigno, vrtigo posicional benigno Neuronitis vestibular Vrtigo central Laberintitis Hipoacusia repentina Tnnitus Acstico (lesin del VIII par) Sordomudez Hipoacusia Catarata congnita y anomalas del cristalino: afaquia congnita o ausencia de cristalino Aniridia Anomalas del iris y cuerpo ciliar (otras): anisocoria congnita, atresia depupila, coloboma de iris Anomalas vtreas, incluye opacidad vtrea congnita Coloboma de fondo de ojo Coloboma del nervio ptico (congnito) Ptosis congnita Anomalas congnitas del prpado (otras)
Anomalies of pupillary function (acquired anisocoria and others included) Congenital nystagmus Deficiencies of smooth pursuit movements (Cogan syndrome/apraxia oculomotora included) Mnires disease Peripheral vertigo Benign paroxysmal positional vertigo Vestibular neuronitis Vertigo of central origin Labyrinthitis Sudden hearing loss Tinnitus Disorders of acoustic or eighth nerve Deaf mutism Unspecified hearing loss Congenital cataract and lens anomalies (infantile cataract not included, congenital aphakia or absence of lens included) Aniridia Anomalies of iris and ciliary body: congenital anisocoria, atresia of pupil, coloboma of iris and corectopia Vitreous anomalies, congenital vitreous opacity included Fundus coloboma Coloboma of optic nerve (congenital) Congenital ptosis Congenital deformities of eyelids, ablepharon or absence of eyelid, congenital ectropion or entropion included
386.00 386.10 386.11 386.12 386.2 386.30 388.2 388.3 388.5 389.7 389.9 743.3
S/E S/E S/E S/E S/E S/E S/E S/E S/E S/E S/E S/E
743.45 743.46
S/E S/E
743.51 743.52 743.57 743.61 743.62
S/E S/E S/E S/E S/E
58
CIE-9/ ICD-9 743.9 780.4 794.12 794.13 794.15
CE/ SC S/E S/E S/E S/E S/E
Diagnstico
Diagnose
Anomalas congnitas del ojo Vrtigo-mareo EOG/ERG anormales PEV anormales PEA/pruebas de audicin anormal
Unspecified congenital anomaly of eye Dizziness and giddiness, light-headedness and vertigo ERG/EOG abnormals VEP abnormalities Abnormal auditory function studies, brainstem auditory evoked potentials abnormal findings Motion sickness
994.6
S/E
Cinetosis o mareo cinesognico
59
16. Patologa vertebral y de la mdula espinal 16. Vertebral column and spinal cord disorders
CIE-9/ ICD-9 322.9 336.0 336.1
CE/ SC S/E S/E S/E
Diagnstico
Diagnose
Aracnoiditis (qumica, secundaria a infeccin menngea) Siringomielia, siringobulbia Mielopata vascular: infarto, trombosis arterial, hematomielia, edema de mdula Degeneracin medular combinada subaguda (mielopata por dficit de vitamina B12) Mielopata (inducida por frmacos, por radiacin) Mielopata compresiva
Arachnoiditis (secondary to chemical agents, meningeal infection, etc.) Syringomyelia, syringobulbia, syringohydromyelia Myelopathy of vascular origin: infarction, arterial thrombosis, hemorrhage; includes spinal cord edema Subacute combined degeneration (myelopathy secondary to vitamin B12 deficiency) Myelopathy, secondary to drug administration, radiotherapyor any other therapeutic intervention Myelopathy, compressive (any etiology)
336.2
S/E
336.8
S/E
336.9 344.0 344.1 344.6 344.89 348.4 349.2 722 722.9 723.0
S/E S/E S/E S/E S/E 01 S/E S/E S/E S/E
Tetrapleja, tetraparesia (por lesin medular Tetraplegia, tetraparesis (secondary to adquirida) acquired spinal cord lesion) Parapleja, paraparesia (por lesin medular adquirida) Anclaje medular. Cola de caballo, cono medular Brown-Squard (sndrome) Chiari I Quistes menngeos espinales Discopata intervertebral (desplazamiento con o sin mielopata) Discitis Estenosis de canal a nivel cervical (mucopolisacaridosis, acondroplasias) Cervicalgia Sndrome cervicobraquial Estenosis de canal medular en general Lumbalgia, lumbago Paraplegia, paraparesis (secondary to acquired spinal cord lesion) Teethered spinal cord, cauda equina syndrome Brown-Squards syndrome Chiari malformation type I Arachnoid cysts (spinal location) Intervertebral disk pathology (displacement, with/without associated myelopathy) Intervertebral disk inflammatory disease Vertebral canal stenosis, cervical level (i.e.: secondary to mucopolysaccharidosis, achondroplasia...) Cervical pain, neck pain Cervicobrachial syndromes Vertebral canal stenosis, any location Lumbar pain
723.1 723.3 724.00 724.2
S/E S/E S/E S/E
60
16. Patologa vertebral y de la mdula espinal 16. Vertebral column and spinal cord disorders
CIE-9/ ICD-9 724.9
CE/ SC S/E
Diagnstico
Diagnose
Alteraciones de espalda no especificadas (fosetas lumbosacras, fstula LCR) Fracturas patolgicas de vrtebras Escoliosis en enfermedades neuromusculares Chiari II Disrafia espinal con hidrocefalia Meningocele, mielomeningocele, lipomeningocele, mielocele (espina bfida abierta)
Back localized disorders, non otherwise specified (i.e.: lubosacral dimples, CSF fistulas...) Vertebrae, pathological fractures Scoliosis, in neuromuscular or neurological conditions Chiari malformation type II (Arnold-Chiari) Spinal dysraphism with hydrocephalus Bifid spine: myelomeningocele, meningocele, lipomeningocele, etc.
733.13 737.4 741.0 741.0 741.9
S/E S/E 01 02 S/E
742.5 756.1
S/E 01
Mielodisplasias y alteraciones de la mdula Myelodysplasias, non specified otherwise espinal (diastematomielia, hidromielia) (diastematomyelia, hydromyelia, etc.) Platibasia, impresin basilar, Klippel-Feil (anomalas craneocervicales) Trastorno de la columna vertebral (espondilolistesis, espondilolisis, pinzamiento, espondilopata inflamatoria, hemivrtebra, fusin o ausencia congnita de vrtebra) Agenesia de sacro Espina bfida oculta Luxacin/subluxacin de vrtebra cervical (atlantoaxoidea) Platybasia, basilar impression, Klippel-Feil anomaly, and other craneocervical anomalies Vertebral disorder (spondylolisthesis, spondylolysis, inflammatory conditions, vertebral malformations...)
756.1
02
756.13 756.17 839.0
S/E S/E S/E
Sacral agenesis Spina bifida occulta Luxation/subluxation of cervical vetebrae (atlanto-axial, atlanto-occipital, and others)
61
17. Enfermedades neuromusculares 17. Neuromuscular diseases
CIE-9/ ICD-9 005.1 138 306.0 334.1 335.0 335.0 335.11 335.20 335.22 351.0 351.8 352.5 352.6 352.6 352.9 353.0 353.1 353.2 353.3 353.4 354.0 354.1 354.2 354.3 354.5
CE/ SC S/E S/E S/E S/E 01 02 S/E S/E S/E S/E S/E S/E 01 02 S/E S/E S/E S/E S/E S/E S/E S/E S/E S/E S/E
Diagnstico
Diagnose
Botulismo Secuelas pospolio Parlisis psicgenas Paraparesia espstica familiar Atrofia muscular espinal infantil tipo I (Werdning-Hoffmann) Atrofia muscular espinal infantil tipo II Atrofia muscular espinal infantil tipo III (Kugelberg-Welander) ELA juvenil Parlisis bulbar progresiva Facial (parlisis de Bell) Facial (otras afectaciones) Hipogloso (afectacin) Moebius Pares craneales (afectacin mltiple) Pares craneales (otras afectaciones aisladas o/y recidivantes) Plexopata braquial (no traumatismo obsttrico) Plexopata lumbosacra Races cervicales (lesin) Races dorsales (lesin) Races lumbosacras (lesin) Tnel carpiano Mediano (lesin) Cubital (lesin) Radial (lesin) Mononeuritis mltiple del miembro superior
Botulism Post-polio syndrome Psychogenic palsy Hereditary spastic paraplegias Spinal muscular atrophy type I (WerdningHoffmann) Spinal muscular atrophy type II Spinal muscular atrophy type III (KugelbergWelander) ALS (amyotrophic lateral sclerosis) Progressive bulbar paresis Facial (Bells palsy) Other disorders of facial nerve Disorders of hypoglossal nerve Moebius Other multiple cranial nerve palsies Disorder of cranial nerves (isolated and/or relapsing) Brachial plexus disorders Lumbosacral plexus disorders Cervical root disorders Thoracic root disorders Lumbosacral root disorders Carpal tunnel syndrome Other lesions of median nerve Lesion of cubital nerve Lesion of radial nerve Mononeuritis multiplex of upper limb
62
CIE-9/ ICD-9 354.8 355.0 355.3 355.79 356.0 356.1 356.1 356.2 356.8
CE/ SC S/E S/E S/E S/E S/E 01 02 S/E 01
Diagnstico
Diagnose
Otras mononeuritis del miembro superior Citico (lesin) Peroneo comn (lesin) Otras mononeuritis del miembro inferior Neuropata hereditaria sensitivomotora tipo III Neuropata hereditaria sensitivomotora tipo I Neuropata hereditaria sensitivomotora tipo II Neuropatas hereditarias sensitivoautonmicas tipos I, II, IV, V
Other mononeuropathies of upper limb Lesion of sciatic nerve Lesion peroneal nerve Other mononeuropathies of lower limb Hereditary motor and sensory neuropathy, type III Hereditary motor and sensory neuropathy, type I Hereditary motor and sensory neuropathy, type II Hereditary sensory and autonomic neuropathy, type I, II, IV, V
Neuropata hereditaria sensitivomotora tipo Hereditary motor and sensory neuropathy, IV (AR con plegamientos focales mielnicos, type IV con glaucoma) Neuropata hereditaria sensitivomotora tipo Hereditary motor and sensory neuropathy, V (con parapleja espstica) type V Neuropata hereditaria sensitivomotora VI (con atrofia ptica, retinopata, sordera) Neuropatas (otras): con afectacin SNC o pares craneales, tomaculosa, neuropata de axones gigantes, Charcot-Marie-Tooth ligado a X Guillain-Barr Polineuropata en enfermedades del colgeno Polineuropata en diabetes Polineuropata en enfermedades malignas Polineuropata en otras enfermedades Polineuropata por frmacos Polineuropata por otros txicos Polineuropata desmielinizante crnica (forma recidivante, forma neonatal) Hereditary motor and sensory neuropathy, type VI Other hereditary and idiopathic neuropathies: tomaculous neuropathy, X-linked Charcot-Marie-Tooth, giant axonal neuropathies Guillain-Barr syndrome Polyneuropathy in systemic connective vascular disorders Diabetic polyneuropathy Polyneuropathy in neoplastic disease Polyneuropathy in other diseases Drug-induced polyneuropathy Polyneuropathy due to other toxic agents Chronic inflammatory demyelinating polyradiculoneuropathy (neonatal type, relapsing type)
356.8 356.8 356.9
02 03 S/E
357.0 357.1 357.2 357.3 357.4 357.6 357.7 357.81
63
CIE-9/ ICD-9 357.82 357.9 358.0 358.1 359.0
Diagnstico
Diagnose
Polineuropata del enfermo crtico Polineuropata no especificada Miastenia grave Miasteniformes (sndromes). LambertEaton Miopata congnita (central core, nemalnica, multicore, miotubular, centronuclear, desproporcin congnita de fibras) Distrofia de cinturas (sarcoglicanopatas, calpeinopatas...)
Critical illness polyneuropathy Polyneuropathy, unspecified Myasthenia gravis Myasthenic syndromes in diseases classified elsewhere. Eaton-Lambert syndrome Congenital myopathies (central core, minicore, multicore, fiber-type disproportion, myotubular, centronuclear, nemaline) Limb-girdle muscular dystrophy
359.1 359.1 359.1 359.1 359.1
01 02 03 04 05
Distrofia facioescapulohumeral (Landouzy- Facioscapulohumeral muscular dystrophy Dejerine) Distrofia muscular (Becker) Distrofia muscular (Duchenne) Distrofia muscular congnita (Fukuyama, MCO, Walker-Warburg, deficiente en merosina o en integrina, miopata de Bethlem) Emery-Dreifuss, enfermedad Distrofia miotnica (Steinert) Miotona congnita (Thomsen) Paramiotona congnita (Eulenburg) Miotona congnita (Becker) Parlisis peridica familiar Miopata toxica o por frmacos Miopata en enfermedad endocrina Miopata inflamatoria asociada a otras enfermedades Miopata del enfermo crtico Miopata metablica Muscular dystrophy (Becker) Muscular dystrophy (Duchenne) Congenital muscular dystrophy (Fukuyama, COMS, Walker-Warburg, merosine deficiency, integrin deficiency, Bethlem myopathy) Benign scapuloperoneal muscular dystrophy with early contractures (Emery-Dreifuss) Dystrophia myotonica (Steinert) Thomsens myotonia congenita Paramyotonia congenita of von Eulenburg Congenital myotonia (Becker type) Periodic paralysis (familial) Drug-induced myopathy Myopathy in endocrine diseases Inflammatory myopathy associated with other disorders Critical care myopathy Myopathy in metabolic diseases
359.1 359.2 359.2 359.2 359.2 359.3 359.4 359.5 359.6 359.81 359.89
06 01 02 03 04 S/E S/E S/E S/E S/E 01
64
CIE-9/ ICD-9 359.89 359.9 710.3 710.4 719.7 728.0 728.88 729.82 754.89 756.81 781.2 781.7 781.99 995.86
CE/ SC 02 S/E S/E S/E S/E S/E S/E S/E S/E S/E S/E S/E S/E S/E
Diagnstico
Diagnose
Miopata mitocondrial Miopata no especificada Dermatomiositis Polimiositis idioptica Trastorno de la marcha Miositis infecciosas Rabdomilisis, mioglobinuria Calambres musculares Artrogriposis congnita Agenesia del msculo oris, Poland
Mitochondrial myopathy Myopathy, unspecified Dermatopolymyositis Polymyositis Gait difficulties Infectious myositis Rhabdomyolysis Cramps Arthrogryposis multiplex congenita Hypoplasia of depressor anguli oris muscle, Poland syndrome
Marcha de puntas tip-toe y otras anomalas Tip-toe gait and other gait abnormalities de la marcha Tetania Dolores de crecimiento Hipertermia maligna Tetany Growing pains Malignant hyperthermia
65
18. Otros 18. Others
CIE-9/ ICD-9 V61.0 V61.20 V61.8 V62.8

V65.5
Diagnstico
Diagnose
Ruptura familiar Problemas entre padres-hijos (discordia paternofilial) Nio adoptado (otras circunstancias familiares especficas) Circunstancias psicosociales adversas Normalidad neurolgica
Parental divorce Family disturbances / Altered family relationships between parents and children Adopted child (or other specific familial circumstance) Adverse familial, social and environmental situations Neurologically normal child / No evidence of neurological disease
66
19. Procedimientos diagnsticos 19. Diagnostic procedures
CIE-9/ ICD-9 01.09
CE/ SC S/E
Procedimientos diagnsticos
Diagnostic procedures
Puncin de fontanela anterior (incluye aspiracin craneal de LCR, sangre, etc.) Puncin lumbar Biopsia muscular (procedimiento) Biopsia muscular (estudio de la cadena respiratoria u otros estudios bioqumicos o de gentica molecular) Biopsia de piel (procedimiento) Biopsia de piel para cultivo de fibroblastos / Estudios bioqumicos o genticos en fibroblastos TAC (tomografa axial computarizada de cabeza) / angio-TAC Radiografa de tejido blando de cara, cabeza, cuello (adenoides, nasofaringe, senos, etc.)
Anterior fontanel puncture (includes blood aspiration, CSF sample obtaining, etc.) Lumbar puncture Biopsy, muscle (procedure) Biopsy, muscle (biochemical or molecular genetics investigations) Biopsy, skin (procedure) Biopsy, skin (for fibroblast culture) / Biochemical or molecular genetics investigations in fibroblasts CT scan, head (computed tomography) / CT angiogram Radiography, plain (soft tissues of the face, neck, skull, etc.)
03.31 04.12 83.21 83.29
S/E S/E S/E S/E
Biopsia de nervio perifrico (procedimiento) Biopsy, peripheral nerve (procedure)
86.11 86.19
S/E S/E
87.03 87.09
S/E S/E
87.16 87.17 87.2 87.21 87.44 87.62
Radiografa de huesos craneofaciales (senos Radiography, plain (craniofacial: orbit, paranasales, rbita) paranasal sinuses, etc.) Radiografa de crneo (AP, lateral, base craneal) Radiografa de columna Mielografa con contraste Radiografa de trax Trnsito esofagogastroduodenal Radiography, plain (cranial vault, skull base) Radiography, plain (vertebral column) Myelography (with contrast agent into the thecal sac) Radiography, plain (thoracic) Upper gastrointestinal tract barium examination (includes other contrast upper GI series) Radiography, plain (whole skeleton X-ray) Angiography, cerebral (carotid arteries, vertebral arteries, basilar artery) Ultrasonography, cerebral / neck (includes Doppler ultrasonography of cerebral vessels) SPECT (single-photon emission computed tomography)
88.31 88.41 88.71 88.90 88.90
S/E S/E S/E 01 02
Serie sea completa Arteriografa cerebral (arterias cartidas, arterias vertebrales, arteria basilar) Ecografa cerebral y de cuello (incluye eco-Doppler vascular) SPECT (tomografa computarizada por emisin de fotn nico)
PET (tomografa por emisin de positrones) PET (positron emission tomography)
67
CIE-9/ ICD-9 88.91
CE/ SC S/E
RM cerebral (neuroimagen por resonancia magntica), angio-RMC RM raqudea (estudio de imagen por resonancia magntica; incluye columna vertebral y mdula espinal)
MRI, cerebral (cerebral imaging study by magnetic resonance) / MRI of cerebral vessels MRI, spinal cord (spinal cord imaging study by magnetic resonance)
88.93
S/E
88.94 88.97
S/E S/E
RM musculoesqueltica (estudio por MRI, muscles and bones (imaging study of resonancia magntica de las extremidades) limbs by magnetic resonance) RM de otras reas (estudio por resonancia magntica de rbitas, cuello, cara, abdomen, etc.) Historia clnica (anamnesis) Consulta de revisin o seguimiento Consulta (primera consulta) MRI, other (imaging study of other body parts by magnetic resonance) Anamnesis / Medical record Consultation, follow-up Consultation (first consultation)
89.01 89.02 89.03 89.05 89.10 89.13 89.14 89.16 89.17 89.18 89.19 89.52 89.65 89.66 89.8 90.0 90.06
S/E S/E S/E S/E S/E S/E S/E S/E S/E S/E S/E S/E S/E S/E S/E S/E 01
Interconsulta (evaluacin solicitada por otro Medical consultation (consultation requested servicio, seccin o unidad hospitalaria) by another service, section or unit) Test de Wada (amobarbital intracarotdeo) Examen neurolgico EEG normal Transiluminacin craneal en neonato y lactante Wada test (carotid artery amobarbital infusion) Examination, neurological EEG, standard Transillumination, cranial (neonate and infant)
EEG de sueo (incluye EEG tras privacin de EEG, sleep recording (includes sleep deprivasueo y estudio polisomnogrfico) tion EEG recording and polysomnography) EEG de sueo especial (test de latencias mltiples para narcolepsia, etc.) EEG, special studies (multiple latency test for narcolepsy, etc.)
EEG monitorizacin (videogrfica, continua, EEG, monitoring (continuous, holter-EEG, holter-EEG, etc.) videographic recording, etc.) ECG (electrocardiograma) Gasometra arterial Gasometra venosa Autopsia / Necropsia LCR (examen) Biopsia cerebral (estudio anatomopatolgico) EKG / ECG (electrocardiogram) Arterial blood gas determination, blood pH Venous blood gas determination Autopsy / Necropsy CSF examination (any kind of determination or study) Biopsy, cerebral (pathologic studies)
68
CIE-9/ ICD-9 90.06 90.5 90.59 90.6 91.5 91.6 93.08 93.09
CE/ SC 02 S/E S/E S/E S/E S/E S/E S/E
Biopsia de nervio perifrico (estudio anatomopatolgico) Examen sangre (cualquier determinacin) Cariotipo y estudio citogentico Mdula sea (estudio anatomopatolgico) Biopsia muscular (estudio anatomopatolgico) Biopsia de piel y anexos (estudio anatomopatolgico) EMG (todas las tcnicas y modalidades) Velocidad de conduccin nerviosa / Electroneurogramas Test de inteligencia general (Wechsler, Standford-Binet, Terman-Merrill, etc.) Escalas para evaluacin del trastorno por dficit de atencin (CONNERS, EDAH) Pruebas para funciones cognitivas (no incluye test de inteligencia ni escalas para TDAH) Fondo de ojo Campimetra visual Electrorretinograma Electrooculograma Potenciales evocados visuales Electronistagmograma Audiometra (incluye todas las modalidades) Pruebas vestibulares Potenciales evocados auditivos Test de edrofonio Consejo gentico
Biopsy, peripheral nerve (pathologic studies) Blood test (any kind of determination or study) Karyotype / Cytogenetics Bone marrow (pathologic studies) Biopsy, muscle (pathologic study) Biopsy, skin (pathologic study) EMG (all kinds of studies) Nerve conduction velocity / Any neurophysiological test in nerves / Somatosensory evoked potential Intelligence, test of general (WISC-R, WAIS, Standford-Binet, Terman-Merrill, etc.) Attention deficit disorder, scales (Conners scale, etc.) Cognitive function test (all except general intelligence tests and attention deficit disorder scales) Funduscopic examination Campimetric study Electroretinogram Electrooculogram Evoked potentials, visual (VEP) Electronystagmography Audiometry (all modalities) Vestibular function tests Evoked potentials, brainstem auditory (BAEP) Edrophonium test Genetic counseling
94.01 94.08 94.09
S/E S/E S/E
95.03 95.05 95.21 95.22 95.23 95.24 95.41 95.44 95.46 99.29 V26.3
S/E S/E S/E S/E S/E S/E S/E S/E S/E 02 S/E
69
CIE-9/ ICD-9 V28.0 V28.3 V28.8
CE/ SC S/E S/E S/E
Cribado prenatal (amniocentesis) para la deteccin de anomalas cromosmicas Cribado para la deteccin prenatal de malformaciones del SNC por ecografa Estudio prenatal (amniocentesis para estudio de error innato metablico en feto de riesgo) Estudios metablicos especficos para fenilcetonuria Estudios metablicos especficos para galactosemia Estudios metablicos para errores innatos metablicos en sentido amplio (en sangre, orina, LCR) Test de isquemia de antebrazo (lactato) Test de lactato tras ejercicio o sobrecarga de glucosa Sobrecarga en sospecha de error innato del metabolismo Gentica molecular (FISH, bsqueda mutacional o cualquier otra tcnica), para enfermedades neurolgicas
Amniocentesis (prenatal screening for chromosomal alterations) Fetal ultrasonography (prenatal diagnosis of CNS malformations) Prenatal diagnosis, in high-risk fetus for inborn error of metabolism Laboratory studies, specific for phenylketonuria Laboratory studies, specific for galactosemia Laboratory studies, for any suspected inborn error of metabolism (in blood, urine, CSF) Overload test, for suspected inborn error of metabolism Forearm ischemic exercise test (lactate determination) Lactate determination after exercise or oral glucose overload Molecular genetics, in neurological diseases (FISH, mutational analysis, etc.)
V77.3 V77.4 V77.7
S/E S/E 01
V77.7 V77.7 V77.7 V80.0
02 03 04 S/E
70
20. Procedimientos teraputicos 20. Therapeutic procedures
CIE-9/ ICD-9 01.24
CE/ SC S/E
Procedimientos teraputicos
Therapeutic procedures
Craneotoma (descompresin, exploratoria, trepanacin,extraccin de cuerpo extrao, absceso epidural, hematoma extradural) Craneotoma (absceso/empiema subdural, absceso cerebral, higroma), con incisin de meninges Hematoma intracerebral (drenaje) Extirpacin de lesin cerebral (tumor, absceso) Fractura craneal (descompresin) Meninges (reparacin: fstula de LCR, encefalocele, etc.) Ventriculostoma (incluye vlvula para monitorizacin de la presin intracraneal, ventriculostoma del III ventrculo endoscpica)
Craniotomy (decompressive, exploratory, trepanation, foreign body extraction, epidural abscess/hematoma) Craniotomy (subdural abscess/empyema/ efussion/hygroma, cerebral abscess), with meningeal incision Removal/drainage (intracerebral hemorrhage) Extirpation, of cerebral lesion (tumour, abscess) Decompressive surgery (in cranial fracture) Dural repair surgery (encephalocele, CSF fistula, etc.) Ventriculostomy (includes intracranial pressure monitoring, 3rd venticle endoscopic ventriculostomy)
01.31
S/E
01.39 01.59 02.01 02.02 02.12 02.2
Craneosinstosis (craneoplastia reparadora) Cranioplasty (in craniostenosis)
02.32 02.34 03.09 03.1 03.51 03.59 03.92 20.95 31.1 86.06 86.94
S/E S/E S/E S/E S/E S/E S/E S/E S/E S/E S/E
Derivacin ventricular al aparato circulatorio Ventriculoatrial shunt (ventriculoatrial, ventriculocava) Derivacin ventriculoperitoneal Laminectoma descompresiva Rizotoma de races dorsales (tratamiento de la espasticidad) Mielomeningocele espinal (reparacin) Disrafia espinal (reparacin; incluye todas excepto mielomeningocele) Intratecal (inyeccin de frmacos por esta va). Excluye anestsicos Implante coclear Traqueostoma Baclofeno (implantacin de bomba de perfusin) Ventriculoperitoneal shunt Laminectomy, decompressive Rhizotomy, dorsal roots (as treatment of spasticity) Dural repair surgery (in myelomeningocele) Dural repair surgery (any type of spinal dysraphism except myelomeningocele) Intrathecal, drug administration (excludes anesthetic agents) Cochlear implant Tracheostomy Baclofen (intrathecal baclofen infusion pump)
Marcapasos vagal (y otros Vagal nerve stimulation (includes any pulse neuroestimuladores generadores de pulsos) generating neurostimulation device)
71
CIE-9/ ICD-9 92.30 93.1 93.22 93.71 93.72 93.74 93.82
Radiociruga estereotxica Fisioterapia en general (sin especificar modalidad) Rehabilitacin de la marcha Dislexia (tratamiento especfico) Logopedia (tratamiento para disfasias) Logopedia (tratamiento para defectos del habla) Escolarizacin especial (para nios con minusvalas psquicas, sensoriales o fsicas) Terapia ocupacional Presin positiva continua de la va respiratoria Terapia familiar Asesoramiento psicolgico Psicoterapia (remitir al paciente para psicoterapia sin especificar el tipo) Intubacin endotraqueal Alimentacin por sonda nasogstrica Alimentacin por gastrostoma Ventilacin mecnica continua Transfusin de concentrado de hemates Transfusin de plaquetas Transfusin de factores de coagulacin Tromblisis (infusin parenteral de agentes trombolticos) Gammaglobulina inespecfica (administracin intravenosa) Alimentacin parenteral Antdoto (administracin parenteral)
Gamma knife stereotactic radiosurgery Rehabilitation, motor / Physiotherapy (includes all modalities or methods) Rehabilitation of gait Dyslexia (specific treatment for this disorder) Logopedia / Logotherapy (in developmental dysphasias) Logopedia / Logotherapy (in speech disorders) Special educational needs (children with cognitive, sensory-perceptual or physical disabilities) Occupational therapy Positive pressure ventilation Family therapy / Psychosocial intervention Psychological assessment Psychotherapy (patient submission with/ without any specification) Endotracheal intubation Nasogastric feeding Gastrostomy feeding Mechanical ventilation, continuous Transfusion, packed red blood cells Transfusion, platelets Transfusion, coagulation factors Thrombolytic therapy (parenteral infusion of thrombolytic drugs) Gamma globulin (intravenous administration) Parenteral nutrition Antidote (parenteral administration)
93.83 93.90 94.42 94.49 94.51 96.04 96.35 96.6 96.70 99.04 99.05 99.06 99.10 99.14 99.15 99.16
S/E S/E S/E S/E S/E S/E S/E S/E S/E S/E S/E S/E S/E S/E S/E S/E
72
CIE-9/ ICD-9 99.19 99.21 99.22
CE/ SC S/E S/E S/E
Anticoagulacin parenteral (heparina, heparinoides) Antibitico (administracin parenteral) Antiinfeccioso (administracin parenteral de frmaco antiinfeccioso no antibitico: aciclovir, antifngicos, etc.) Corticoides (administracin parenteral)
Anticoagulant therapy, parenteral Antibiotic (parenteral administration) Antiinfectious agent (parenteral administration of non-antibiotic antiinfectious: acyclovir, antifungal, etc.) Corticosteroids (parenteral administration)
99.23 99.25 99.26
S/E S/E S/E
Inmunosupresor (administracin parenteral Immunosuppressive therapy (parenteral) del frmaco) Anticonvulsionante (administracin parenteral de frmaco antiepilptico para tratamiento de crisis o profilaxis de las mismas) Anticonvulsant (parenteral administration for seizure treatment or prophylaxis)
99.29
Toxina botulnica IM (u otro frmaco no Botulinum toxin administration, clasificado bajo otro concepto, administrado intramuscular / Any other drug nonIM, SC, IV) classified in other concept parenterally administered Reanimacin cardiopulmonar Plasmafresis teraputica Neuroproteccin farmacolgica (administracin de cualquier agente con este fin) Hipotermia (central, local) Resuscitation, cardiopulmonary Plasmapheresis, therapeutic Neuroprotection, pharmacological (administration of any type of drug for this purpose) Hypothermia (local, central)
99.60 99.71 99.75
S/E S/E S/E
99.81
S/E
73
21. Motivos de consulta 21. Reasons for medical consultation
CIE-9/ ICD-9 042 243 292.2 293.0 299 300.9 301.3 306.1 306.8 307.0 307.20 307.3
CE/ SC S/E S/E S/E S/E S/E S/E S/E S/E S/E S/E S/E S/E
Motivo de consulta
Reasons for medical consultation Acquired immunodeficiency syndrome (AIDS) Congenital hypothyroidism Drug overdose (illegal drugs) Acute confusional state Pervasive developmental disorder Psychiatric disorder Aggressiveness Psychogenic hyperventilation Bruxism Stuttering Tics Motor stereotypies
Sndrome de inmunodeficiencia humana (sida) Hipotiroidismo congnito Intoxicacin por drogas Sndrome confusional agudo Trastorno generalizado del desarrollo (autismo, Asperger) Trastorno psiquitrico Crisis de agresividad Hiperventilacin psicgena Bruxismo Tartamudeo Tics Estereotipias motoras (balanceos, ritmias motoras, spasmus nutans, golpeteos rtmicos de la cabeza, etc.) Terrores nocturnos, sonambulismo Pesadillas, parasomnias Trastorno de alimentacin Pica Conmocin cerebral (signos/sntomas poscontusin o encefalopata traumtica) Trastorno del comportamiento Ansiedad Dficit de atencin con/sin hiperactividad Dislexia Discalculia Trastorno del lenguaje
307.46 307.47 307.50 307.52 310.2 312.9 313.0 314.0 315.0 315.1 315.3 315.4 315.9
S/E S/E S/E S/E S/E S/E S/E S/E S/E S/E S/E S/E S/E
Sleepwalking / Somnambulism Parasomnia Eating disorder behaviour Pica Cerebral commotion (post-traumatic signs/ symptoms) Behaviour disorder Anxiety / Anxiety attack Attention deficit disorder (with/without hyperactivity) Dyslexia Dyscalculia Language or speech disorder
Torpeza motora / Mala coordinacin motora Clumsiness / Impaired motor coordination Trastorno del aprendizaje escolar Learning disorder
74
CIE-9/ ICD-9 319 333.7 342 343 343.4 344 346 348.3 348.31 348.8 349.0 351.0 352 358.9 368.0 368.1 368.2 368.4 369.00 374.3 377.00 378.5 378.9
CE/ SC S/E 03 S/E S/E S/E S/E S/E S/E 02 S/E S/E S/E S/E S/E S/E S/E S/E S/E S/E S/E S/E S/E S/E
Motivo de consulta
Reasons for medical consultation Mental retardation Drug-induced extrapyramidal side effects Hemiparesis / Hemiplegia (nonspecific), or suspicion of Cerebral palsy / Static encephalopathy with motor dysfunction Hemiparesis / Hemiplegia (acquired; excludes hemiplegic cerebral palsy) Paresis / Paralysis (all forms except cerebral palsy) Migraine Encephalopathy, acute Encephalopathy, infectious origin Brain death Post-lumbar puncture syndrome Facial nerve paralysis (includes Bells palsy) Cranial nerve disorder (any nerve or type of dysfunction) Neuromuscular disease (nonspecific), or suspicion of Visual acuity, diminished Visual perception disorder (macropsia, micropsia, photophobia, scotomata) Diplopia Visual field defect Blindness Ptosis Papilledema Strabismus / Squint Eye motility disorders
Retraso mental Reaccin extrapiramidal inducida por frmacos Hemiparesia/hemipleja no especificada (o sospecha de la misma) Parlisis cerebral infantil / Encefalopata esttica motora Hemiplejia adquirida (excluye la PCI hemipljica) Parlisis no especificada (cualquier forma excepto PCI) Migraa Encefalopata aguda Encefalopata infecciosa Muerte cerebral Sndrome pospuncin lumbar Parlisis facial perifrica Pares craneales, no facial (parlisis u otra alteracin) Enfermedad perifrica neuromuscular no especificada (sospecha de la misma) Alteracin visual (disminucin de la agudeza visual) Alteracin visual subjetiva (escotomas, fotofobia, macro/micropsia, etc.) Diplopa Campimetra visual alterada Ceguera Ptosis Edema de papila Estrabismo Alteracin de la motilidad ocular
75
CIE-9/ ICD-9 379.51 389 437.1 536.2 709.0
Motivo de consulta
Reasons for medical consultation Congenital nystagmus Deafness / Hypoacusis Hypoxic-ischaemic brain injury (non perinatal) Vomiting (cyclic, recurrent) Cutaneous manifestations, suggestive of neurocutaneous disease (caf-au-lait spots, hypomlanotic macules...) Cutaneous lesions of vascular origin (angiomata of any kind, port-wine stain) Walking difficulty / Lameness Neck pain Torticollis Lumbar pain Back pain Myalgia / Muscle pain (focal, generalized, at rest or exercise-induced, etc.) Limb pain Scoliosis Bifid spine (spinal dysraphism) Microcephaly
Nistagmo congnito Sordera / Hipoacusia Hipoxia-isquemia cerebral no neonatal Vmitos persistentes, cclicos Discroma cutnea (incluye lesiones hipocrmicas, manchas caf con leche) Discroma/trastorno vascular (incluye angiomas variados,en vino de Oporto...) Dificultad para la marcha / Cojera Dolor de cuello / Cervicalgia Tortcolis Dolor lumbar / Lumbalgia Dolor de espalda Mialgia (focal, generalizada, en reposo, o inducida por ejercicio) Dolor de una extremidad Escoliosis Espina bfida abierta (meningocele, mielomeningocele) Microcefalia
709.1 719.7 723.1 723.5 724.2 724.5 729.1 729.5 737.3 741.9 742.1 742.9 743.46 743.52 743.61 744.9 754.0 754.1 754.51
S/E S/E S/E S/E S/E S/E S/E S/E S/E S/E S/E S/E S/E S/E S/E S/E S/E S/E S/E
Malformacin del cerebro o medula espinal Brain or spinal cord malformation (includes (incluye anomala congnita del SNC) any congenital abnormality of CNS) Anisocoria (congnita, coloboma del iris) Coloboma de fondo de ojo Ptosis congnita Fenotipo peculiar facial Alteracin craneal (incluye plagiocefalia posicional, sospecha de craneosinstosis) Tortcolis congnita Pie equinovaro congnito Anisocoria (congenital, iris coloboma) Fundus coloboma Congenital ptosis Facial dysmorphism Cranial shape alteration (includes postural plagiocephaly, suspected craniosynostosis) Congenital torticollis Pes equinovarus, clubfoot (congenital)
76
CIE-9/ ICD-9 754.71 754.89 756.0 756.0 756.10 756.17 757.8 759.7 764.9 765.0 765.1 767.0
CE/ SC S/E S/E 01 03 S/E S/E S/E S/E S/E S/E S/E S/E
Motivo de consulta
Reasons for medical consultation Pes cavus Congenital multiple arthrogryposis Craniosynostosis (does not include syndromic acrocephalosyndactylias: Apert) Macrocephaly Vertebral column abnormality Spina bifida occulta Neurocutaneous syndrome (or suspicion based in cutaneous manifestations) Multiple malformation syndrome Intrauterine growth retardation Preterm neonate < 1000 g Preterm neonate 1000-2499 g Intracranial hemorrhage, neonatal (epidural, subdural, cerebral; does not include intraventricular) Brachial paralysis, neonatal/congenital Fetal distress Perinatal asphyxia, hypoxic-ischaemic encephalopathy (perinatal/neonatal) Neonatal apnea Rubella infection, congenital Cytomegalovirus infection, congenital
Pie cavo Artrogriposis mltiple congnita Craneosinstosis (excluye acrocefalosindactilia: Apert) Macrocefalia Anomala de la columna vertebral Espina bfida oculta Sndrome neurocutneo (sospecha del mismo por signos drmicos) Malformaciones congnitas mltiples. Sndrome polimalformativo Crecimiento intrauterino retardado Neonato pretrmino < 1000 g Neonato pretrmino 1000-2499 g Hemorragia intracraneal neonatal (epidural, subdural, cerebral, no incluye intraventricular) Parlisis braquial obsttrica/congnita Prdida de bienestar fetal (antiguo sufrimiento fetal) Asfixia perinatal, encefalopata hipoxicoisqumica neonatal Apnea del neonato Infeccin congnita por rubola Infeccin congnita por CMV
767.6 768.4 768.9 770.81 771.0 771.1 771.2 772.1 772.2 775.0 775.6 779.0
S/E S/E S/E S/E S/E S/E S/E S/E S/E S/E S/E S/E
Infeccin congnita (excluye rubola, CMV) Congenital infection (excludes rubella and cytomegalovirus) Hemorragia intraventricular neonatal Hemorragia subaracnoidea perinatal Hijo de madre diabtica Hipoglucemia neonatal Convulsiones neonatales Intraventricular hemorrhage, neonatal Subarachnoid hemorrhage, neonatal Infant of diabetic mother Hypoglycemia, neonatal Seizures, neonatal
77
CIE-9/ ICD-9 779.1 779.2 779.5 779.7 779.89 779.9 780.01 780.02 780.03 780.09 780.1 780.2 780.2 780.31 780.39 780.4 780.5
CE/ SC S/E S/E S/E S/E S/E S/E S/E S/E S/E S/E S/E 01 02 S/E 01 S/E S/E
Motivo de consulta
Reasons for medical consultation Hyperexcitability, neonatal Abnormal neurological signs, neonatal
Hiperexcitabilidad neurolgica Depresin neonatal. Anormalidad neurolgica neonatal Leucomalacia periventricular Hipotona congnita Neonato de riesgo neurolgico Coma Alteracin transitoria de la conciencia Estado vegetativo persistente Obnubilacin / Estupor Alucinaciones, ilusiones Espasmos del sollozo / Apnea del llanto Sncope vasovagal / Presncope Convulsin febril Crisis epilptica, convulsin Vrtigo / Mareo Trastorno del sueo (incluye insomnio, hipersomnia, alteraciones del ciclo vigiliasueo, apnea del sueo) Escalofros con la fiebre Debilidad muscular inespecfica / Fatiga Amnesia (retrgrada) Movimientos anormales (incluye temblor) Trastorno de la marcha (incluye tip-toe, excluye ataxia, cojera) Ataxia Parlisis transitoria de las extremidades Meningismo
Sndrome de abstinencia a drogas neonatal Drug abstinence syndrome, neonatal Periventricular leukomalacia Hypotonia, congenital Neonate with neurological risk factors Coma Transient or episodic alteration of consciousness Persistent vegetative state Obnubilation / Stupor Hallucinations, illusions Crying spells / Breath-holding spells Syncope / Presyncope Febrile seizure Epileptic seizure, convulsive seizure Dizziness / Vertigo / Light-headedness Sleep disorder (includes insomnia, hypersomnia, nightmares, sleep-wake cycle disorder, and sleep apnea) Febrile shivering Muscle weakness / Fatigability Amnesia Abnormal movements (includes tremor) Altered gait (includes tip-toe and others; does not include ataxia or lameness) Ataxia Transient limb paralysis Meningeal signs
780.6 780.79 780.93 781.0 781.2 781.3 781.4 781.6
78
CIE-9/ ICD-9 781.92 781.99 782.0 783.42 783.5 784.0 784.2 784.3 784.5 787.2 787.6 788.30 788.36 789.1 790.5 791.3 793.0 794.01 794.02 794.09 794.13 794.15 794.17 795.2 796.1
CE/ SC S/E S/E S/E S/E S/E S/E S/E S/E S/E S/E S/E S/E S/E S/E S/E S/E S/E S/E S/E S/E S/E S/E S/E S/E S/E
Motivo de consulta
Reasons for medical consultation Abnormal posture Leg pains Paresthesia (hyperesthesia, anaesthesia or other abnormal cutaneous sensation) Development retardation (motor, language) / Psychomotor development retardation Polydipsia Headache (includes facial pains) Mass in the head or neck Acquired aphasia Dysarthria / Altered speech Dysphagia Encopresis Enuresis Nocturnal enuresis Hepatomegaly CPK (creatine-phosphokinase), increased blood levels Myoglobinuria Cranial roentgenography: abnormal findings Cerebral ultrasonography: abnormal findings EEG, abnormal Cranial CT/MRI: abnormal findings Visual evoked potentials: abnormal findings
Postura anormal Dolor en piernas Parestesias (hiperestesia, anestesias u otra sensacin anormal cutnea) Retraso psicomotor en general Polidipsia Cefalea, dolor facial Masa o bulto en cabeza o cuello Afasia adquirida Disartria / Trastornos de la articulacin del lenguaje Disfagia Encopresis Enuresis inespecfica Enuresis nocturna Hepatomegalia CPK elevada en sangre Mioglobinuria Rx craneal: hallazgos anormales Ecografa cerebral: hallazgos anormales EEG anormal TC/RM: hallazgos anormales Potenciales evocados visuales anormales
Potenciales evocados auditivos/audiometra Brainstem auditory evoked potentials: anormales abnormal findings EMG anormal Anomala cromosmica Reflejos anormales EMG: abnormal findings Chromosomal anomaly, chromosomal aberration Myotatic reflexes, abnormal
79
CIE-9/ ICD-9 796.5 796.6 798.0 799.2 852
Motivo de consulta
Reasons for medical consultation Abnormal findings in prenatal screening (ultrasonography or other) Neonatal screening: abnormal findings Sudden infant death Irritability / Nervousness Intracranial hemorrhage, traumatic (includes all types) Cranial trauma Drug overdose (prescription drugs) Drug adverse effect Child abuse / Child neglect Cerebrospinal shunt malfunction Neurological consultation without specific reason (includes to discard neurologic disorder) Neurological examination for legal or forensic reason
Hallazgos anormales en ecografa u otra prueba prenatal Cribado neonatal: hallazgos anormales Sndrome de muerte sbita del lactante Irritabilidad / Nerviosismo Hemorragia cerebral traumtica (incluye subdural, epidural, subaracnoidea, parenquimatosa, etc.) Traumatismo craneal Intoxicacin por frmaco Efecto adverso de frmaco Maltrato / Abuso infantil Disfuncin de derivacin ventricular Consulta sin motivo especfico (incluye descartar patologa neurolgica no especificada de otro modo) Examen por motivos medicolegales
959.01 977.9 995.2 995.50 996.2 V65.9
V70.4
S/E
80
CIE-9/ ICD-9 272.5
CE/ SC 01
Diagnstico
Diagnose
Section
A-beta-lipoproteinemia Abetalipoproteinemia Inborn errors of metabolism familiar (Bassen-Kornzweig), (Bassen-Kornzweig disease), with neurological hipobetalipoproteinemia Hypobetalipoproteinemia manifestations Absceso cerebral y cerebeloso Absceso extradural de la punta de peasco o sndrome de Gradenigo Cerebral or cerebellar abscess Infectious and inflammatory diseases Infectious of apex of petrous bone (Gradenigos syndrome) Infectious and inflammatory diseases Infectious and inflammatory diseases Inborn errors of metabolism with neurological manifestations Inborn errors of metabolism with neurological manifestations Inborn errors of metabolism with neurological manifestations Inborn errors of metabolism with neurological manifestations Malformative syndromes. Chromosomical and genomic diseases Malformative syndromes. Chromosomical and genomic diseases Neuro-ophthalmology/ neurotology Morphology of neoplasms of NS Inborn errors of metabolism with neurological manifestations Developmental and behavioral disorders. Learning disabilities
324.0 383.02
S/E S/E
324.1 270.7
S/E 01
Absceso y empiema espinal Spinal abscess or empyema Aciduria glutrica tipo I Glutaric aciduria, type I
277.85
01
Aciduria glutrica tipo II
Glutaric aciduria, type II
270.3
01
Aciduria metilmalnica
Methylmalonic acidemia
270.9
01
Aciduria orgnica: isovalrica, propinica y otras (2-OH-glutarica, 3-metiglutacnica...) Acondroplasia y otras condrodistrofias Acortamiento congnito de tendn Acstico (lesin VIII par) Adenoma Adrenoleucodistrofia (Schilder) Afasia adquirida (Landau-Kleffner, afasia postraumtica o lesional)
Organic aciduria: isovaleric, propionic, and others not specified otherwise Achondroplasia and other chondrodystrophies Congenital shortening of tendon Disorders of acoustic or eighth nerve Adenoma Adrenoleukodistrophy
756.4
01
756.89
01
388.5
S/E
M8140/0 S/E 341.1 S/E
784.3
S/E
Acquired childhood aphasia (Landau-Kleffner, following brain lesion)
83
CIE-9/ ICD-9 763.9
CE/SC
Diagnstico
Diagnose
Section
S/E
Afectacin del RN por complicaciones del parto Afectacin psquica acompaante a otras enfermedades sistmicas
Complication of labour and delivery affecting fetus or newborn Psychic factors associated with diseases classified elsewhere
Fetal and perinatal neurology Developmental and behavioral disorders. Learning disabilities CNS malformations. Cranial malformations. Hydrocephalus Vertebral column and spinal cord diseases Neuromuscular diseases
316
S/E
742.2
01
Agenesia del cuerpo calloso Callosal agenesis
756.13 756.81
S/E S/E
Agenesia de sacro Agenesia del msculo oris, Poland Agresividad
Sacral agenesis Hypoplasia of depressor anguli oris muscle, Poland syndrome Aggressiveness
301.3
S/E
Developmental and behavioral disorders. Learning disabilities Neuro-ophthalmology/ neurotology Neurodegeneratives diseases. Leukodystrophies Neuro-ophthalmology / neurotology Iatrogenic, toxic, traumatic encephalopathies. Coma
270.2 330.8 368.5 780.02 724.9
2 1 S/E S/E S/E
Albinismo Alpers Alteracin de la visin cromtica Alteracin transitoria de la conciencia Alteraciones de espalda no especificadas (fosetas lumbosacras, fstula de LCR) Alteraciones de la voz: disfona, ronquera, hipernasalidad Alteraciones de refraccin y acomodacin Alteraciones del ciclo vigilia-sueo
Albinism Alpers disease Colour vision deficiencies Transient alteration of awareness
Back localized disorders, non Vertebral column and spinal otherwise specified cord diseases (i.e.: lumbosacral dimples, CSF fistulas, etc.) Voice disturbance: dysphonia, hypernasality, hoarseness Disorders of refraction and accommodation Disruptions of 24 hour sleep wake cycle, unspecified Developmental and behavioral disorders. Learning disabilities Neuro-ophthalmology / neurotology Epilepsy, paroxysmal disorders, sleep disorders
784.4
S/E
367.0 780.55
S/E S/E
84
CIE-9/ ICD-9 307.45
CE/SC
Diagnstico
Diagnose
Section
S/E
Alteraciones del ritmo circadiano (ciclo vigiliasueo) Alucinacin Alucinacin inducida por drogas Ambliopa y defectos refractivos
Sleep-wake cycle alteration, circadian rhythm disorders Hallucination Hallucinosis drug-induced Amblyopia
Epilepsy, paroxysmal disorders, sleep disorders Iatrogenic, toxic, traumatic encephalopathies. Coma Iatrogenic, toxic, traumatic encephalopathies. Coma Neuro-ophthalmology/ neurotology Inborn errors of metabolism with neurological manifestations Malformative syndromes. Chromosomical and genomic diseases Developmental and behavioral disorders. Learning disabilities Vertebral column and spinal cord diseases CNS malformations. Cranial malformations. Hydrocephalus Vascular diseases Infectious and inflammatory diseases
780.1 292.12 368.0 270.0
S/E S/E S/E S/E
Aminoacidopata (alteracin Disorders of aminoacid del trasporte): Hartnup, transport: Hartnup disease, cistinosis, otros cystinosis, etc. Amiotrofia congnita Amyotrophia congenita
756.89
02
780.93
S/E
Amnesia (retrgrada) y prdida de memoria Anclaje medular. Cola de caballo, cono medular Anencefalo
Amnesia, memory loss
344.6 740.0
S/E S/E
Teethered spinal cord, cauda equina syndrome Anencephalus
437.3 325
S/E S/E
Aneurisma arterial intracraneal Angetis, flebitis, tromboflebitis sptica de senos venosos intracraneales Angelman: delecin 15q11-q13 materna Angiofibroma Angioqueratoma Anillo de Kayser-Fleischer
Intracranial arterial aneurysms Infectious arteritis or phlebitis (includes septic thrombophlebitis of cerebral venous sinuses) Angelman syndrome, deletion 15q11-q13 maternal Angiofibroma Angiokeratoma Kayser-Fleischer ring
758.33
01
Malformative syndromes. Chromosomical and genomic diseases Morphology of neoplasms of NS Morphology of neoplasms of NS Neuro-ophthalmology/ neurotology
M9160/0 S/E M9141/0 S/E 371.14 S/E
85
CIE-9/ ICD-9 743.45 379.4
CE/SC
Diagnstico
Diagnose
Section
S/E S/E
Aniridia Anisocoria y otros problemas pupilares (adquiridos) Anomalas cerebrales (otras) Anomalas congnitas del miembro superior (otras) Anomalas congnitas del ojo Anomalas congnitas del prpado (otras)
Aniridia
Neuro-ophthalmology/ neurotology
Anomalies of pupillary Neuro-ophthalmology/ function (acquired anisocoria neurotology and others included) Anomalies of brain (others) CNS malformations. Cranial malformations. Hydrocephalus Malformative syndromes. Chromosomical and genomic diseases Neuro-ophthalmology/ neurotology
742.4
05
755.59
01
Congenital anomalies of upper limb (any type) Unspecified congenital anomaly of eye
743.9 743.62
S/E S/E
Congenital deformities Neuro-ophthalmology/ of eyelids, ablepharon or neurotology absence of eyelid, congenital ectropion or entropion included Other disorders of optic disc, congenital coloboma included Neuro-ophthalmology/ neurotology
377.2
S/E
Anomalas de disco ptico, incluye coloboma del disco ptico (congnito) Anomalas del iris y cuerpo ciliar (otras): anisocoria congnita, atresia de pupila, coloboma de iris Anomalas vtreas, incluye opacidad vtrea congnita Anorexia nerviosa
743.46
S/E
Anomalies of iris and ciliary Neuro-ophthalmology/ body: congenital anisocoria, neurotology atresia of pupil, coloboma of iris and corectopia Vitreous anomalies, congenital vitreous opacity included Anorexia nervosa Neuro-ophthalmology/ neurotology Developmental and behavioral disorders. Learning disabilities Developmental and behavioral disorders. Learning disabilities Malformative syndromes. Chromosomical and genomic diseases Fetal and perinatal neurology
743.51
S/E
307.1
S/E
313.0
S/E
Ansiedad (trastorno)
Anxiety disorder
755.55
S/E
Apert o acrocefalosindactilia Apert syndrome, acrocephalosyndactyly Apnea del neonato Apnea of newborn
770.81
S/E
86
CIE-9/ ICD-9 379.58
CE/SC
Diagnstico
Diagnose
Section
S/E
Apraxia oculomotora, incluye sndrome de Cogan
Deficiencies of smooth pursuit movements (Cogan syndrome/apraxia oculomotora included) Arachnoiditis (secondary to chemical agents, meningeal infection, etc.) Arthrogryposis multiplex congenita Birth asphyxia Birth asphyxia with neurological impact. Hypoxic-ischemic encephalopathy Asymetry of face or postural plagiocephaly Asperger syndrome
322.9
S/E
Aracnoiditis (qumica, secundaria a infeccin menngea) Artrogriposis congnita Asfixia al nacer Asfixia grave al nacer (con repercusin neurolgica). EHI Asimetra craneal (facial) o plagiocefalia postural Asperger
Vertebral column and spinal cord diseases Neuromuscular diseases Fetal and perinatal neurology Fetal and perinatal neurology
754.89 768.9 768.5
S/E S/E S/E
754.0
01
CNS malformations. Cranial malformations. Hydrocephalus Developmental and behavioral disorders. Learning disabilities Morphology of neoplasms of NS Morphology of neoplasms of NS Morphology of neoplasms of NS Morphology of neoplasms of NS Morphology of neoplasms of NS Morphology of neoplasms of NS Cerebral palsy. Movement disorders
299.8
S/E
M9430/3 S/E M9400/3 S/E M9401/3 S/E M9421/1 S/E M9384/1 S/E M9412/1 S/E 781.3 S/E
Astroblastoma Astrocitoma Astrocitoma anaplsico Astrocitoma piloctico
Astroblastoma Astrocytoma Astrocytoma, anaplastic Pilocytic astrocytoma
Astrocitoma subependimario Subependymal giant cell de clulas gigantes astrocytoma Astrocitoma/ganglioglioma Desmoplastic infantile desmoplsico infantil astrocytoma Ataxia aguda Acute cerebellar ataxia
87
CIE-9/ ICD-9 334.4
CE/SC
Diagnstico
Diagnose
Section
S/E
Ataxia asociada a ECM, encefalopata degenerativa, encefalopatas epilpticas
Cerebellar ataxia in inborn error of metabolism, degenerative disease, epileptic encephalopathy...
Neurodegeneratives diseases. Leukodystrophies
334.2
S/E
Ataxia con atrofia cerebelosa Primary cerebellar o degeneracin cerebelosa degeneration or ataxia with primaria cerebellar atrophy Ataxia con incoordinacin oculoceflica Ataxia de Friedreich Ataxia peridica hereditaria Ataxia telangiectasia Ataxias cerebelosas autosmicas dominantes, ligadas al sexo Atrofia cerebral Cerebellar ataxia with oculomotor apraxia Friedreichs ataxia Episodic ataxia
Neurodegeneratives diseases. Leukodystrophies Neurodegeneratives diseases. Leukodystrophies Neurodegeneratives diseases. Leukodystrophies Neurodegeneratives diseases. Leukodystrophies
334.8 334.0 334.8 334.8 334.8
2 S/E 3 4 1
Ataxia telangiectasia, ataxia Neurodegeneratives telangiectasia-like disorder diseases. Leukodystrophies Cerebellar ataxia, autosomal Neurodegeneratives recessive, dominant, X-linked diseases. Leukodystrophies (includes Joubert and other similar disorders) Cerebral atrophy CNS malformations. Cranial malformations. Hydrocephalus
742.4
01
335.0
01
Atrofia muscular espinal infantil tipo I (WerdningHoffmann) Atrofia muscular espinal infantil tipo II Atrofia muscular espinal infantil tipo III (KugelbergWelander) Atrofia ptica Atrofia ptica hereditaria, incluye atrofia ptica de Leber y hereditaria dominante Ausencias atpicas
Spinal muscular atrophy Neuromuscular diseases type I (Werdning-Hoffmann) Spinal muscular atrophy type II Spinal muscular atrophy type III (KugelbergWelander) Optic atrophy Hereditary optic atrophy, dominant hereditary and Lebers optic atrophy included Atypical absences Neuromuscular diseases Neuromuscular diseases
335.0 335.11
02 S/E
377.1 377.16
S/E S/E
Neuro-ophthalmology/ neurotology Neuro-ophthalmology/ neurotology
345.0
01
Epilepsy, paroxysmal disorders, sleep disorders
88
CIE-9/ ICD-9 345.0 345.0 345.0 299.0
CE/SC
Diagnstico
Diagnose
Section
02 04 03 S/E
Ausencias infantiles Ausencias juveniles Ausencias mioclnicas Autismo
Childhood absence epilepsy Juvenile absence epilepsy Myoclonic absences Autism
Epilepsy, paroxysmal disorders, sleep disorders Epilepsy, paroxysmal disorders, sleep disorders Epilepsy, paroxysmal disorders, sleep disorders Developmental and behavioral disorders. Learning disabilities Cerebral palsy. Movement disorders Inborn errors of metabolism with neurological manifestations Inborn errors of metabolism with neurological manifestations Inborn errors of metabolism with neurological manifestations Neuro-ophthalmology/ neurotology Cerebral palsy. Movement disorders Neuromuscular diseases Vertebral column and spinal cord diseases Epilepsy, paroxysmal disorders, sleep disorders Developmental and behavioral disorders. Learning disabilities Neuromuscular diseases Cerebral palsy. Movement disorders
307.9 277.85
S/E 03
Autoestimulacin Self-stimulation, infant (masturbacin del lactante) masturbation Beta-oxidacin de los cidos grasos (trastorno del metabolismo) Biotina (trastorno del metabolismo) Biotinidasa (dficit) Beta-oxidation of fatty acids, congenital disorder Biotine (inborn error of metabolism of) Biotinidase deficiency
266.2
02
277.6
S/E
374.46 333.81 005.1 344.89 306.8 307.51
Blefarofimosis Blefarospasmo Botulismo
Blepharophimosis Blepharospasm Botulism
Brown-Squard (sndrome) Brown-Squards syndrome Bruxismo Bulimia Bruxism Bulimia (eating disorder)
729.82 275.40
S/E S/E
Calambres musculares Calcificacin de ncleos basales cerebrales
Cramps Basal ganglia calcifications
89
CIE-9/ ICD-9 270.9
CE/SC
Diagnstico
Diagnose
Section
02
Canavan o degeneracin esponjosa del cerebro Carbohidratos (glicerocinasa), trastorno del metabolismo Carcinoma del plexo coroideo Carcinoma embrionario
Canavan disease (aspartate acylase deficiency) Carbohydrates, congenital disorder of metabolism Choroid plexus carcinoma Embryonal carcinoma
Inborn errors of metabolism with neurological manifestations Inborn errors of metabolism with neurological manifestations Morphology of neoplasms of NS Morphology of neoplasms of NS Inborn errors of metabolism with neurological manifestations Inborn errors of metabolism with neurological manifestations Inborn errors of metabolism with neurological manifestations
271.9
02
M9390/3 S/E M9070/3 S/E 277.85 02
Carnitil palmitoil transferasa Carnitine palmitoyl (dficit de CPT) transferase deficiency Carnitina (trastorno del metabolismo) Carnosinemia Carnitine, disorder of metabolism Carnosinemia
277.82
S/E
270.8
01
743.3
S/E
Catarata congnita y anomalas del cristalino: afaquia congnita o ausencia de cristalino Catarata infantil Cefalea Cefalea crnica diaria Cefalea histamnica Cefalea pospuncin Cefalea secundaria Cefalea tensional
Congenital cataract and lens Neuro-ophthalmology/ anomalies (infantile cataract neurotology not included, congenital aphakia or absence of lens included) Infantile cataract Headache Chronic daily headache Histamine cephalalgia Headache, post-lumbar puncture Secondary headache Tension headache Neuro-ophthalmology/ neurotology Headache and related disorders Headache and related disorders Headache and related disorders Headache and related disorders Headache and related disorders Headache and related disorders
366.0 784.0 307.81 346.2 349.0 784.0 307.81
S/E 01 01 04 S/E 02 02
90
CIE-9/ ICD-9 307.80 377.75 950.9 368.6 369.00
CE/SC
Diagnstico
Diagnose
Section
S/E S/E S/E S/E S/E
Cefaleas de origen psiquitrico Ceguera cortical Ceguera cortical traumtica Ceguera nocturna o nictalopa
Psychogenic pain (headache) Cortical blindness Traumatic cortical blindness Night blindness
Headache and related disorders Neuro-ophthalmology/ neurotology Iatrogenic, toxic, traumatic encephalopathies. Coma Neuro-ophthalmology/ neurotology
Ceguera y baja visin (no Impairment level not further Neuro-ophthalmology/ incluye defectos refractivos) specified (blindness and low neurotology vision included, disorders of refraction not included) Celulitis orbitaria Cerebelitis posvaricelosa Ceroidolipofuscinosis Orbital cellulitis Varicella cerebellar ataxia Ceroid lipofuscinosis, neuronal Cervical pain, neck pain Ketolisis, congenital deficiency CHARGE association Infectious and inflammatory diseases Infectious and inflammatory diseases Inborn errors of metabolism with neurological manifestations Vertebral column and spinal cord diseases Inborn errors of metabolism with neurological manifestations Malformative syndromes. Chromosomical and genomic diseases Neurocutaneous Vertebral column and spinal cord diseases Vertebral column and spinal cord diseases Neuromuscular diseases
376.01 052.7 330.1
S/E S/E 01
723.1 277.87
S/E 01
Cervicalgia Cetlisis (defecto)
759.89
01
CHARGE
288.2 348.4 741.0 355.0
S/E 01 01 S/E
Chediak-Higashi Chiari I Chiari II Citico (lesin)
Chediak-Higashi syndrome Chiari malformation type I Chiari malformation type II (Arnold-Chiari) Lesion of sciatic nerve
91
CIE-9/ ICD-9 270.6
CE/SC
Diagnstico
Diagnose
Section
S/E
Ciclo de la urea (trastorno): sndrome HHH (hiperamonemia, hiperornitinemia, homocitrulinuria), aciduria argininosuccnica Cinetosis o mareo cinesognico
Urea cycle disorder: HHH syndrome, argininosuccinic aciduria, etc.
Inborn errors of metabolism with neurological manifestations
994.6 V62.8 771.1 759.89
S/E S/E S/E 02
Motion sickness
Neuro-ophthalmology/ neurotology Others Fetal and perinatal neurology Malformative syndromes. Chromosomical and genomic diseases Neurocutaneous Malformative syndromes. Chromosomical and genomic diseases Malformative syndromes. Chromosomical and genomic diseases Iatrogenic, toxic, traumatic encephalopathies. Coma Neuro-ophthalmology/ neurotology Neuro-ophthalmology/ neurotology Neuro-ophthalmology/ neurotology Iatrogenic, toxic, traumatic encephalopathies. Coma Iatrogenic, toxic, traumatic encephalopathies. Coma Iatrogenic, toxic, traumatic encephalopathies. Coma
Circunstancias psicosociales Adverse familial, social and adversas environmental situations Citomegalovirus congnito Cockayne Congenital cytomegalovirus infection Cockayne syndrome
757.39 759.89
01 03
Cockayne-Weber (epidermolisis bullosa) Coffin-Lowry
Cockayne-Weber (epidermolysis bullosa) Coffin-Lowry syndrome
759.89
04
Cohen
Cohen syndrome
952.4 743.52 377.23 743.57 780.01 250.3 572.2
S/E S/E S/E S/E S/E S/E S/E
Cola de caballo (lesin traumtica) Coloboma de fondo de ojo Coloboma del disco ptico (adquirido)
Cauda equina (traumatic injury) Fundus coloboma Coloboma of optic disc (acquired)
Coloboma del nervio ptico Coloboma of optic nerve (congnito) (congenital) Coma Coma diabtico cetoacidtico Coma heptico (encefalopata heptica) Coma Diabetic coma (with ketoacidosis) Hepatic coma (hepatic encephalopathy)
92
CIE-9/ ICD-9 251.0 345.3 349.82
CE/SC
Diagnstico
Diagnose
Section
S/E 02 S/E
Coma hipoglucmico Coma poscrtico (tras crisis epilptica) Coma txico (accidental, drogas de abuso, frmacos...)
Hypoglycemic coma
Iatrogenic, toxic, traumatic encephalopathies. Coma
Epileptic coma (after seizure) Iatrogenic, toxic, traumatic encephalopathies. Coma Coma caused by poisoning (accident, drug abuse, biological or chemical substances, etc.) / Toxic encephalopathy Traumatic coma Uremic coma Complication of migraine Cerebral concussion Iatrogenic, toxic, traumatic encephalopathies. Coma
850.5 588.89 346.9 850.0 850.4
S/E S/E S/E S/E S/E
Coma traumtico Coma urmico Complicaciones de la migraa Conmocin cerebral Conmocin cerebral con coma profundo sin recuperacin (TCE) Conmocin cerebral con coma prolongado con recuperacin (TCE) Conmocin cerebral con prdida de conocimiento transitorio (TCE) Contusin cerebelosa (o de pednculos cerebrales) Contusin cerebral cortical Contusin cerebral de otras estructuras (meninges) Conversin o trastorno conversivo: parlisis, sordera, ceguera Convulsin febril y estatus febril
Iatrogenic, toxic, traumatic encephalopathies. Coma Iatrogenic, toxic, traumatic encephalopathies. Coma Headache and related disorders Iatrogenic, toxic, traumatic encephalopathies. Coma
Cerebral concussion with Iatrogenic, toxic, traumatic deep coma without recovery encephalopathies. Coma Cerebral concussion with prolonged coma and recovery Cerebral concussion with transitory loss of consciousness (brain injury) Cerebellar concussion Cerebral cortical concussion Cerebral concussion of other structures (meninges) Conversion disorder: palsy, blindness, deafness Febrile seizures and febrile status Iatrogenic, toxic, traumatic encephalopathies. Coma Iatrogenic, toxic, traumatic encephalopathies. Coma Iatrogenic, toxic, traumatic encephalopathies. Coma Iatrogenic, toxic, traumatic encephalopathies. Coma Iatrogenic, toxic, traumatic encephalopathies. Coma Developmental and behavioral disorders. Learning disabilities Epilepsy, paroxysmal disorders, sleep disorders
850.3
S/E
850.1
S/E
851.4 851.0 851.8 300.11
S/E S/E S/E S/E
780.31
S/E
93
CIE-9/ ICD-9 345.51
CE/SC
Diagnstico
Diagnose
Section
01
Convulsiones infantiles benignas familiares (Vigevano) Convulsiones infantiles benignas no familiares (Watanabe) Convulsiones neonatales (otras) Convulsiones neonatales familiares y no familiares benignas Convulsiones neonatales sintomticas por EHI, hipoglucemia, hipocalcemia, ECM Cordoma Corea familiar benigna
Benign familial infantile seizures Benign infantile seizures nonfamilial Neonatal seizures (other types, not specified) Benign familial and nonfamilial neonatal seizures Symptomatic neonatal seizures (hypoglicemia, IHE, hypocalcemia, etc.) Chordoma Benign hereditary chorea
Epilepsy, paroxysmal disorders, sleep disorders Epilepsy, paroxysmal disorders, sleep disorders Epilepsy, paroxysmal disorders, sleep disorders Epilepsy, paroxysmal disorders, sleep disorders Epilepsy, paroxysmal disorders, sleep disorders
345.50
01
779.0 779.0
05 01
779.0
02
M9370/3 S/E 333.5 333.5 392.0 333.5 02 01 S/E 03
Morphology of neoplasms of NS Cerebral palsy. Movement disorders Cerebral palsy. Movement disorders Cerebral palsy. Movement disorders Cerebral palsy. Movement disorders Cerebral palsy. Movement disorders Morphology of neoplasms of NS Neuro-ophthalmology/ neurotology Malformative syndromes. Chromosomical and genomic diseases Neuro-ophthalmology/ neurotology
Corea inducida por frmacos Drug induced chorea Corea reumtica de Sydenham Sydenham chorea, rheumatic chorea
Coreas (otras): corea y SAFL, Chorea (any etiology): lupus, vasculitis antiphospholipid syndrome, lupus, vasculitis... Coreoatetosis paroxstica cinesiognica Coriocarcinoma Coriorretinitis por toxoplasma Cornelia de Lange Paroxysmal kinesigenic choreoathetosis Choriocarcinoma Chorioretinitis due to toxoplasmosis Cornelia de Lange syndrome
333.5
04
M9100/3 S/E 130.2 759.89 S/E 05
377.7
S/E
Corteza visual, afectacin
Disorders of visual cortex (agnosia and hallutination not included)
94
CIE-9/ ICD-9 756.2
CE/SC
Diagnstico
Diagnose
Section
S/E
Costilla cervical
Cervical rib
Malformative syndromes. Chromosomical and genomic diseases Morphology of neoplasms of NS CNS malformations. Cranial malformations. Hydrocephalus CNS malformations. Cranial malformations. Hydrocephalus Inborn errors of metabolism with neurological manifestations Fetal and perinatal neurology Infectious and inflammatory diseases Malformative syndromes. Chromosomical and genomic diseases Epilepsy, paroxysmal disorders, sleep disorders Epilepsy, paroxysmal disorders, sleep disorders Epilepsy, paroxysmal disorders, sleep disorders Epilepsy, paroxysmal disorders, sleep disorders
M9350/1 S/E 740.1 S/E
Craneofaringioma Craneorraquisquisis
Craniopharyngioma Craniorrachischisis
756.0
01
Craneosinstosis
Craniosynostosis
270.8
03
Creatina cerebral (dficit)
Creatine deficiency, cerebral
764.9 046.1 758.31
S/E S/E S/E
Crecimiento intrauterino retardado Creutzfeldt-Jakob Cri du Chat: delecin 5p
Fetal growth retardation Creutzfeldt-Jakob disease Cri du Chat syndrome, deletion 5p Drug or other chemically induced seizures Immediate and early posttraumatic seizures Migrating partial seizures of early infancy Symptomatic neonatal seizures (hypoglicemia, IHE, hypocalcemia...) Benign infantile convulsions associated with mild gastroenteritis Seizures in intracranial hypertension (hydrocephalus, tumours)
780.39 780.39 345.41 780.39
02 03 01 04
Crisis inducidas por frmacos o drogas Crisis inmediatas a traumatismo Crisis parciales migratorias de la infancia temprana Crisis por accidente cerebral agudo (hipxico, hemorrgico, inflamatorio, infeccioso...) Crisis por gastroenteritis
780.39
05
Epilepsy, paroxysmal disorders, sleep disorders Epilepsy, paroxysmal disorders, sleep disorders
780.39
06
Crisis por hipertensin endocraneal (hidrocefalia, tumores)
95
CIE-9/ ICD-9 345.91
CE/SC
Diagnstico
Diagnose
Section
S/E
Crisis secundarias a: ECM, celiaqua, infecciones peri/posnatales, TCE, enfermedad gentica o cuadro malformativo conocido Crisis nica o grupo de crisis aisladas o raramente repetitivas Cromosomopatas autosmicas numricas, estructurales o monognicas (cromosoma 20 anillo, trisoma 9...) Cromosomopatas gonosmicas, numricas, estructurales o monognicas (otras) Crouzon
Seizures in inborn errors of Epilepsy, paroxysmal metabolism, coeliac disease, disorders, sleep disorders chromosomal abnormalities and cerebral malformations
780.39
01
Single seizure or isolated clusters of seizures
758.5
S/E
Malformative syndromes. Autosomic chromosomopaties: numeric, Chromosomical and genomic diseases structural or monogenic (ring chromosome 20, trisomy 9...) Malformative syndromes. Gonosomic chromosomopaties: numeric, Chromosomical and genomic diseases structurals or monogenics (others) Crouzon syndrome CNS malformations. Cranial malformations. Hydrocephalus Neuromuscular diseases
758.81
S/E
756.0
02
354.2 997.09
S/E S/E
Cubital (lesin) Dao cerebral secundario a procedimiento quirrgico o mdico (hemorragia o infarto) Dao cerebral secundario a procedimiento quirrgico o mdico (lesin anxica)
Lesion of cubital nerve
Nervous system lesion Iatrogenic, toxic, traumatic caused by surgical or medical encephalopathies. Coma procedure (cerebrovascular infarction or hemorrhage) Nervous system lesion Iatrogenic, toxic, traumatic caused by surgical or medical encephalopathies. Coma procedure
997.01
S/E
728.2
S/E
Debilidad muscular y atrofia Muscular wasting or atrophy Developmental and muscular not elsewhere classified behavioral disorders. Learning disabilities Defectos del campo visual Deficiencia mltiple de carboxilasas (MCAD) Visual field defects Multiple carboxylases deficiency (MCAD) Neuro-ophthalmology/ neurotology Inborn errors of metabolism with neurological manifestations
368.4 270.9
S/E 03
96
CIE-9/ ICD-9 331.7
CE/SC
Diagnstico
Diagnose
Section
S/E
Degeneracin cerebral por enf. cerebrovascular, neoplasia, hidrocefalia, deficiencia vitamnica o nutricional Degeneracin cerebral secundaria a quimioterepia antineoplsica (con o sin RT) Degeneracin espinocerebelosa Degeneracin estriatongrica Degeneracin medular combinada subaguda (mielopata por dficit de vitamina B12) Degeneracin o regresin neurolgica de etiologa desconocida Degeneracin olivopontocerebelosa Delecin 18p/q
Cerebral degeneration in cerebrovascular disease, neoplastic disease, hydrocephalus, vitamin or nutritional deficiency
E933.1
S/E
Cerebral degeneration caused Iatrogenic, toxic, traumatic by chemotherapy (with or encephalopathies. Coma without radiotherapy) Spinocerebellar ataxia/ degeneration Striatopallidal disease Subacute combined degeneration (myelopathy secondary to vitamin B12 deficiency) Cerebral degenerative disease in childhood Neurodegeneratives diseases. Leukodystrophies Cerebral palsy. Movement disorders Vertebral column and spinal cord diseases
334.9 333.0 336.2
S/E 01 S/E
330.9
S/E
333.0 758.39
02 01
Olivopontocerebellar atrophy Cerebral palsy. Movement disorders Deletion 18p/q Malformative syndromes. Chromosomical and genomic diseases
758.39
02
Deleciones autosmicas (otras) Depsitos corneanos asociados con trastornos metablicos (otros) Depresin neurolgica neonatal Derivacin ventricular (complicacin mecnica) Derivacin ventricular (complicacin) Dermatomiositis
Autosomal deletions (others) Malformative syndromes. Chromosomical and genomic diseases Other corneal deposits associated with metabolic disorders Cerebral depression in fetus or newborn Ventriculoperitoneal shunt malfunction Ventriculoperitoneal shunt (complication) Dermatopolymyositis Neuro-ophthalmology/ neurotology Fetal and perinatal neurology Iatrogenic, toxic, traumatic encephalopathies. Coma Iatrogenic, toxic, traumatic encephalopathies. Coma Neuromuscular diseases
371.15
S/E
779.2 996.2 349.1 710.3
S/E S/E S/E S/E
97
CIE-9/ ICD-9 341.9
CE/SC
Diagnstico
Diagnose
Section
Desmielinizacin no especificada del SNC DiGeorge
Demyelinating disease of central nervous system, unspecified DiGeorge syndrome
Neurodegeneratives diseases. Leukodystrophies Malformative syndromes. Chromosomical and genomic diseases Neuro-ophthalmology/ neurotology Developmental and behavioral disorders. Learning disabilities Developmental and behavioral disorders. Learning disabilities Cerebral palsy. Movement disorders Vertebral column and spinal cord diseases
279.11
S/E
368.2 784.5
S/E S/E
Diplopa Disartrias
Diplopia Dysarthria, slurred speech
315.1
S/E
Discalculia
Dyscalculia
333.82 722.9 722
02 S/E S/E
Discinesia tarda Discitis Discopata intervertebral (desplazamiento con o sin mielopata) Diseccin arteria vertebral Diseccin carotdea Disfasia expresiva
Tardive dyskinesia Intervertebral disk inflammatory disease
Intervertebral disk pathology Vertebral column and spinal (displacement, with/without cord diseases associated myelopathy) Vertebral artery dissection Carotid artery dissection Vascular diseases Vascular diseases
443.24 443.21 315.31
S/E S/E 02
Expressive language disorder Developmental and behavioral disorders. Learning disabilities Developmental and behavioral disorders. Learning disabilities Developmental and behavioral disorders. Learning disabilities Developmental and behavioral disorders. Learning disabilities
315.32
S/E
Disfasia mixta: comprensiva Mixed receptive-expressive y expresiva language disorder Dislexia Dyslexia
315.0
S/E
312.20
S/E
Disocial (trastorno)
Conduct disorder, dissocial personality disorder
98
CIE-9/ ICD-9 755.59
CE/SC
Diagnstico
Diagnose
Section
02
Disstosis cleidocraneal
Cleidocranial dysostosis
Malformative syndromes. Chromosomical and genomic diseases Malformative syndromes. Chromosomical and genomic diseases CNS malformations. Cranial malformations. Hydrocephalus CNS malformations. Cranial malformations. Hydrocephalus Vertebral column and spinal cord diseases Cerebral palsy. Movement Cerebral palsy. Movement disorders Cerebral palsy. Movement disorders Cerebral palsy. Movement disorders Cerebral palsy. Movement disorders Epilepsy, paroxysmal disorders, sleep disorders Cerebral palsy. Movement disorders Cerebral palsy. Movement disorders
756.5
S/E
Displasia sea con afectacin neurolgica Displasia septoptica
Skeletal dysplasia with neurological manifestations Septo-optic dysplasia
742.2
03
742.2
02
Displasias o hipoplasias o agenesias de parte del cerebro Disrafia espinal con hidrocefalia Distona de inicio tardo Distona de torsin idioptica
Dysplasia or hypoplasia or agenesis of part of brain Spinal dysraphism with hydrocephalus Late onset dystonia Idiopathic torsion dystonia
741.0 333.7 333.6 333.8 333.82 333.89 780.59 333.7 333.7
02 04 S/E S/E 01 S/E 01 03 01
Distona focal sin especificar Focal or segmental dystonia Distona orofacial y disfona Distona paroxstica familiar Distona paroxstica nocturna Distona por frmacos Distona secundaria a ECM: alteracin de NT, pterinas, dficit de creatina cerebral Distona sintomtica Orofacial dyskinesia Familial paroxysmal dystonia Nocturnal paroxismal dystonia Drug induced dystonia Dystonia, secondary to neurometabolic diseases.
333.7 333.90
02 01
Symptomatic dystonia
Cerebral palsy. Movement disorders
Distona transitoria: distona Transient idiopathic dystonia Cerebral palsy. Movement paroxstica transitoria del disorders lactante
99
CIE-9/ ICD-9 359.1
CE/SC
Diagnstico
Diagnose
Section
01
Distrofia cinturas (sarcoglicanopatias, calpeinopatas...) Distrofia facioescapulohumeral (Landouzy-Dejerine) Distrofia miotnica (Steinert) Distrofia muscular (Becker) Distrofia muscular (Duchenne) Distrofia muscular congnita (Fukuyama, MCO, Walker-Warburg, deficiente en merosina o en integrina, miopata de Bethlem) Distrofia neuroaxonal infantil (Schindler) Dolicocefalia
Limb-girdle muscular dystrophy Facioscapulohumeral muscular dystrophy Dystrophia myotonica (Steinert) Muscular dystrophy (Duchenne) Congenital muscular dystrophy (Fukuyama, COMS, Walker-Warburg, merosine deficiency, integrin deficiency, Bethlem myopathy) Neuroaxonal dystrophy (Schindler disease) Dolichocephaly
Neuromuscular diseases
359.1
02
359.2 359.1 359.1 359.1
01 03 04 05
Muscular dystrophy (Becker) Neuromuscular diseases Neuromuscular diseases Neuromuscular diseases
330.8 754.0
2 02
Neurodegeneratives diseases. Leukodystrophies CNS malformations. Cranial malformations. Hydrocephalus Neuromuscular diseases Malformative syndromes. Chromosomical and genomic diseases Neuro-ophthalmology/ neurotology Neuro-ophthalmology/ neurotology Malformative syndromes. Chromosomical and genomic diseases Iatrogenic, toxic, traumatic encephalopathies. Coma
781.99 758.0
S/E S/E
Dolores de crecimiento Down: trisoma 21
Growing pains Down syndrome, trisomy 21
377.21 378.71 759.89
S/E S/E 06
Drusas del disco ptico Duane Dubowitz
Drusen of optic disc Duanes syndrome Dubowitz syndrome
348.5
S/E
Edema cerebral (de cualquier etiologa)
Cerebral edema (any etiology)
100
CIE-9/ ICD-9 758.2
CE/SC
Diagnstico
Diagnose
Section
S/E
Edwards: trisoma 18
Edwards syndrome, trisomy 18 Abnormal EEG Adverse effect of biological, correct substance properly administered Maternal anesthesia and analgesia affecting fetus or newborn Maternal drug reactions and intoxications specific to newborn
Malformative syndromes. Chromosomical and genomic diseases Epilepsy, paroxysmal disorders, sleep disorders Iatrogenic, toxic, traumatic encephalopathies. Coma
794.02 E947.9
S/E S/E
EEG anormal Efecto adverso de un frmaco (administrado de forma apropiada y dosis correctas) Efecto de la analgesia y anestesia maternas sobre el feto/RN Efecto sobre el feto o RN de la administracin materna de frmacos
763.5
S/E
Fetal and perinatal neurology Fetal and perinatal neurology Iatrogenic, toxic, traumatic encephalopathies. Coma Malformative syndromes. Chromosomical and genomic diseases Neuromuscular diseases Neuromuscular diseases
779.4
S/E
989.5 756.83
S/E S/E
Efecto txico de: mordedura Bite of snakes, spiders, etc., de serpientes, araas, etc. toxic effect Ehlers-Danlos Ehlers-Danlos syndrome
335.20 359.1
S/E 06
ELA juvenil Emery-Dreifuss, enfermedad
ALS (amyotrophic lateral sclerosis) Benign scapuloperoneal muscular dystrophy with early contractures (EmeryDreifuss) Subdural or extradural empyema Herpes virus encephalitis
324.9 054.3 323.4
S/E S/E S/E
Empiema subdural, extradural Encefalitis herptica Encefalitis infecciosas (otras): cisticercosis, hidatidosis del SNC, otros parsitos Encefalitis postinfecciosa Encefalitis postsarampin
Infectious and inflammatory diseases Infectious and inflammatory diseases
Other infectious encephalitis: Infectious and inflammatory neurocysticercosis, cerebral diseases echinococcosis, other parasitic infestation Postinfectious encephalitis Measles encephalitis Infectious and inflammatory diseases Infectious and inflammatory diseases
323.6 055.0
01 S/E
101
CIE-9/ ICD-9 323.5 052.0 049.9 323.8
CE/SC
Diagnstico
Diagnose
Section
S/E S/E S/E 01
Encefalitis posvacunacin Encefalitis posvaricela Encefalitis vrica (MNI, parotiditis, rubola, CMV)
Post-immunization encephalitis Varicella encephalitis Viral encephalitis (EpsteinBarr, mumps, rubella, CMV)
Infectious and inflammatory diseases Infectious and inflammatory diseases Infectious and inflammatory diseases Infectious and inflammatory diseases
Encefalitis: paraneoplsicas, Postinfectious, procesos autoinmunes, paraneoplastic or neurosarcoidosis autoimmune encephalitis (neurosarcoidosis) Encefalocele Encephalocele
742.0
S/E
CNS malformations. Cranial malformations. Hydrocephalus Infectious and inflammatory diseases Infectious and inflammatory diseases Epilepsy, paroxysmal disorders, sleep disorders
323.6 084.9 779.0
02 S/E 03
Encefalomielitis aguda diseminada Encefalopata en malaria Encefalopata epilptica infantil precoz
Acute disseminated encephalomyelitis (ADEM) Cerebral malaria Early-infantile epileptic encephalopathy with suppression-bursts (Ohtahara syndrome) Hypertensive encephalopathy (posterior reversible encephalopathy syndrome) Metabolic encephalopathy (inborn metabolic errors, water-electrolyte disorders, diabetes, etc.) Early myoclonic encephalopathy Rickettsial encephalitis Septic encephalopathy (caused by any infection)
437.2
S/E
Encefalopata hipertensiva (incluye encefalopata posterior reversible) Encefalopata metablica (ECM, alteraciones hidroelectrolticas, diabetes, etc.) Encefalopata mioclnica temprana/precoz Encefalopata por Rickettsia Encefalopata sptica (asociada a cualquier infeccin)
348.31
01
779.0 083.9 348.31
04 S/E 02
Epilepsy, paroxysmal disorders, sleep disorders Infectious and inflammatory diseases Iatrogenic, toxic, traumatic encephalopathies. Coma
102
CIE-9/ ICD-9 787.6
CE/SC
Diagnstico
Diagnose
Section
S/E
Encopresis
Encopresis
Developmental and behavioral disorders. Learning disabilities Neuro-ophthalmology/ neurotology Developmental and behavioral disorders. Learning disabilities Developmental and behavioral disorders. Learning disabilities Neuro-ophthalmology/ neurotology Morphology of neoplasms of NS Morphology of neoplasms of NS
378.0 788.36
S/E S/E
Endotropa Enuresis nocturna
Esotropia, intermittent esotropia not included Nocturnal enuresis
307.6
S/E
Enuresis primaria o secundaria (no orgnica) EOG/ERG anormales Ependimoma Ependimoma anaplsico Ependimoma mixopapilar Ependimoma papilar
Enuresis (primary) (secondary) of nonorganic origin ERG/EOG abnormals Ependymoma Ependymoma, anaplastic
794.12
S/E
M9391/3 S/E M9392/3 S/E M9394/1 S/E M9393/3 S/E 345.1 345.41 345.41 345.90 345.51 345.51 345.5 03 02 03 01 04 02 S/E
Myxopapillary ependymoma Morphology of neoplasms of NS Papillary ependymoma Morphology of neoplasms of NS Epilepsy, paroxysmal disorders, sleep disorders Epilepsy, paroxysmal disorders, sleep disorders Epilepsy, paroxysmal disorders, sleep disorders Epilepsy, paroxysmal disorders, sleep disorders Epilepsy, paroxysmal disorders, sleep disorders Epilepsy, paroxysmal disorders, sleep disorders
Epilepsia con crisis Epilepsy with generalized tonicoclnicas del despertar tonic-clonic on awake Epilepsia del lbulo frontal Frontal lobe epilepsy
Epilepsia del lbulo occipital Nonidiopathic occipital no idioptica epilepsy Epilepsia del sobresalto Startle epilepsy
Epilepsia familiar del lbulo Familial temporal lobe temporal epilepsy Epilepsia focal familiar con focos variables Familial focal epilepsy with variable foci
Epilepsia focal o parcial Focal idiopathic and familial Epilepsy, paroxysmal idioptica o familiar con/sin epilepsy with/without disorders, sleep disorders generalizacin secundaria secondary generalization
103
CIE-9/ ICD-9 345.40
CE/SC
Diagnstico
Diagnose
Section
01
Epilepsia focal/parcial secundaria a displasias, tberes, hamartomas Epilepsia focal/parcial sintomtica y criptognica Epilepsia fotosensible idioptica del lbulo occipital Epilepsia fotosensible o visual sensitiva Epilepsia frontal nocturna autonmica dominante Epilepsia generalizada convulsiva sintomtica o criptognica Epilepsia generalizada con crisis febriles plus Epilepsia generalizada primaria convulsiva Epilepsia del lbulo temporal mesial con o sin esclerosis hipocampal Epilepsia mioclnica benigna de la infancia
Epilepsy associated to cortical dysplasia, neurocutaneous disorders, hamartoma...) Symptomatic and cryptogenic focal epilepsy Idiopathic photosensitive occipital lobe Other visual sensitive epilepsies Autosomal dominant nocturnal frontal lobe epilepsy Symptomatic or cryptogenic generalized convulsive epilepsy Generalized epilepsies with febrile seizures plus Convulsive generalized epilepsy Mesial temporal lobe epilepsy with or without hippocampal sclerosis Benign myoclonic epilepsy in infancy
345.4 345.90
S/E 03
Epilepsy, paroxysmal disorders, sleep disorders Epilepsy, paroxysmal disorders, sleep disorders Epilepsy, paroxysmal disorders, sleep disorders Epilepsy, paroxysmal disorders, sleep disorders Epilepsy, paroxysmal disorders, sleep disorders Epilepsy, paroxysmal disorders, sleep disorders Epilepsy, paroxysmal disorders, sleep disorders Epilepsy, paroxysmal disorders, sleep disorders Epilepsy, paroxysmal disorders, sleep disorders Epilepsy, paroxysmal disorders, sleep disorders
345.90 345.51
02 03
345.1
02
345.90 345.1 345.40
04 01 02
345.80 345.80 345.81 345.80 345.9
02 03 02 01 S/E
Epilepsia mioclnica juvenil Juvenile myoclonic epilepsy Epilepsia mioclnica grave (Dravet) Epilepsia mioclnico asttica Epilepsia no especificada si focal o generalizada
Severe myoclonic epilepsy Epilepsy, paroxysmal in infancy (Dravet syndrome) disorders, sleep disorders Epilepsy with myoclonic astatic seizures Nondetermined focal or generalized epilepsy Epilepsy, paroxysmal disorders, sleep disorders Epilepsy, paroxysmal disorders, sleep disorders
104
CIE-9/ ICD-9 345.50
CE/SC
Diagnstico
Diagnose
Section
04
Epilepsia occipital idioptica temprana (tipo Panayiotopoulos) y tarda (tipo Gastaut)
Early-onset benign childhood occipital epilepsy (Panayiotopoulos type) and late-onset childhood occipital epilepsy (Gastaut type) Atypical benign childhood epilepsy Benign childhood epilepsy with centrotemporal spikes Epilepsia partialis continua (Kozhevnikov and Rasmussen type) Primary reading epilepsy Progressive myoclonic epilepsies: UnverrichtLundborg disease, Lafora disease, neuronal ceroid lipofuscinosis, sialidosis, MERRF, other types Reflex epilepsies
345.50 345.50 345.7
03 02 S/E
Epilepsia parcial benigna atpica Epilepsia parcial benigna centrotemporal Epilepsia parcial continua: tipo I (Kojevnikov) y tipo II (Rasmussen) Epilepsia primaria de la lectura Epilepsias mioclnicas progresivas: UnverrichtLundborg, Lafora, ceroidolipofuscinosis
Epilepsy, paroxysmal disorders, sleep disorders Epilepsy, paroxysmal disorders, sleep disorders Epilepsy, paroxysmal disorders, sleep disorders Epilepsy, paroxysmal disorders, sleep disorders Epilepsy, paroxysmal disorders, sleep disorders
345.90 345.81
05 01
345.90 345.8
06 S/E
Epilepsias reflejas Epilepsias y sndromes especficos sin cdigo propio EPOCS
Other epilepsies and epileptic Epilepsy, paroxysmal syndromes not otherwise disorders, sleep disorders specified Epilepsy with continuous spike-waves during slowwave sleep (CSWS) Inborn error of metabolism, suspected Shuddering associated to fever Shuddering attacks, jitteriness Multiple sclerosis Epilepsy, paroxysmal disorders, sleep disorders Inborn errors of metabolism with neurological manifestations Epilepsy, paroxysmal disorders, sleep disorders Cerebral palsy. Movement disorders Neurodegeneratives diseases. Leukodystrophies
345.81
05
330.3
S/E
Error innato metablico (sospecha) Escalofros por fiebre Escalofros, sobresaltos (shuddering, jitteriness) Esclerosis mltiple
780.6 333.93 340
S/E S/E S/E
105
CIE-9/ ICD-9 759.5 737.4 333.84 780.2 756.17 742.2
CE/SC
Diagnstico
Diagnose
Section
S/E S/E S/E 01 S/E 04
Esclerosis tuberosa Escoliosis en enfermedades neuromusculares Espasmo del escribiente Espasmos del sollozo Espina bfida oculta Esquisencefalia
Tuberous sclerosis Scoliosis, in neuromuscular or neurological conditions Writers cramp Breathholding spells Spina bifida occulta Schizencephaly
Neurocutaneous Vertebral column and spinal cord diseases Cerebral palsy. Movement disorders Epilepsy, paroxysmal disorders, sleep disorders Vertebral column and spinal cord diseases CNS malformations. Cranial malformations. Hydrocephalus Iatrogenic, toxic, traumatic encephalopathies. Coma Epilepsy, paroxysmal disorders, sleep disorders Epilepsy, paroxysmal disorders, sleep disorders Epilepsy, paroxysmal disorders, sleep disorders
780.03 345.3 345.2 345.3 723.0
S/E 01 S/E 03 S/E
Estado vegetativo persistente Estatus epilptico convulsivo Estatus epilptico no convulsivo Estatus mioclnico Estenosis de canal a nivel cervical (mucopolisacaridosis, acondroplasias) Estenosis de canal medular en general Estereotipias Estrabismo paraltico
Persistent vegetative state Convulsive epileptic status Non-convulsive epileptic status Myoclonic epileptic status
Vertebral canal stenosis, Vertebral column and spinal cervical level (i.e.: secondary cord diseases to mucopolysaccharidosis, achondroplasia, etc.) Vertebral canal stenosis, any Vertebral column and spinal location cord diseases Stereotypies Paralytic strabismus Cerebral palsy. Movement disorders Neuro-ophthalmology/ neurotology Fetal and perinatal neurology Neuro-ophthalmology/ neurotology Neuromuscular diseases
724.00 307.3 378.5 779.1 378.1 351.8
S/E 01 S/E S/E S/E S/E
Excitabilidad neuromuscular Neurological irritability in del RN y lactante newborn Exotropa Facial (otras afectaciones) Exotropia, intermittent exotropia not included Other disorders of facial nerve
106
CIE-9/ ICD-9 351.0 272.8
CE/SC
Diagnstico
Diagnose
Section
S/E S/E
Facial (parlisis de Bell) Farber
Facial (Bells palsy) Farber disease
Neuromuscular diseases Inborn errors of metabolism with neurological manifestations Inborn errors of metabolism with neurological manifestations Epilepsy, paroxysmal disorders, sleep disorders
270.1
S/E
Fenilcetonuria
Phenilketonuria
255.6 437.8
S/E S/E
Feocromocitoma Fstulas intracraneales: carotidocavernosa, fstula dural Fobia o trastorno fbico
Pheochromocytoma
Intracranial fistulas (carotid- Vascular diseases cavernous, dural) Phobic disorder Developmental and behavioral disorders. Learning disabilities Inborn errors of metabolism with neurological manifestations Iatrogenic, toxic, traumatic encephalopathies. Coma Iatrogenic, toxic, traumatic encephalopathies. Coma
300.2
S/E
266.2
01
Folato cerebral y cido folnico (dficit) Fractura de bveda craneal abierta Fractura de bveda craneal cerrada Fractura de base craneal abierta con hemorragia subaracnoidea, subdural, extradural Fractura de base craneal cerrada (incluye techo de la rbita) Fractura de clavcula al nacimiento
Folic acid and folinic acid (cerebral deficiency) Skull fracture, open Skull fracture, closed
800.5 800.0 801.7
S/E S/E S/E
Skull open fracture with Iatrogenic, toxic, traumatic subarachnoid, subdural, and encephalopathies. Coma extradural hemorrhage Closed fracture of base of skull (orbital ceiling included) Fracture of clavicle due to birth trauma Iatrogenic, toxic, traumatic encephalopathies. Coma Fetal and perinatal neurology
801.0
S/E
767.2 806.8 805.8 733.13
S/E S/E S/E S/E
Fractura vertebral con lesin Vertebral fracture with spinal Iatrogenic, toxic, traumatic medular cord damage encephalopathies. Coma Fractura vertebral sin lesin medular Fracturas patolgicas de vrtebras Vertebral fracture without spinal cord damage Vertebrae, pathological fractures Iatrogenic, toxic, traumatic encephalopathies. Coma Vertebral column and spinal cord diseases
107
CIE-9/ ICD-9 759.89
CE/SC
Diagnstico
Diagnose
Section
07
Freeman-Sheldon
Freeman-Sheldon syndrome Malformative syndromes. Chromosomical and genomic diseases Hereditary fructose intolerance (fructose 1,6 diphosphatase deficiency) Galactosemia Inborn errors of metabolism with neurological manifestations Inborn errors of metabolism with neurological manifestations Inborn errors of metabolism with neurological manifestations Morphology of neoplasms of NS
271.2
S/E
Fructosa 1,6 difosfato (dficit) o intolerancia hereditaria a la fructosa Galactosemia
271.1
S/E
330.1
02
Galactosialidosis
Galactosialidosis
M9492/0 S/E M9493/0 S/E
Gangliocitoma Gangliocitoma displstico del cerebelo (LhermitteDuclos) Ganglioglioma Ganglioglioma anaplsico Ganglioneuroblastoma Ganglioneuroroma Gangliosidosis GM1 y GM2 (Tay-Sachs, Sandhoff) Germinoma Gerstmann
Gangliocytoma
Dysplastic gangliocytoma of Morphology of neoplasms cerebellum (Lhermitteof NS Duclos) Ganglioglioma Ganglioglioma, anaplastic Ganglioneuroblastoma Ganglioneuroma GM1 and GM2 gangliosidosis (Tay-Sachs and Sandhof diseases, etc.) Germinoma Gerstmann developmental syndrome Gigantism, overgrowth syndromes (Sotos, Weaver, etc.) Tourette syndrome Morphology of neoplasms of NS Morphology of neoplasms of NS Morphology of neoplasms of NS Morphology of neoplasms of NS Inborn errors of metabolism with neurological manifestations Morphology of neoplasms of NS Developmental and behavioral disorders. Learning disabilities Malformative syndromes. Chromosomical and genomic diseases Cerebral palsy. Movement disorders
M9505/1 S/E M9505/3 S/E M9490/3 S/E M9490/0 S/E 330.1 03
M9064/3 S/E 784.69 S/E
253.0
S/E
Gigantismo, sndrome de hipercrecimiento. Sotos, Weaver Gilles de la Tourette
307.23
S/E
108
CIE-9/ ICD-9 271.9
CE/SC
Diagnstico
Diagnose
Section
01
Glicoprotenas deficientes en carbohidratos Glioblastoma Glioma cordoide Glioma maligno Glioma mixto Gliomatosis cerebri Glucogenosis
Glycosylation, congenital disorders Glioblastoma Chordoid glioma Glioma, malignant Mixed glioma Gliomatosis cerebri Glycogenosis
Inborn errors of metabolism with neurological manifestations Morphology of neoplasms of NS Morphology of neoplasms of NS Morphology of neoplasms of NS Morphology of neoplasms of NS Morphology of neoplasms of NS Inborn errors of metabolism with neurological manifestations Inborn errors of metabolism with neurological manifestations Iatrogenic, toxic, traumatic encephalopathies. Coma Malformative syndromes. Chromosomical and genomic diseases Neuromuscular diseases Malformative syndromes. Chromosomical and genomic diseases Cerebral palsy. Movement disorders
M9440/3 S/E M9444/1 S/E M9380/3 S/E M9382/3 S/E M9381/3 S/E 271.0 S/E
270.8
02
Glutatin sintetasa (dficit)
Glutathione synthetase deficiency Heatstroke / Sunstroke Gorlin syndrome
992.5 759.89
S/E 08
Golpe de calor Gorlin
357.0 756.0
S/E 05
Guillain-Barr Hallerman-Streiff
Guillain-Barr syndrome Hallerman-Streiff syndrome
333.0
03
Hallervorden-Spatz (deficiencia de pantotenato cinasa) Hemangioblastoma Hemangioma
Hallervorden-Spatz disease, pantothenate kinase associated neurodegeneration (PKAN) Haemangioblastoma Haemangioma
M9161/1 S/E M9120/0 S/E
Morphology of neoplasms of NS Morphology of neoplasms of NS
109
CIE-9/ ICD-9
CE/SC
Diagnstico
Diagnose
Section
M9121/0 S/E M9122/0 S/E M9150/1 S/E 852.4 853.0 S/E S/E
Hemangioma cavernoso Hemangioma venoso Hemangiopericitoma Hematoma epidural traumtico
Cavernous haemangioma Venous haemangioma Haemangiopericytoma Traumatic epidural hematoma
Morphology of neoplasms of NS Morphology of neoplasms of NS Morphology of neoplasms of NS Iatrogenic, toxic, traumatic encephalopathies. Coma Iatrogenic, toxic, traumatic encephalopathies. Coma Iatrogenic, toxic, traumatic encephalopathies. Coma CNS malformations. Cranial malformations. Hydrocephalus Cerebral palsy. Movement disorders Epilepsy, paroxysmal disorders, sleep disorders Cerebral palsy. Movement disorders Fetal and perinatal neurology Vascular diseases Fetal and perinatal neurology Vascular diseases
Hematoma parenquimatoso Traumatic parenchymatous traumtico (incluye HIV) hematoma (intraventricular hemorrhage included) Hematoma subdural traumtico Hemimegalencefalia Traumatic subdural hematoma Hemimegalencephaly
852.2 742.2
S/E 05
343.4
S/E
Hemipleja adquirida (excluye la PCI hemipljica)
Hemiparesis / Hemiplegia (acquired; excludes hemiplegic cerebral palsy)
345.41 342.8 767.0 432.0 772.9 431 772.1 362.81 430
04 S/E 01 S/E S/E 01 S/E S/E S/E
Hemipleja-hemiconvulsin Hemiconvulsion-hemiplegia (sndrome) syndrome Hemiplejia alternante Hemorragia cerebral al nacimiento Hemorragia epidural no traumtica Alternating hemiplegia of childhood Cerebral hemorrhage due to birth trauma Non-traumatic extradural hemorrhage
Hemorragia fetal y neonatal Unspecified hemorrhage of sin especificacin newborn Hemorragia intraparenquimatosa Parenchymal hemorrhage
Hemorragia intraventricular Intraventricular hemorrhage Fetal and perinatal fetal y neonatal perinatal of fetus or newborn neurology Hemorragia retiniana Hemorragia subaracnoidea Retinal hemorrhage Subarachnoid hemorrhage Neuro-ophthalmology/ neurotology Vascular diseases
110
CIE-9/ ICD-9 772.2 852.0 767.0 432.1 431 348.4
CE/SC
Diagnstico
Diagnose
Section
S/E S/E 02 S/E 02 02
Hemorragia subaracnoidea perinatal Hemorragia subaracnoidea traumtica Hemorragia subdural al nacimiento Hemorragia subdural no traumtica Hemorragia ventricular Herniacin cerebral (cualquier sndrome por herniacin) Heterotopas
Subarachnoid hemorrhage of newborn Traumatic subarachnoid hemorrhage
Fetal and perinatal neurology Iatrogenic, toxic, traumatic encephalopathies. Coma
Subdural hemorrhage due to Fetal and perinatal birth trauma neurology Non-traumatic subdural hemorrhage Brain (stem) herniation Vascular diseases
Intraventricular hemorrhage Vascular diseases Iatrogenic, toxic, traumatic encephalopathies. Coma CNS malformations. Cranial malformations. Hydrocephalus CNS malformations. Cranial malformations. Hydrocephalus CNS malformations. Cranial malformations. Hydrocephalus CNS malformations. Cranial malformations. Hydrocephalus CNS malformations. Cranial malformations. Hydrocephalus CNS malformations. Cranial malformations. Hydrocephalus Developmental and behavioral disorders. Learning disabilities
742.2
06
Neuronal heterotopias
742.4
02
Hidranencefalia
Hydranencephaly
331.3
S/E
Hidrocefalia comunicante
Communicating hydrocephalus Congenital hydrocephalus
742.3
S/E
Hidrocefalia congnita
742.8
S/E
Hidrocefalia externa, External hydrocephalus, higroma cerebral o aumento cerebral hygroma or de espacios subaracnoideos enlargement subarachnoid spaces Hidrocefalia obstructiva (no Obstructive hydrocephalus comunicante) (noncommunicating) Hipercinesia/inatencin no especificada o de otras causas Hiperglicinemia no cetsica Hyperactivity or inattention not otherwise specified
331.4
S/E
314.9
S/E
270.7
02
Non-ketotic hyperglycinemia Inborn errors of metabolism with neurological manifestations
111
CIE-9/ ICD-9 270.8
CE/SC
Diagnstico
Diagnose
Section
04
Hiperprolinemia
Hyperprolinemia
Inborn errors of metabolism with neurological manifestations Headache and related disorders Neuromuscular diseases CNS malformations. Cranial malformations. Hydrocephalus Neuro-ophthalmology/ neurotology Neuro-ophthalmology/ neurotology Fetal and perinatal neurology Developmental and behavioral disorders. Learning disabilities Neuromuscular diseases Fetal and perinatal neurology Neurocutaneous CNS malformations. Cranial malformations. Hydrocephalus Epilepsy, paroxysmal disorders, sleep disorders Fetal and perinatal neurology
348.2
S/E
Hipertensin intracraneal benigna o pseudotumor cerebri Hipertermia maligna Hipervitaminosis A
Pseudotumor cerebri / Benign intracranial hypertension Malignant hyperthermia Hypervitaminosis (vitamin A) Unspecified hearing loss Sudden hearing loss
995.86 278.2
S/E S/E
389.9 388.2 775.4
S/E S/E S/E
Hipoacusia Hipoacusia repentina
Hipocalcemia e Hypocalcemia, hipomagnesemia del recin hypomagnesemia of nacido newborn Hipoestimulacin Child neglect
995.59
S/E
352.5 775.6 757.33 742.2
S/E S/E 01 07
Hipogloso (afectacin) Hipoglucemia neonatal Hipomelanosis de Ito, incontinencia pigmenti Hipoplasia cerebelosa
Disorders of hypoglossal nerve Neonatal hypoglycemia Ito hypomelanosis, incontinentia pigmenti Cerebellar hypoplasia
458.0 243 358.8
S/E S/E S/E
Hipotensin ortosttica Hipotiroidismo neonatal Hipotona benigna del lactante
Ortostathic hypotension Congenital hypothiroidism
Benign congenital hypotonia Developmental and behavioral disorders. Learning disabilities
112
CIE-9/ ICD-9 779.89 270.5
CE/SC
Diagnstico
Diagnose
Section
S/E S/E
Hipotona central neonatal Histidinemia
Central hypotonia present in the perinatal period Histidinemia
Fetal and perinatal neurology Inborn errors of metabolism with neurological manifestations Morphology of neoplasms of NS CNS malformations. Cranial malformations. Hydrocephalus Inborn errors of metabolism with neurological manifestations Neuro-ophthalmology/ neurotology Cerebral palsy. Movement disorders Epilepsy, paroxysmal disorders, sleep disorders Neurodegeneratives diseases. Leukodystrophies Fetal and perinatal neurology
M9720/3 S/E 742.2 08
Histiocitosis maligna Holoprosencefalia
Malignant histiocytosis Holoprosencephaly
270.4
04
Homocistinuria (ECM de aminocidos sulfurados) Horner Huntington Hipersomnia, no especificada Inclusiones intraneuronales (enfermedad)
Homocystinuria (and other inborn errors of sulfurcontaining aminoacids) Horner syndrome Huntington disease Hypersomnia, unspecified Intraneuronal inclusions disease
337.9 333.4 780.54 335.8 771.2
S/E S/E S/E S/E S/E
Infeccin congnita (incluye Other congenital infections toxoplasmosis congnita) specific to the perinatal period including congenital toxoplasmosis Infeccin del SNC por virus lentos Other specified slow virus infection of central nervous system
046.8
S/E
Infectious and inflammatory diseases Fetal and perinatal neurology Epilepsy, paroxysmal disorders, sleep disorders
765.0 780.51 780.5 305.0
S/E S/E S/E S/E
Inmaduridad extrema, gran Immature or extremely prematuro premature Insomnio con apnea Insomnio o perturbaciones del sueo Intoxicacin alcohlica Insomnia with nocturnal apnea
Insomnia and sleep disorders Epilepsy, paroxysmal disorders, sleep disorders Alcoholic intoxication/abuse Iatrogenic, toxic, traumatic encephalopathies. Coma
113
CIE-9/ ICD-9 988.9 986 292.2 977.9 989 985 984 437.1 435 270.3
CE/SC
Diagnstico
Diagnose
Section
S/E S/E S/E S/E S/E S/E S/E S/E S/E 02
Intoxicacin por alimentos (hongos, plantas) Intoxicacin por monxido de carbono Intoxicacin por droga de abuso Intoxicacin por frmacos
Food poisoning (mushrooms, Iatrogenic, toxic, traumatic plants, fish, shellfish) encephalopathies. Coma Carbon monoxide poisoning Drug intoxication Poisoning by medicinal and biological substances Iatrogenic, toxic, traumatic encephalopathies. Coma Iatrogenic, toxic, traumatic encephalopathies. Coma Iatrogenic, toxic, traumatic encephalopathies. Coma Iatrogenic, toxic, traumatic encephalopathies. Coma Iatrogenic, toxic, traumatic encephalopathies. Coma Iatrogenic, toxic, traumatic encephalopathies. Coma
Intoxicacin por insecticida, Insecticide, pesticide pesticidas, venenos poisoning Intoxicacin por metales Heavy metal poisoning
Intoxicacin por plomo y sus Lead and lead compound compuestos poisoning
Isquemia cerebral crnica. Chronic cerebral ischemia. Vascular diseases Insuficiencia cerebrovascular Cerebrovascular insufficiency Isquemia cerebral transitoria Transient cerebral ischemia Jarabe de arce (ECM de aminocidos de cadena ramificada) Johanson-Blizard Vascular diseases Inborn errors of metabolism Maple urine syrup disease (and other inborn errors with neurological manifestations of the metabolism of branched-chain aminoacids) Johanson-Blizard syndrome Malformative syndromes. Chromosomical and genomic diseases Malformative syndromes. Chromosomical and genomic diseases Fetal and perinatal neurology Malformative syndromes. Chromosomical and genomic diseases Neuro-ophthalmology/ neurotology
759.89
09
759.89
10
Kabuki
Kabuki syndrome
774.7 758.7
S/E S/E
Kernicterus Klinefelter
Kernicterus of fetus or newborn (any etiology) Klinefelter syndrome
759.89 386.30
24 S/E
Klippel-Trenaunay Laberintitis
Klippel-Trenaunay syndrome Neurocutaneous Labyrinthitis
114
CIE-9/ ICD-9 345.81
CE/SC
Diagnstico
Diagnose
Section
04
Landau-Kleffner
Landau-Kleffner syndrome
Epilepsy, paroxysmal disorders, sleep disordersdisorders Malformative syndromes. Chromosomical and genomic diseases Neurodegeneratives diseases. Leukodystrophies Developmental and behavioral disorders. Learning disabilities Epilepsy, paroxysmal disorders, sleep disorders Neurocutaneous
759.89
11
Laurence-Moon-Biedl
Laurence-Moon-Biedl syndrome Leighs disease Specific language impairment Lennox-Gastaut syndrome Lentigines-deafnesscardiomyopathy (Leopard syndrome) Diffuse axonal injury Leukokoria Leukodystrophy: Krabbe, Pelizaeus-Merzbacher, Alexander, globoid cell, van der Knaap, metachromatic, Aicardi-Goutires Acute haemorrhagic leukoencephalitis Progressive multifocal leukoencephalopathy
330.8 315.3
3 S/E
Leigh Lenguaje (TEL)
345.81 709.09
03 S/E
Lennox-Gastaut Lentiginosis-sorderacardiopata Lesin axonal difusa Leucocoria Leucodistrofias: Krabbe, Pelizaeus, Alexander, van der Knaap, LDM, AicardiGoutires Leucoencefalitis hemorrgica aguda Leucoencefalopata multifocal progresiva Leucomalacia periventricular Linfangioma Linfoma maligno
341.9 360.44 330.0
01 S/E S/E
Iatrogenic, toxic, traumatic encephalopathies. Coma Neuro-ophthalmology/ neurotology Neurodegeneratives diseases. Leukodystrophies
323.6 046.3 779.7
03 S/E S/E
Infectious and inflammatory diseases Neurodegeneratives diseases. Leukodystrophies
Periventricular leukomalacia Fetal and perinatal neurology Lymphangioma Malignant lymphoma Morphology of neoplasms of NS Morphology of neoplasms of NS
M9170/0 S/E M9590/3 S/E
115
CIE-9/ ICD-9 330.2
CE/SC
Diagnstico
Diagnose
Section
01
Lipidosis clsicas con afectacin cerebral: Niemann-Pick A, B, C, Gaucher, Fabry Lipidosis con afectacin cerebral (otras): Smith-Lemli-Opitz, aciduria mevalnica, Tangier, xantomatosis cerebrocutnea Lipoma Lisencefalia
Classic cerebral lipidoses: Niemann-Pick A, B, C, Gaucher, Fabry, etc. Cerebral lipidoses, not specified otherwise (i.e. Smith-Lemli-Opitz, mevalonic aciduria, cerebrotendinous xanthomatosis, etc.) Lipoma Lissencephaly
Inborn errors of metabolism with neurological manifestations Inborn errors of metabolism with neurological manifestations
330.2
02
M8850/0 S/E 742.2 09
Morphology of neoplasms of NS CNS malformations. Cranial malformations. Hydrocephalus Iatrogenic, toxic, traumatic encephalopathies. Coma Malformative syndromes. Chromosomical and genomic diseases Vertebral column and spinal cord diseases Vertebral column and spinal cord diseases
344.81
S/E
Locked-in (enclaustramiento o estado similar) Lowe
Locked-in state
270.8
05
Lowe syndrome
724.2 839.0
S/E S/E
Lumbalgia, lumbago Luxacin/subluxacin de vrtebra cervical (atlantoaxoidea) Lyme (neuroborreliosis) Macrocefalia
Lumbar pain Luxation/subluxation of cervical vetebrae (atlantoaxial, atlanto-occipital, and others) Lyme disease (borreliosis) Macrocephaly
088.81 756.0
S/E 03
Infectious and inflammatory diseases CNS malformations. Cranial malformations. Hydrocephalus Neurocutaneous
756.4
02
Maffucci
Maffucci syndrome (enchondromatosis, Olliers disease)
747.82
S/E
Malformacin arteriovenosa Spinal arteriovenous and Vascular diseases espinal o hemangioma hemangioma malformations espinal
116
CIE-9/ ICD-9 747.81
CE/SC
Diagnstico
Diagnose
Section
S/E
Malformacin arteriovenosa, aneurismas venosos (vena de Galeno) y fstulas congnitas cerebrales Malformacin craneofacial
Arteriovenous malformation, Vascular diseases venous aneurysm (includes vein of Galen malformation and other congenital fistulas) Craniofacial malformation CNS malformations. Cranial malformations. Hydrocephalus Iatrogenic, toxic, traumatic encephalopathies. Coma Neuromuscular diseases
756.0
04
995.50 781.2
S/E S/E
Malos tratos infantiles Marcha de puntas tip-toe y otras anomalas de la marcha Marfan
Child abuse, unspecified Tip-toe gait and other gait abnormalities Marfan syndrome
759.82
S/E
Malformative syndromes. Chromosomical and genomic diseases Malformative syndromes. Chromosomical and genomic diseases Malformative syndromes. Chromosomical and genomic diseases Neuromuscular diseases Iatrogenic, toxic, traumatic encephalopathies. Coma Iatrogenic, toxic, traumatic encephalopathies. Coma Iatrogenic, toxic, traumatic encephalopathies. Coma Iatrogenic, toxic, traumatic encephalopathies. Coma Morphology of neoplasms of NS Morphology of neoplasms of NS Morphology of neoplasms of NS
759.89
12
Marshall-Smith
Marshall-Smith syndrome
759.89
13
MASA
MASA syndrome
354.1 952.0 952.2 952.3 952.1
S/E S/E S/E S/E S/E
Mediano (lesin) Mdula espinal cervical (lesin traumtica) Mdula espinal lumbar (lesin traumtica) Mdula espinal sacra (lesin traumtica) Mdula espinal torcica (lesin traumtica) Meduloblastoma Meduloepitelioma Melanocitoma
Other lesions of median nerve Cervical spinal cord (traumatic injury) Lumbar spinal cord (traumatic injury) Sacral spinal cord (traumatic injury) Thoracic spinal cord (traumatic injury) Medulloblastoma Medulloepithelioma Meningeal melanocytoma
M9470/3 S/E M9501/3 S/E M8728/1 S/E
117
CIE-9/ ICD-9
CE/SC
Diagnstico
Diagnose
Section
M8728/0 S/E M8720/3 S/E M8728/3 S/E 386.00 S/E
Melanocitosis difusa Melanoma maligno Melanomatosis menngea Mnire Meningioma Meningitis bacteriana y meningoencefalitis bacteriana Meningitis inespecfica: reaccin menngea qumica, secundaria a foco infeccioso, o LOE intracraneal, migraa con pleocitosis Meningitis por otros organismos: hongos, parsitos Meningitis tuberculosa Meningitis vrica no especificada Meningocele, mielomeningocele, lipomeningocele, mielocele (espina bfida abierta) Meningoencefalitis por toxoplasma adquirida Menkes (trastornos del metabolismo del cobre) Metstasis
Diffuse melanocytosis Malignant melanoma Meningeal melanomatosis Mnires disease Meningioma Bacterial meningitis o meningoencephalitis
Morphology of neoplasms of NS Morphology of neoplasms of NS Morphology of neoplasms of NS Neuro-ophthalmology/ neurotology Morphology of neoplasms of NS Infectious and inflammatory diseases
M9530/0 S/E 320.9 S/E
322
S/E
Non-infectious meningitis: Infectious and inflammatory diseases malignancies, toxic, drug-induced, migraine with pleocytosis Other organisms meningitis: Infectious and inflammatory fungal, parasitic meningitis diseases Tuberculous meningitis Non-determined viral meningitis Bifid spine: myelomeningocele, meningocele, lipomeningocele, etc. Toxoplasmic encephalitis Menkes disease Infectious and inflammatory diseases Infectious and inflammatory diseases Vertebral column and spinal cord diseases
321.8
S/E
013.0 047.9 741.9
S/E S/E S/E
130.0 759.89
S/E 25
Infectious and inflammatory diseases Inborn errors of metabolism with neurological manifestations Morphology of neoplasms of NS
M8000/6 S/E
Neoplasm, metastatic
118
CIE-9/ ICD-9 270.4
CE/SC
Diagnstico
Diagnose
Section
02
Metiltetrahidrofolatorreductasa (dficit MTHFR) Metionina sintasa (dficit)
Methylenetetrahydrofolate reductase deficiency Methionine synthase deficiency Myasthenia gravis Neonatal myasthenia gravis (transient and autoimmune caused)
Inborn errors of metabolism with neurological manifestations Inborn errors of metabolism with neurological manifestations Neuromuscular diseases Fetal and perinatal neurology
270.4
01
358.0 775.2
S/E S/E
Miastenia grave Miastenia grave neonatal (transitoria neonatal, asociada a alteraciones autoinmunes)
358.1
S/E
Neuromuscular diseases Miasteniformes (sndromes). Myasthenic syndromes in Lambert- Eaton diseases classified elsewhere. Eaton-Lambert syndrome Microcefalia Microcephaly CNS malformations. Cranial malformations. Hydrocephalus Malformative syndromes. Chromosomical and genomic diseases CNS malformations. Cranial malformations. Hydrocephalus Neurodegeneratives diseases. Leukodystrophies Infectious and inflammatory diseases Vertebral column and spinal cord diseases
742.1
S/E
758.33
02
Microdeleciones (otras)
Microdeletions (others)
742.2
10
Microgirias
Microgyria
341.8 323.8
S/E 02
Mielinosis central pontina
Central pontine myelinosis
Mielitis postinfecciosa, Postinfectious, paraneoplsica, en procesos paraneoplastic or autoinmunes autoimmune myelitis Mielodisplasias y alteraciones de la mdula espinal (diastematomielia, hidromielia) Mielopata (inducida por frmacos, por radiacin) Myelodysplasias, non specified otherwise (diastematomyelia, hydromyelia, etc.) Myelopathy, secondary to drug administration, radiotherapy or any other therapeutic intervention Myelopathy, compressive (any etiology)
742.5
S/E
336.8
S/E
Vertebral column and spinal cord diseases
336.9
S/E
Mielopata compresiva
119
CIE-9/ ICD-9 336.1
CE/SC
Diagnstico
Diagnose
Section
S/E
Mielopata vascular: infarto, trombosis arterial, hematomielia, edema de mdula Migraa Migraa abdominal Migraa basilar Migraa con aura Migraa en racimos Migraa hemipljica familiar Migraa oftalmopljica Migraa retiniana Migraa sin aura Miller-Dieker: delecin 17p13.3 Mioclonas benignas del lactante Mioclonas de sueo Mioclonas no epilpticas
Myelopathy of vascular origin: infarction, arterial thrombosis, hemorrhage; includes spinal cord edema Migraine Migraine, abdominal Migraine, basilar type Migraine with aura Cluster headache Migraine, hemiplegic familiar Migraine, ophtalmoplegic Migraine, retinal Migraine without aura Miller-Dieker syndrome, deletion 17p13.3 Benign myoclonus of early infancy Nocturnal myoclonus Non-epileptic myoclonus
346 346.2 346.2 346.0 346.2 346.8 346.8 346.2 346.1 758.33
S/E 01 02 S/E 03 01 02 05 S/E 03
Headache and related disorders Headache and related disorders Headache and related disorders Headache and related disorders Headache and related disorders Headache and related disorders Headache and related disorders Headache and related disorders Headache and related disorders Malformative syndromes. Chromosomical and genomic diseases Cerebral palsy. Movement disorders Epilepsy, paroxysmal disorders, sleep disorders Cerebral palsy. Movement disorders Cerebral palsy. Movement disorders Cerebral palsy. Movement disorders Cerebral palsy. Movement disorders
333.2 780.59 333.2 333.2 333.2 333.2
01 02 02 03 04 05
Mioclono benigno neonatal Benign neonatal sleep del sueo myoclonus Mioclono esencial familiar Mioclono negativo Essential myoclonus Negative myoclonus
120
CIE-9/ ICD-9 359.0
CE/SC
Diagnstico
Diagnose
Section
S/E
Miopata congnita (central core, nemalnica, multicore, miotubular, centronuclear, desproporcin congnita de fibras) Miopata en enfermedad endocrina Miopata inflamatoria asociada a otras enfermedades Miopata metablica Miopata mitocondrial Miopata no especificada Miopata toxica o por frmacos Miositis infecciosas Miotona congnita (Becker) Miotona congnita (Thomsen) Mitocondrial (trastorno del metabolismo): cadena respiratoria, citopatas mitocondriales Moebius Mononeuritis mltiple del miembro superior Motilidad ocular alterada (excluye nistagmo y movimientos irregulares de ojos) Moyamoya
Congenital myopathies (central core, minicore, multicore, fibre-type disproportion, myotubular, centronuclear, nemaline) Myopathy in endocrine diseases Inflammatory myopathy associated with other disorders Myopathy in metabolic diseases Mitochondrial myopathy Myopathy, unspecified Drug-induced myopathy Infectious myositis Congenital myotonia (Becker type) Thomsens myotonia congenita
359.81 359.5 359.6
S/E S/E S/E
Miopata del enfermo crtico Critical care myopathy
Neuromuscular diseases Neuromuscular diseases Neuromuscular diseases
359.89 359.89 359.9 359.4 728.0 359.2 359.2 277.87
01 02 S/E S/E S/E 04 02 02
Neuromuscular diseases Neuromuscular diseases Neuromuscular diseases Neuromuscular diseases Neuromuscular diseases Neuromuscular diseases Neuromuscular diseases
Mitochondrial metabolism Inborn errors of metabolism disorder: respiratory chain, with neurological any mitochondrial cytopathy manifestations Moebius Mononeuritis multiplex of upper limb Unspecified disorder of eye movements, nystagmus and other irregular eyes movements not included Moya-moya disease Neuromuscular diseases Neuromuscular diseases Neuro-ophthalmology/ neurotology
352.6 354.5 378.9
01 S/E S/E
437.5
S/E
Vascular diseases
121
CIE-9/ ICD-9 272.7
CE/SC
Diagnstico
Diagnose
Section
S/E
Mucolipidosis I, II, III, IV (sialidosis, I-cell) Mucopolisacaridosis
Mucolipidoses I, II, III, IV (sialidoses, I cell disease, etc.) Mucopolysaccharidosis
Inborn errors of metabolism with neurological manifestations Inborn errors of metabolism with neurological manifestations Epilepsy, paroxysmal disorders, sleep disorders Iatrogenic, toxic, traumatic encephalopathies. Coma Developmental and behavioral disorders. Learning disabilities Epilepsy, paroxysmal disorders, sleep disorders Neoplasms
277.5
S/E
348.8 798.0 313.23
S/E S/E S/E
Muerte cerebral Muerte sbita del lactante Mutismo electivo
Brain-death Sudden infant death syndrome Selective mutism
347 227.4 227.3
S/E S/E S/E
Narcolepsia-catapleja Neoplasia benigna de la glndula pineal Neoplasia benigna de la glndula pituitaria y conducto craneofarngeo Neoplasia benigna de la mdula espinal Neoplasia benigna de las meninges cerebrales Neoplasia benigna de las meninges espinales Neoplasia benigna de los nervios craneales Neoplasia benigna de otras glndulas endocrinas y estructuras relacionadas Neoplasia benigna del encfalo Neoplasia benigna del sistema nervioso central
Narcolepsy-cataplexy Benign neoplasm of pineal gland
Benign neoplasia of pituitary Neoplasms gland and craniopharyngeal duct (pouch) Benign neoplasia of spinal cord Benign neoplasia of cerebral meninges Benign neoplasia of spinal meninges Benign neoplasia of cranial nerves Neoplasms Neoplasms Neoplasms Neoplasms
225.3 225.2 225.4 225.1 227
S/E S/E S/E S/E S/E
Benign neoplasia of other Neoplasms endocrine glands and related structures Benign neoplasia of brain Neoplasms
225.0 225.9
S/E S/E
Benign neoplasia of nervous Neoplasms system, part unspecified
122
CIE-9/ ICD-9 225.8
CE/SC
Diagnstico
Diagnose
Section
S/E
Neoplasia benigna en otros sitios especificados del sistema nervioso (de contigidad) Neoplasia de evolucin incierta de la glndula pineal Neoplasia de evolucin incierta de la glndula pituitaria y conducto craneofarngeo Neoplasia de evolucin incierta de las meninges Neoplasia de evolucin incierta de otras partes no especificadas del sistema nervioso Neoplasia de evolucin incierta del cerebro y mdula espinal Neoplasia maligna de la glndula pineal Neoplasia maligna de la glndula pituitaria y conducto craneofarngeo Neoplasia maligna de la mdula espinal Neoplasia maligna de las meninges cerebrales Neoplasia maligna de las meninges espinales Neoplasia maligna de los nervios craneales Neoplasia maligna de los ventrculos Neoplasia maligna de otras glndulas endocrinas y estructuras relacionadas
Benign neoplasia of other specified sites of nervous system Neoplasia of uncertain behavior of pineal gland Neoplasia of uncertain behavior of pituitary gland and craniopharyngeal duct Neoplasia of uncertain behavior of meninges Neoplasia of uncertain behavior of other and unspecified parts of nervous system Neoplasia of uncertain behavior of brain and spinal cord Malignant neoplasia of pineal gland Malignant neoplasia of pituitary gland and craniopharyngeal duct Malignant neoplasia of spinal cord Malignant neoplasia of cerebral meninges Malignant neoplasia of spinal meninges Malignant neoplasia of cranial nerves Malignant neoplasia of ventricles
Neoplasms
237.1
S/E
Neoplasms
237.0
S/E
Neoplasms
237.6 237.9
S/E S/E
Neoplasms Neoplasms
237.5
S/E
Neoplasms
194.4 194.3
S/E S/E
Neoplasms Neoplasms
192.2 192.1 192.3 192.0 191.5 194
Neoplasms Neoplasms Neoplasms Neoplasms Neoplasms
Malignant neoplasia of other Neoplasms endocrine glands and related structures
123
CIE-9/ ICD-9 191.8
CE/SC
Diagnstico
Diagnose
Section
S/E
Neoplasia maligna de otras partes del cerebro en contigidad, cuerpo calloso
Malignant neoplasia of other parts of brain (corpus callosum/tapetum, malignant neoplasm of contiguous or overlapping sites of brain) Malignant neoplasia of other specified sites of nervous system (malignant neoplasm of contiguous or overlapping sites of other parts of nervous system) Malignant neoplasia of cerebellum Malignant neoplasia of brain, unspecified Malignant neoplasia of cerebrum, except lobes and ventricles (basal ganglia/ cerebral cortex/corpus striatum/globus pallidus/ hypothalamus/thalamus) Malignant neoplasia of frontal lobe Malignant neoplasia of occipital lobe Malignant neoplasia of parietal lobe Malignant neoplasia of temporal lobe Malignant neoplasia of nervous system, part unspecified Malignant neoplasia of brain stem Secondary malignant neoplasia of brain and spinal cord
Neoplasms
192.8
S/E
Neoplasia maligna de otros sitios especificados del sistema nervioso (en contigidad)
Neoplasms
191.6 191.9 191.0
S/E S/E S/E
Neoplasia maligna del cerebelo Neoplasia maligna del cerebro Neoplasia maligna del cerebro, excepto lbulos y ventrculos (ganglios basales)
Neoplasms Neoplasms Neoplasms
191.1 191.4 191.3 191.2 192.9
S/E S/E S/E S/E S/E
Neoplasia maligna del lbulo frontal Neoplasia maligna del lbulo occipital Neoplasia maligna del lbulo parietal Neoplasia maligna del lbulo temporal Neoplasia maligna del sistema nervioso central Neoplasia maligna del tronco cerebral Neoplasia maligna secundaria en cerebro y mdula espinal
Neoplasms Neoplasms Neoplasms Neoplasms Neoplasms
191.7 198.3
S/E S/E
Neoplasms Neoplasms
124
CIE-9/ ICD-9 198.4
CE/SC
Diagnstico
Diagnose
Section
S/E
Neoplasia maligna secundaria en otras partes del sistema nervioso (meninges) Nervio craneal (lesin traumtica) Nervio ptico (lesin traumtica) Nervio perifrico de miembro inferior o cintura plvica (lesin traumtica) Nervio perifrico de miembro superior o cintura escapular (lesin traumtica)
Secondary malignant neoplasia of other parts of nervous system (meninges) Cranial nerve (traumatic injury) Optic nerve (traumatic injury) Peripheral nerve of lower limb or pelvic girdle (traumatic injury) Peripheral nerve of upper limb or shoulder girdle (traumatic injury)
Neoplasms
951.8 950.0 956.9
S/E S/E S/E
Iatrogenic, toxic, traumatic encephalopathies. Coma Iatrogenic, toxic, traumatic encephalopathies. Coma Iatrogenic, toxic, traumatic encephalopathies. Coma Iatrogenic, toxic, traumatic encephalopathies. Coma
955.9
S/E
352.1 350.1 377.3 377.32 272.5
S/E S/E S/E S/E 02
Neuralgia del glosofarngeo Glossopharyngeal neuralgia Neuralgia del trigmino Neuritis ptica Neuritis ptica retrobulbar Neuroacantocitosis Neuroblastoma Neuroblastoma olfatorio (estesioneuroblastoma) Neurobrucelosis Neurocitoma central Neurocutneos (otros sndromes) Neuroepitelioma olfatorio Trigeminal neuralgia
Headache and related disorders Headache and related disorders
Optic neuritis, meningococcal Neuro-ophthalmology/ neuritis not included neurotology Retrobulbar optic neuritis (acute) Neuroacanthocytosis Neuroblastoma Olfactory neuroblastoma Neurobrucellosis Central neurocytoma Neurocutaneous syndromes (others) Olfactory neuroepithelioma Neuro-ophthalmology/ neurotology Cerebral palsy. Movement disorders Morphology of neoplasms of NS Morphology of neoplasms of NS Infectious and inflammatory diseases Morphology of neoplasms of NS Neurocutaneous Morphology of neoplasms of NS
M9500/3 S/E M9522/3 S/E 023.8 S/E
M9506/1 S/E 757.8 S/E
M9523/3 S/E
125
CIE-9/ ICD-9
CE/SC
Diagnstico
Diagnose
Section
M9540/0 S/E M9550/0 S/E 237.71 237.72 S/E S/E
Neurofibroma Neurofibroma plexiforme Neurofibromatosis tipo 1 (NF1) Neurofibromatosis tipo 2 (NF2)
Neurofibroma Plexiform neurofibroma Neurofibromatosis, type 1 Neurofibromatosis, type 2
Morphology of neoplasms of NS Morphology of neoplasms of NS Neurocutaneous Neurocutaneous Morphology of neoplasms of NS Neurocutaneous Cerebral palsy. Movement disorders Neurodegeneratives diseases. Leukodystrophies Neuro-ophthalmology/ neurotology Neuromuscular diseases Neuromuscular diseases Neuromuscular diseases Neuromuscular diseases
M9540/3 S/E
Neurofibrosarcoma o tumor Malignant peripheral maligno de vaina de nervio nerve sheath tumour perifrico (neurofibrosarcoma) Neuroictiosis Neurolptico maligno (sndrome) Neuromielitis ptica Neuronitis vestibular Neuropata hereditaria sensitivomotora tipo I Neuropata hereditaria sensitivomotora tipo II Neuropata hereditaria sensitivomotora tipo III Neuropata hereditaria sensitivomotora tipo IV (AR con plegamientos focales mielnicos, con glaucoma) Neuropata hereditaria sensitivomotora tipo V (con parapleja espstica) Neuroichthyosis Neuroleptic malignant syndrome Neuromyelitis optica Vestibular neuronitis Hereditary motor and sensory neuropathy, type I Hereditary motor and sensory neuropathy, type II Hereditary motor and sensory neuropathy, type III Hereditary motor and sensory neuropathy, type IV
757.1 333.92 341.0 386.12 356.1 356.1 356.0 356.8
01 S/E S/E S/E 01 02 S/E 01
356.8
02
Hereditary motor and sensory neuropathy, type V
356.8
03
Neuropata hereditaria Hereditary motor and sensitivomotora tipo VI (con sensory neuropathy, type VI atrofia ptica, retinopata, sordera)
126
CIE-9/ ICD-9 356.9
CE/SC
Diagnstico
Diagnose
Section
S/E
Neuropatas (otras): con afectacin del SNC o pares craneales, tomaculosa, neuropata de axones gigantes, Charcot-MarieTooth ligado a X... Neuropatas hereditarias sensitivoautonmicas tipos I, II, IV, V Neurosfilis
Other hereditary and idiopathic neuropathies: tomaculous neuropathy, X-linked Charcot-MarieTooth, giant axonal...
356.2
S/E
Neuromuscular diseases Hereditary sensory and autonomic neuropathy, type I, II, IV, V Neurosyphilis Infectious and inflammatory diseases Inborn errors of metabolism with neurological manifestations Neurocutaneous Neurocutaneous
090.4 277.89
S/E 02
Neurotransmisores Neurotransmitters, disorders (trastorno del metabolismo) of metabolism Nevo lineal sebceo Nevo pigmentado (epidrmico lineal, Jadasshon, melanosis neurocutnea) Nio adoptado (otras circunstancias familiares especficas) Nistagmo congnito Noonan Linear nevus sebaceous of Jadassohn Pigmented nevus (linear epidermal nevus, neurocutaneous melanosis) Adopted child (or other specific familial circumstance) Congenital nystagmus Noonan syndrome
702.8 216.8
S/E S/E
V61.8
S/E
Others
379.51 759.89
S/E 14
Neuro-ophthalmology/ neurotology Malformative syndromes. Chromosomical and genomic diseases
V65.5
S/E
Normalidad neurolgica
Neurologically normal child / Others No evidence of neurological disease Iatrogenic, toxic, traumatic encephalopathies. Coma Vascular diseases
780.09
S/E
Obnubilacin, somnolencia, Drowsiness, estupor unconsciousness, somnolence, stupor Oclusin arteria cerebral (embolia, trombosis) Cerebral arterial occlusion (embolism, thrombosis)
434 433
S/E S/E
Oclusin arterial precerebral Precerebral arterial occlusion Vascular diseases (cartida, basilar, vertebral) (carotid, basilar, vertebral)
127
CIE-9/ ICD-9 378.55
CE/SC
Diagnstico
Diagnose
Section
S/E
Oftalmopleja externa (incluye sndrome de Tolosa-Hunt) Oftalmopleja externa progresiva Oftalmopleja internuclear Oligodendroglioma Oligodendroglioma anaplsico Oligosacaridosis (manosidosis, fucosidosis, aspartilglucosaminuria) Oposicionista desafiante (trastorno) Opsoclono-mioclono o sndrome de Kinsbourne Otorrea de LCR Otras mononeuritis del miembro inferior Otras mononeuritis del miembro superior Pallister-Hall
External ophthalmoplegia (includes Tolosa-Hunt syndrome) Progressive external ophthalmoplegia Internuclear ophthalmoplegia Oligodendroglioma Oligodendroglioma, anaplastic Oligosaccharidoses (mannosidosis, fucosidosis, aspartylglycosaminuria)
Neuro-ophthalmology/ neurotology Neuro-ophthalmology/ neurotology Neuro-ophthalmology/ neurotology Morphology of neoplasms of NS Morphology of neoplasms of NS Inborn errors of metabolism with neurological manifestations
378.72 378.86
S/E S/E
M9450/3 S/E M9451/3 S/E 271.8 02
313.81
S/E
Oppositional defiant disorder Developmental and behavioral disorders. Learning disabilities Opsoclonus-myoclonus syndrome, Kinsbourne syndrome Otorrhea of cerebrospinal fluid Other mononeuropathies of lower limb Other mononeuropathies of upper limb Pallister-Hall syndrome Cerebral palsy. Movement disorders Iatrogenic, toxic, traumatic encephalopathies. Coma Neuromuscular diseases Neuromuscular diseases Malformative syndromes. Chromosomical and genomic diseases Infectious and inflammatory diseases Neuro-ophthalmology/ neurotology Neuro-ophthalmology/ neurotology Morphology of neoplasms of NS
379.59
S/E
388.61 355.79 354.8 759.89
S/E S/E S/E 15
046.2 377.00 377.31
S/E S/E S/E
Panencefalitis esclerosante subaguda Papiledema Papilitis
Subacute sclerosing panencephalitis (SSPE) Papilledema Optic papillitis
M9390/0 S/E
Papiloma del plexo coroideo Choroid plexus papilloma
128
CIE-9/ ICD-9
CE/SC
Diagnstico
Diagnose
Section
M8680/1 S/E 335.22 378.81 S/E S/E
Paraganglioma Parlisis bulbar progresiva Parlisis conjugada de la mirada (incluye Parinaud) Parlisis peridica familiar Parlisis psicgenas Paramiotona congnita (Eulenburg) Paraparesia espstica familiar Parapleja, paraparesia (por lesin medular adquirida) Pares craneales (afectacin mltiple) Pares craneales (otras afectaciones aisladas y/o recidivantes) Parkinson Parkinsonismo secundario Patau: trisoma 13
Paraganglioma filum terminale Progressive bulbar paresis Palsy of conjugate gaze (Parinaud syndrome and others) Periodic paralysis (familial) Psychogenic palsy Paramyotonia congenita of von Eulenburg Hereditary spastic paraplegias Paraplegia, paraparesis (secondary to acquired spinal cord lesion) Other multiple cranial nerve palsies Disorder of cranial nerves (isolated and/or relapsing) Parkinson disease Secondary parkinsonism Patau syndrome, trisomy 13
Morphology of neoplasms of NS Neuromuscular diseases Neuro-ophthalmology/ neurotology Neuromuscular diseases Neuromuscular diseases Neuromuscular diseases Neuromuscular diseases Vertebral column and spinal cord diseases Neuromuscular diseases Neuromuscular diseases
359.3 306.0 359.2 334.1 344.1
S/E S/E 03 S/E S/E
352.6 352.9
02 S/E
332.0 332.1 758.1
S/E S/E S/E
Cerebral palsy. Movement disorders Cerebral palsy. Movement disorders Malformative syndromes. Chromosomical and genomic diseases Cerebral palsy. Movement disorders
343 343.8
S/E 02
PCI PCI atxica o ataxia cerebelosa congnita (Marinesco-Sjgren) PCI coreoatetoide PCI dipljica
Cerebral palsy
Ataxic cerebral palsy Cerebral palsy. Movement (includes Marinesco-Sjgren disorders syndrome) Choreoathetotic cerebral palsy Spastic diplegia, cerebral palsy Cerebral palsy. Movement disorders Cerebral palsy. Movement disorders
333.5 343.0
05 S/E
129
CIE-9/ ICD-9 343.8 343.1 343.2 794.15
CE/SC
Diagnstico
Diagnose
Section
01 S/E S/E S/E
PCI distnica, mixta espstico-distnica PCI hemipartica espstica PCI tetrapartica espstica PEA/pruebas de audicin anormal
Dyskinetic cerebral palsy Spastic hemiplegia, cerebral palsy Spastic tetraplegia, cerebral palsy Abnormal auditory function studies, brainstem auditory evoked potentials abnormal findings Perineurioma Lesion of peroneal nerve
Cerebral palsy. Movement disorders Cerebral palsy. Movement disorders Cerebral palsy. Movement disorders Neuro-ophthalmology/ neurotology
M9571/0 S/E 355.3 277.86 S/E S/E
Perineurioma Peroneo comn (lesin) Peroxisomales (enfermedades) Perturbacin visual subjetiva (macromicropsias, fotofobia) Perturbacin visual, incluye visin borrosa Pesadillas, parasomnias PEV anormales Pica
Morphology of neoplasms of NS Neuromuscular diseases
Peroxisomal diseases (except Inborn errors of metabolism adrenoleukodistrophy) with neurological manifestations Subjective visual disturbances: macropsia, micropsia, metamorphopsia Other visual disturbances, blurred vision included Nightmare VEP abnormalities Pica (eating disorder) Neuro-ophthalmology/ neurotology Neuro-ophthalmology/ neurotology Epilepsy, paroxysmal disorders, sleep disorders Neuro-ophthalmology/ neurotology Developmental and behavioral disorders. Learning disabilities Morphology of neoplasms of NS Morphology of neoplasms of NS Morphology of neoplasms of NS Inborn errors of metabolism with neurological manifestations
368.1
S/E
368.8 307.47 794.13 307.52
S/E S/E S/E S/E
M9360/1 S/E M9362/3 S/E M9361/1 S/E 266.9 S/E
Pinealoma Pineoblastoma Pineocitoma Piridoxina (dependencia)
Pinealoma Pineoblastoma Pineocytoma Piridoxine dependency syndrome
130
CIE-9/ ICD-9 271.8
CE/SC
Diagnstico
Diagnose
Section
01
Piruvato carboxilasa y piruvato deshidrogenasa (dficit)
Pyruvate dehydrogenase, pyruvate carboxylase deficiencies
Inborn errors of metabolism with neurological manifestations Vertebral column and spinal cord diseases
756.1
01
Platibasia, impresin basilar, Platybasia, basilar Klippel-Feil (anomalas impression, Klippel-Feil craneocervicales) anomaly, and other craneocervical anomalies Plexo o raz (lesin traumtica) Plexopata braquial (no trauma obsttrico) Plexopata lumbosacra Polimiositis idioptica Polineuropata del enfermo crtico Polineuropata desmielinizante crnica (forma recidivante, forma neonatal) Polineuropata en diabetes Spinal plexus or nerve roots (traumatic injury) Brachial plexus disorders Lumbosacral plexus disorders Polymyositis Critical illness polyneuropathy Chronic inflammatory demyelinating polyradiculoneuropathy (neonatal type, relapsing type) Diabetic polyneuropathy
953.9 353.0 353.1 710.4 357.82 357.81
Iatrogenic, toxic, traumatic encephalopathies. Coma Neuromuscular diseases Neuromuscular diseases Neuromuscular diseases Neuromuscular diseases Neuromuscular diseases
357.2 357.1 357.3 357.4 357.9 357.6 357.7 045.10
Polineuropata en Polyneuropathy in systemic Neuromuscular diseases enfermedades del colgeno connective vascular disorders Polineuropata en enfermedades malignas Polineuropata en otras enfermedades Polineuropata no especificada Polyneuropathy in neoplastic Neuromuscular diseases disease Polyneuropathy in other diseases Polyneuropathy, unspecified Neuromuscular diseases Neuromuscular diseases Neuromuscular diseases
Polineuropata por frmacos Drug-induced polyneuropathy Polineuropata por otros txicos Poliomielitis aguda
Polyneuropathy due to other Neuromuscular diseases toxic agents Paralytic poliomyelitis Infectious and inflammatory diseases
131
CIE-9/ ICD-9 742.4
CE/SC
Diagnstico
Diagnose
Section
03
Porencefalia (congnita o verdadera) Porfirias (trastorno del metabolismo) Posmadurez Prader-Willi
Porencephaly (congenital)
CNS malformations. Cranial malformations. Hydrocephalus Inborn errors of metabolism with neurological manifestations
277.1
S/E
Porphyrias
766.22 759.81
S/E S/N
Prolonged gestation of infant Fetal and perinatal neurology Prader-Willi syndrome Malformative syndromes. Chromosomical and genomic diseases Fetal and perinatal neurology
765.1 V61.20
S/E S/E
Prematuridad (otra) Problemas entre padres-hijos (discordia paternofilial) Progeria Proteus Pseudopapiledema Ptosis congnita Ptosis del prpado, excluye ptosis congnita Puncin lumbar (complicacin secundaria) Purinas y pirimidinas (trastorno del metabolismo): Lesch-Nyhan, dficit de adenilosuccinatoliasa, dficit de adenosina deaminasa, sndrome deplecin nucletidos Quiste coloide del III ventrculo
Preterm (other)
Family disturbances / Altered Others family relationships between parents and children Progeria Proteus syndrome, Proteuslike syndrome Pseudopapilledema Congenital ptosis Ptosis of eyelid, congenital ptosis not included Neurocutaneous Neurocutaneous Neuro-ophthalmology/ neurotology Neuro-ophthalmology/ neurotology Neuro-ophthalmology/ neurotology
259.8 757.39 377.24 743.61 374.3 E879.4 277.2
S/E 02 S/E S/E S/E S/E S/E
Lumbar puncture (secondary Iatrogenic, toxic, traumatic complication) encephalopathies. Coma Purines and pirimidines, metabolic disorders: Lesch-Nyhan disease, adenylosuccinate lyase deficiency, etc. Inborn errors of metabolism with neurological manifestations
742.4
04
Neoplasia of uncertain behavior of cholloid cyst of third ventricle
Neoplasms
132
CIE-9/ ICD-9
CE/SC
Diagnstico
Diagnose
Section
M9084/0 S/E M9084/3 S/E 348.0 02
Quiste dermoide Quiste dermoide con transformacin maligna Quiste porenceflico (adquirido) Quistes cerebrales
Dermoid cyst Dermoid cyst with malignant transformation
Morphology of neoplasms of NS Morphology of neoplasms of NS
Porencephalic cyst (acquired) CNS malformations. Cranial malformations. Hydrocephalus Cerebral cysts CNS malformations. Cranial malformations. Hydrocephalus Vertebral column and spinal cord diseases Neuromuscular diseases Infectious and inflammatory diseases Iatrogenic, toxic, traumatic encephalopathies. Coma Neuromuscular diseases Neuromuscular diseases Neuromuscular diseases Neuromuscular diseases Fetal and perinatal neurology Inborn errors of metabolism with neurological manifestations
348.0
01
349.2 728.88 071 990 354.3 353.2 353.3 353.4 766.1
S/E S/E S/E S/E S/E S/E S/E S/E S/E
Quistes menngeos espinales Rabdomilisis, mioglobinuria Rabia Radiacin. Efectos de la misma no especificados Radial (lesin) Races cervicales (lesin) Races dorsales (lesin)
Arachnoid cysts (spinal location) Rhabdomyolysis Rabies Effects of radiation Lesion of radial nerve Cervical root disorders Thoracic root disorders
Races lumbosacras (lesin) Lumbosacral root disorders Recin nacido de peso elevado para la edad gestacional Refsum Exceptionally large baby relating to long gestation Refsum disease
356.3
S/E
362.74
S/E
Retinitis pigmentosa Retinoblastoma Retinopata del prematuro
Pigmentary retinal dystrophy Neuro-ophthalmology/ neurotology Retinoblastoma Retrolental fibroplasia / Retinopathy of prematurity Morphology of neoplasms of NS Neuro-ophthalmology/ neurotology
M9510/3 S/E 362.21 S/E
133
CIE-9/ ICD-9 362.72
CE/SC
Diagnstico
Diagnose
Section
S/E
Retinopata en otros trastornos: Refsum, A-beta-lipoproteinemia Retraso mental moderado (CI 36-50) Retraso mental ligero (CI 70-51) Retraso mental lmite (CI 71-80) Retraso mental profundo (CI < 20) Retraso mental grave (CI 35-21) Retraso psicomotor
Retinal dystrophy in other systemic disorders and syndromes: Refsum, abetalipoproteinemia
318.0
S/E
Moderate mental retardation Developmental and (IQ 36-50) behavioral disorders. Learning disabilities Mild mental retardation (IQ 70-51) Borderline cognitive impairment (IQ 71-80) Developmental and behavioral disorders. Learning disabilities Developmental and behavioral disorders. Learning disabilities
317
S/E
319
02
318.2
S/E
Profound mental retardation Developmental and (IQ < 20) behavioral disorders. Learning disabilities Severe mental retardation (IQ 35-21) Delayed psychomotor development Developmental and behavioral disorders. Learning disabilities Developmental and behavioral disorders. Learning disabilities Developmental and behavioral disorders. Learning disabilities Developmental and behavioral disorders. Learning disabilities Developmental and behavioral disorders. Learning disabilities Iatrogenic, toxic, traumatic encephalopathies. Coma Cerebral palsy. Movement disorders Iatrogenic, toxic, traumatic encephalopathies. Coma
318.1
S/E
783.42
S/E
315.31
01
Retraso simple del lenguaje Speech delay
319
01
Retraso sin especificacin
Mental retardation, not otherwise specified Rett syndrome
330.8
04
Rett
331.81 333.91 349.81
S/E S/E S/E
Reye (sndrome) Rgido acinticohiperekplexia (sndrome) Rinorrea de LCR
Reyes syndrome Hyperekplexia, startle disease Rhinorrhea of cerebrospinal fluid
134
CIE-9/ ICD-9 771.0 759.89
CE/SC
Diagnstico
Diagnose
Section
S/E 16
Rubola congnita Rubinstein-Taybi
Congenital rubella infection Rubinstein-Taybi syndrome
Fetal and perinatal neurology Malformative syndromes. Chromosomical and genomic diseases Others Cerebral palsy. Movement disorders Morphology of neoplasms of NS Malformative syndromes. Chromosomical and genomic diseases Morphology of neoplasms of NS Neuromuscular diseases Infectious and inflammatory diseases Malformative syndromes. Chromosomical and genomic diseases Epilepsy, paroxysmal disorders, sleep disorders Epilepsy, paroxysmal disorders, sleep disorders Malformative syndromes. Chromosomical and genomic diseases Vertebral column and spinal cord diseases Iatrogenic, toxic, traumatic encephalopathies. Coma Fetal and perinatal neurology Malformative syndromes. Chromosomical and genomic diseases
V61.0 333.90
S/E 02
Ruptura familiar Sandifer Sarcoma mieloide (granuloctico) Schinzel-Giedion
Parental divorce Sandifer syndrome Myeloid sarcoma Schinzel-Giedion syndrome
M9930/3 S/E 759.89 17
M9560/0 S/E 138 042 759.89 S/E S/E 18
Schwannoma / Neurinoma Secuelas pospolio Sida (aadir 049.9) Silver-Russell
Neurilemmoma / Schwannoma Post-polio syndrome HIV (add 049.9 AIDS encephalopathy) Silver-Russell syndrome
780.2 337.0 760.71
02 S/E S/E
Sncope (incluye sncope febril) Sncope del seno carotdeo Sndrome alcohlico fetal
Syncope (includes febrile syncope) Carotid sinus syncope Fetal alcohol syndrome
723.3 293.0 779.5 759.9
S/E S/E S/E S/E
Sndrome cervicobraquial Sndrome confusional agudo Sndrome de abstinencia a drogas Sndrome malformativo no especificado
Cervicobrachial syndromes Acute confusional state Drug withdrawal syndrome in newborn Malformative syndrome, unspecified
135
CIE-9/ ICD-9 310.2
CE/SC
Diagnstico
Diagnose
Section
S/E
Sndrome postraumtico (posconmocin cerebral) Sndromes malformativos conocidos que afectan a mltiples rganos o sistemas (otros)
Postconcussive syndrome
Developmental and behavioral disorders. Learning disabilities
759.89
21
Known malformative Malformative syndromes. syndromes affecting multiple Chromosomical and genomic organs or systems (others) diseases Malformative syndromes. Chromosomical and genomic diseases Vertebral column and spinal cord diseases Neurocutaneous
758.3
S/E
Sndromes por Autosomal deletion syndromes, microdeletions, delecin autosmica, microdeleciones, deleciones subtelomeric deletions subtelomricas Siringomielia, siringobulbia Syringomyelia, syringobulbia, syringohydromyelia Sjgren-Larsson (ictiosis congnita) Smith-Lemli-Opitz Sjgren-Larsson (congenital ichthyosis)
336.0
S/E
757.1 759.89
02 19
Smith-Lemli-Opitz syndrome Malformative syndromes. Chromosomical and genomic diseases Smith-Magenis syndrome, deletion 17p11.2 Malformative syndromes. Chromosomical and genomic diseases
758.33
04
Smith-Magenis: delecin 17p11.2
969.9 965.9
S/E S/E
Sobredosis (accidental o no) Overdose (accidental or not) Iatrogenic, toxic, traumatic de psicotrpicos of psychotropic agents encephalopathies. Coma Sobredosis (accidental o no) Overdose (accidental or de analgsicos (opiceos, not) of analgesics (opioids, AINE) antirheumatics) Iatrogenic, toxic, traumatic encephalopathies. Coma
967.0 969.4 962.9
S/E S/E S/E
Sobredosis (accidental o no) Overdose (accidental or not) Iatrogenic, toxic, traumatic de barbitricos of barbiturates encephalopathies. Coma Sobredosis (accidental o no) Overdose (accidental or not) Iatrogenic, toxic, traumatic de benzodiacepinas of benzodiazepines encephalopathies. Coma Sobredosis (accidental o no) de corticoides u otras hormonas y sustitutos sintticos Overdose (accidental or not) of corticosteroids, other hormones or synthetic substitutes Iatrogenic, toxic, traumatic encephalopathies. Coma
136
CIE-9/ ICD-9 966.3
CE/SC
Diagnstico
Diagnose
Section
S/E
Sobredosis (accidental o no) de cualquier anticonvulsionante (excepto fenitona, etosuximida, barbitricos, benzodiacepinas)
Overdose (accidental or not) of any antiepileptic drug (except phenytoin, ethosuximide, barbiturates)
966.2 966.1 969.7
S/E S/E S/E
Sobredosis (accidental o no) Overdose (accidental or not) Iatrogenic, toxic, traumatic de etosuximida of ethosuximide encephalopathies. Coma Sobredosis (accidental o no) Overdose (accidental or not) Iatrogenic, toxic, traumatic de fenitona of phenytoin encephalopathies. Coma Sobredosis (accidental o no) de psicoestimulantes (metilfenidato, anfetaminas) Socializacin (problemas) Overdose (accidental or not) of central nervous system stimulants (methylphenidate, amphetamines) Social and interpersonal problems Somatization disorder, somatoform disorder (unexplained complaints) Somnambulism, night terrors Deaf mutism Spasmus nutans, rhythmic movements (body rocking, head banging, bobble head, jactatio capitis) Sprengel malformation (congenital elevation of scapula) Sturge-Weber syndrome Subependymoma Fetal distress, loss of fetal well-being Iatrogenic, toxic, traumatic encephalopathies. Coma
313.3
S/E
Developmental and behavioral disorders. Learning disabilities Developmental and behavioral disorders. Learning disabilities Epilepsy, paroxysmal disorders, sleep disorders Neuro-ophthalmology/ neurotology Cerebral palsy. Movement disorders
300.81
S/E
Somatizacin (dolencias mltiples) Sonambulismo, terrores nocturnos Sordomudez Spasmus nutans, movimientos repetitivos rtmicos (body rocking, head banging, bobble head) Sprengel. Elevacin congnita de la escpula Sturge-Weber Subependimoma Sufrimiento fetal, prdida de bienestar fetal
307.46 389.7 307.3
S/E S/E 02
755.52
S/E
Malformative syndromes. Chromosomical and genomic diseases Neurocutaneous Morphology of neoplasms of NS Fetal and perinatal neurology
759.6
01
M9383/1 S/E 768.4 S/E
137
CIE-9/ ICD-9 277.89
CE/SC
Diagnstico
Diagnose
Section
01
Sulfatasa (dficit)
Sulfatase deficiency
Inborn errors of metabolism with neurological manifestations Inborn errors of metabolism with neurological manifestations Cerebral palsy. Movement disorders Developmental and behavioral disorders. Learning disabilities Iatrogenic, toxic, traumatic encephalopathies. Coma Cerebral palsy. Movement disorders Cerebral palsy. Movement disorders Cerebral palsy. Movement disorders Cerebral palsy. Movement disorders Cerebral palsy. Movement disorders Morphology of neoplasms of NS Morphology of neoplasms of NS Morphology of neoplasms of NS Neuromuscular diseases Fetal and perinatal neurology Vertebral column and spinal cord diseases Cerebral palsy. Movement disorders
270.4
03
Sulfito oxidasa (dficit)
Sulfite oxidase deficiency
333.90 307.0
03 S/E
Supraversin paroxstica benigna de la mirada Tartamudeo
Paroxysmal tonic upgaze Stuttering, stammering
959.01 333.1 333.1 333.1 333.1 333.1
S/E 01 02 03 04 05
TCE Temblor esencial Temblor esencial larngeo Temblor esencial palatino Temblor familiar Temblor por frmacos Teratoma Teratoma benigno Teratoma maligno Tetania Ttanos neonatal
Traumatic head injury Benign essential tremor Essential laryngeal tremor Essential palatal tremor Familial tremor Drug induced tremor Teratoma Teratoma, benign Teratoma, malignant Tetany Tetanus neonatorum
M9080/1 S/E M9080/0 S/E M9080/3 S/E 781.7 771.3 344.0 S/E S/E S/E
Tetrapleja, tetraparesia (por Tetraplegia, tetraparesis lesin medular adquirida) (secondary to acquired spinal cord lesion) Tics Tics
307.2
S/E
138
CIE-9/ ICD-9 307.22 307.21 313.2
CE/SC
Diagnstico
Diagnose
Section
S/E S/E S/E
Tics crnicos Tics transitorios Timidez y retraimiento social Tnnitus Tirosinemia, alteraciones del triptfano (ECM de aminocidos aromticos excepto fenilalanina) Tirotoxicosis neonatal Tortcolis congnita
Chronic tics Transient tics Shyness
Cerebral palsy. Movement disorders Cerebral palsy. Movement disorders Developmental and behavioral disorders. Learning disabilities Neuro-ophthalmology/ neurotology Inborn errors of metabolism with neurological manifestations
388.3 270.2
S/E 01
Tinnitus Hypertyrosinemia, other inborn errors of the metabolism of aromatic aminoacids (except phenylalanine) Neonatal thyrotoxicosis Congenital torticollis
775.3 754.1
S/E S/E
Fetal and perinatal neurology CNS malformations. Cranial malformations. Hydrocephalus Cerebral palsy. Movement disorders Cerebral palsy. Movement disorders
333.83 781.93 333.83 772.0 758.4
01 S/E 02 S/E S/E
Tortcolis espasmdica Tortcolis ocular Tortcolis paroxstica benigna Transfusin fetomaterna o fetofetal Traslocacin autosmica balanceada en individuo normal Trastorno del aprendizaje
Spasmodic torticollis Torticollis, in ocular disease
Benign paroxysmal torticollis Cerebral palsy. Movement disorders Feto-fetal or fetal-maternal transfusion syndrome Balanced autosomal translocation in normal individual Learning disabilities Fetal and perinatal neurology Malformative syndromes. Chromosomical and genomic diseases Developmental and behavioral disorders. Learning disabilities
315.9
S/E
139
CIE-9/ ICD-9 756.1
CE/SC
Diagnstico
Diagnose
Section
02
Trastorno de columna vertebral (espondilolistesis, espondilolisis, pinzamiento, espondilopata inflamatoria, hemivrtebra, fusin o ausencia congnita de vrtebra) Trastorno de la conducta (secundario, trastorno de adaptacin) Trastorno de la conducta (en la infancia) Trastorno de la marcha Trastorno de orientacin visuoespacial Trastorno del desarrollo de la coordinacin Trastorno desintegrativo infantil Trastorno emocional (distimia en la infancia) Trastorno generalizado del desarrollo no especificado Trastorno por dficit atencin con/sin hiperactividad Trastornos convulsivos no epilpticos (hiperekplexia, pseudocrisis, sncope convulsivo)
Vertebral disorder Vertebral column and spinal (spondylolisthesis, cord diseases spondylolysis, inflammatory conditions, vertebral malformations...)
309.3
S/E
Adjustment disorder, adjustment reaction
Developmental and behavioral disorders. Learning disabilities
312.9
S/E
Behavior disorder (disruptive Developmental and behavioral disorder) behavioral disorders. Learning disabilities Gait difficulties Visual-spatial and perception disorder Neuromuscular diseases Developmental and behavioral disorders. Learning disabilities
719.7 315.8
S/E S/E
315.4
S/E
Developmental coordination Developmental and disorder behavioral disorders. Learning disabilities Childhood disintegrative disorder Emotional disorder (dysthymia in childhood) Pervasive developmental disorder not otherwise specified Attention deficit hyperactivity disorder Paroxysmal nonepileptic events (hiperekplexia, pseudoseizures, convulsive syncope) Developmental and behavioral disorders. Learning disabilities Developmental and behavioral disorders. Learning disabilities Developmental and behavioral disorders. Learning disabilities Developmental and behavioral disorders. Learning disabilities Epilepsy, paroxysmal disorders, sleep disorders
299.1
S/E
313.9
S/E
299.9
S/E
314.0
S/E
780.39
07
333.99
S/E
Trastornos del movimiento Movement disorder (other: (otros): piernas inquietas restless legs syndrome)
Cerebral palsy. Movement disorders
140
CIE-9/ ICD-9 767.4
CE/SC
Diagnstico
Diagnose
Section
S/E
Traumatismo de la columna Spine and spinal cord injury vertebral y de la mdula due to birth trauma espinal en el nacimiento Traumatismo del cuero cabelludo en el nacimiento Traumatismo del esqueleto en el nacimiento (otros) Traumatismo del nervio facial al nacimiento Traumatismo del plexo braquial al nacimiento Traumatismo obsttrico al nacimiento Traumatismos de pares craneales y nervios perifricos al nacimiento (otros) Treacher-Collins Scalp injury due to birth trauma
Fetal and perinatal neurology Fetal and perinatal neurology
767.1 767.3 767.5 767.6 767.9 767.7
Other injuries to skeleton due Fetal and perinatal to birth trauma neurology Facial nerve injury due to birth trauma Fetal and perinatal neurology
Brachial plexus injury due to Fetal and perinatal birth trauma neurology Other birth trauma Other cranial and peripheral nerve injuries due to birth trauma Treacher-Collins syndrome Fetal and perinatal neurology Fetal and perinatal neurology
756.0
06
Malformative syndromes. Chromosomical and genomic diseases Vascular diseases
437.6
S/E
Trombosis de seno venoso intracraneal (incluye trombosis del seno cavernoso) Tuberculoma cerebral Tumor del seno endodrmico Tumor neuroectodrmico primitivo Tumor neuroepitelial disembrioplsico Tumor teratoide/rabdoide atpico
Sino-venous thrombosis (includes cavernous sinus thrombosis) Cerebral tuberculoma Yolk sac tumour Primitive neuroectodermal tumour Dysembryoplastic neuroepithelial tumour Atypical teratoid/rhabdoid tumour
013.2
S/E
Infectious and inflammatory diseases Morphology of neoplasms of NS Morphology of neoplasms of NS Morphology of neoplasms of NS Morphology of neoplasms of NS Morphology of neoplasms of NS Neuromuscular diseases
M9071/3 S/E M9473/3 S/E M9413/0 S/E M9508/3 S/E M9085/3 S/E 354.0 S/E
Tumores germinales mixtos Mixed germ cell tumour Tnel carpiano Carpal tunnel syndrome
141
CIE-9/ ICD-9 758.6
CE/SC
Diagnstico
Diagnose
Section
S/E
Turner
Turner syndrome
Malformative syndromes. Chromosomical and genomic diseases Neuro-ophthalmology/ neurotology Fetal and perinatal neurology Vascular diseases
364.3
S/E
Uvetis Varicela congnita Vasculitis y arteritis cerebrales Velocardiofacial: delecin 22q11.2 Vrtigo central
Unspecified iridocyclitis/ uveitis Congenital chickenpox Cerebral vasculitis, cerebral arteritis
771.2/052 S/E 437.4 758.32 S/E S/E
Velo-cardio-facial syndrome, Malformative syndromes. deletion 22q11.2 Chromosomical and genomic diseases Vertigo of central origin Neuro-ophthalmology/ neurotology Neuro-ophthalmology/ neurotology Neuro-ophthalmology/ neurotology Neuro-ophthalmology/ neurotology Neuro-ophthalmology/ neurotology
386.2 386.11 386.10 780.4
S/E S/E S/E S/E
Vrtigo paroxstico benigno, Benign paroxysmal vrtigo posicional benigno positional vertigo Vrtigo perifrico Vrtigo-mareo Peripheral vertigo Dizziness and giddiness, light-headedness and vertigo Disorders of other visual pathways
377.6 771.89/ 042 995.53 266.2
S/E S/E
Vas pticas, afectacin VIH de transmisin vertical
Human immunodeficiency Fetal and perinatal virus infection (HIV), vertical neurology transmission Child sexual abuse Vitamin B12 (inborn error of metabolism of) Vogt-Koyanagi-Harada syndrome Vomiting (cyclic, recurrent) Von Hippel-Lindau syndrome Iatrogenic, toxic, traumatic encephalopathies. Coma Inborn errors of metabolism with neurological manifestations Neuro-ophthalmology/ neurotology Headache and related disorders Neurocutaneous
S/E 03
Violacin a menores Vitamina B12 (trastorno del metabolismo) Vogt-Koyanagi-Harada Vmitos cclicos Von Hippel-Lindau
364.24 536.2 759.6
S/E S/E 02
142
CIE-9/ ICD-9 756.89 759.89
CE/SC
Diagnstico
Diagnose
Section
03 20
Waardenburg Weaver
Waardenburg syndrome Weaver syndrome
Neurocutaneous Malformative syndromes. Chromosomical and genomic diseases Epilepsy, paroxysmal disorders, sleep disorders
345.6 758.33
S/E 05
West tpico, atpico y variantes
West syndrome (typical, atypical and variants)
Williams: delecin: 7q11.23 Williams syndrome, deletion Malformative syndromes. 7q11.23 Chromosomical and genomic diseases Wilson X frgil Wilson disease Fragile X syndrome Cerebral palsy. Movement disorders Malformative syndromes. Chromosomical and genomic diseases Morphology of neoplasms of NS Neurocutaneous Iatrogenic, toxic, traumatic encephalopathies. Coma
275.1 759.83
S/E S/E
M9424/3 S/E 757.33 995.55 02 S/E
Xantoastrocitoma pleomrfico Xerodermia pigmentosa Zarandeado (sndrome del nio)
Pleomorphic xanthroastrocytoma Xeroderma pigmentosum Shaken infant syndrome
143
2008, de los autores 2008, de la presente edicin: Viguera Editores SL Plaza Tetun, 7. 08010 Barcelona, Espaa www.viguera.com Diseo y diagramacin: Llus Mestres ISBN: 978-84-85424-83-2 Printed in EU by IG Galileo SA D.L.: B-38021-2008

CIE-9 Códico Neuropediatrico

Diunggah oleh

Informasi Dokumen

Hak Cipta

Format Tersedia

Bagikan dokumen Ini

Bagikan atau Tanam Dokumen

Opsi Berbagi

Apakah menurut Anda dokumen ini bermanfaat?

Apakah konten ini tidak pantas?

Hak Cipta:

Format Tersedia

CIE-9 Códico Neuropediatrico

Diunggah oleh

Hak Cipta:

Format Tersedia

Codificacin en Neurologa Peditrica (CIE-9) Coding in Neuropediatrics (ICD-9)

Disponible en: www.neurologia.com/cie-9

Clasificacin por patologas Classification of disorders

Clasificacin alfabtica Alphabetical classification

Codificacin en Neurologa Peditrica (CIE-9) Coding in Neuropediatrics (ICD-9)

8. 9. 10. 11. 12.I

14. 15. 16. 17. 18. 19. 20. 21.

Clasificacin alfabtica Alphabetical classification (Spanish)

La codificacin en neurologa peditrica: un buen indicador de la calidad asistencial

Editorial La codificacin en neurologa peditrica: un buen indicador de la calidad asistencial

Codificacin en neurologa peditrica basada en la CIE-9, 5. ed. (2006)

Introduccin Codificacin en neurologa peditrica basada en la CIE-9, 5. ed. (2006)

Introduccin Codificacin en neurologa peditrica basada en la CIE-9, 5. ed. (2006)

Introduccin Codificacin en neurologa peditrica basada en la CIE-9, 5. ed. (2006)

Introduccin Codificacin en neurologa peditrica basada en la CIE-9, 5. ed. (2006)

Introduccin Codificacin en neurologa peditrica basada en la CIE-9, 5. ed. (2006)

Coding in Neuropediatrics based on the ICD-9, 5th ed. (2006)

Introduction Coding in Neuropediatrics based on the ICD-9, 5th ed. (2006)

Introduction Coding in Neuropediatrics based on the ICD-9, 5th ed. (2006)

Materials and methods

Introduction Coding in Neuropediatrics based on the ICD-9, 5th ed. (2006)

Introduction Coding in Neuropediatrics based on the ICD-9, 5th ed. (2006)

Introduccin Coding in Neuropediatrics based on the ICD-9, 5th ed. (2006)

Clasificacin por patologas Classification of disorders

1. Neurologa fetal y perinatal 1. Fetal and perinatal neurology

Hipotiroidismo neonatal Efecto de la analgesia y anestesia maternas sobre el feto/RN

Congenital hypothyroidism Maternal anesthesia and analgesia affecting fetus or newborn

1. Neurologa fetal y perinatal 1. Fetal and perinatal neurology

CIE-9/ ICD-9 771.1 771.2

CE/ SC S/E S/E

775.3 775.4 775.6 779.1 779.2 779.4 779.5 779.7 779.89

S/E S/E S/E S/E S/E S/E S/E S/E S/E

CIE-9/ ICD-9 754.0 754.1 756.0 756.0 756.0 756.0

Dolicocefalia Tortcolis congnita Craneosinstosis Crouzon Macrocefalia Malformacin craneofacial

Dolichocephaly Congenital torticollis Craniosynostosis Crouzon syndrome Macrocephaly Craniofacial malformation

CIE-9/ ICD-9 758.33 758.33 758.39 758.39 758.4 758.5

CE/ SC 04 05 01 02 S/E S/E

S/E S/E S/E S/N S/E S/E 01 02 03 04 05 06 07 08 09 10 11 12 13

4. Sndromes neurocutneos 4. Neurocutaneous syndromes

CE/ SC 02 S/E S/E S/E S/E S/E S/E 01 02

307.9 332.0 332.1 333.0 333.0 333.0

S/E S/E S/E 01 02 03

CIE-9/ ICD-9 784.3 784.4 784.5 784.69 787.6 788.36 995.59

CE/ SC S/E S/E S/E S/E S/E S/E S/E

CIE-9/ ICD-9 345.50 345.50 345.50 345.50

01 02 03 04 S/E S/E S/E 01 02 03 01

345.81 345.81 345.81 345.81

CE/ SC S/E 01 02 03 04 05 06 S/E

S/E S/E S/E 01 02 03 04 05 01 02 S/E 01 02 03

CIE-9/ ICD-9 780.39

780.39 780.39 780.39

780.5 780.51 780.54 780.55 780.59 780.59 780.6 794.02

S/E S/E S/E S/E 01 02 S/E S/E

8. Cefaleas 8. Headaches and related disorders

9. Patologa infecciosa e inflamatoria 9. Infectious and inflammatory disorders

9. Patologa infecciosa e inflamatoria 9. Infectious and inflammatory disorders

CIE-9/ ICD-9 323.4

S/E 01 02 03 01 02 S/E S/E S/E S/E

10. Patologa vascular 10. Vascular disorders

CE/ SC S/E S/E S/E S/E S/E S/E S/E 01 S/E 02 01

348.31 348.4 348.5 349.1 349.81 349.82

02 02 S/E S/E S/E S/E

388.61 437.2 572.2 588.89 780.01 780.02 780.03

S/E S/E S/E S/E S/E S/E S/E