N103 Hematological Disorders Pediatric Nursing NAME:______________________________________SECTION:____________CLASS NO._____ Write your answers before the number in CAPI A!

letters Ron, a 4 y/o was admitted in the pediat i! wa d "e!a#se o$ easy " #isin%. &e was %i'en a dia%nosis o$ a!#te (ympho!yti! (e#)emia. *. The symptoms o$ (e#)emia may "e asso!iated with the $o((owin% E+CE,T: a. E-!essi'e p o(i$e ation !. In'asion o$ 'as!#(a st #!t# es ". In$i(t ation o$ s# o#ndin% st #!t# es d. &ype $#n!tionin% ./C 0. Ron is a"o#t to #nde %o "one ma ow "iopsy. As the n# se assi%ned, yo# %i'e inst #!tions to the mothe and the !hi(d e%a din% the p o!ed# e. .hi!h o$ the $o((owin% statements he(ps in the assessment o$ the mothe 1s #nde standin% o$ the p o!ed# e2 a. 3they wi(( #se a (a %e need(e to %et "one ma ow $ om the "a!)4 ". 3the e is a p o"(em a"o#t in$e!tion d# in% the p o!ed# e4 !. 3a$te ta)in% some ma ow, they wi(( ep(a!e it with no ma( ma ow4 d. 3Ron m#st "e sedated d# in% the p o!ed# e4 5. To he(p the pa ents mana%e Ron1s sepa ation an-iety, yo# may s#%%est a. Lea'e the !hi(d a$te he is as(eep ". Sho ten the 'isits !. / in% his $a'o ite toys $ om home d. Te(( the !hi(d that they a e (ea'in% and when they wi(( et# n 4. Ron #nde went !hemothe apy. /e$o e he was dis!ha %ed, yo# %i'e yo# hea(th tea!hin% a"o#t Ron1s !ondition. 6o# wo#(d )now that $# the tea!hin% is ne!essa y when the mothe states: a. 3he needs to eat $ #its and 'e%eta"(es, $ esh $ om the sto e4 ". 3he needs to !ontin#e and "e !omp(iant with his $o((ow7#p4 !. 3i$ he has mi(d $e'e , we sho#(d ha'e him !he!)ed #p4 d. 3i$ he has mo#th so es, we ha'e to ha'e him !he!)ed #p4 8. ,ediat i! patients with (e#)emia a e p one to in$e!tion "e!a#se: a. ./C is easi(y hemo(y9ed. ". ./C a e $ew, and a e o#tn#m"e ed "y the in'adin% mi! oo %anism. !. ./C is immat# e, and is #na"(e to pha%o!ytose "a!te ia. d. R/Cs a e mi! o!yti! and hypo!h omi!. :ante Lim, an *; y/o, was admitted "e!a#se o$ se'e e <oint pains. &e was a(so noted to ha'e easy " #isin%, and that he "(eeds easi(y and p o$#se(y when he %ets simp(e s! apes = !#ts. >. 6o# assessment is a. &emophi(ia !. IT, ". :en%#e ?e'e d. A th itis @. The main %oa( o$ !a e $o :ante is a. (owe the is) o$ "(eedin% ". p o'ide adeA#ate $(#ids to p e'ent sho!) !. p o'ide s#ppo t to patient and $ami(y d. p e'ent the sp ead o$ the disease ;. 6o# )now that his disease is t ansmitted %eneti!a((y th o#%h a. se-7(in)ed 6 !h omosome ". se-7(in)ed + !h omosome !. a#tosoma( e!essi'e t ait d. a#tosoma( dominant t ait B. To t eat his diso de , the $o((owin% is #sed E+CE,T: a. ?a!to CIII !. ? esh $ o9en p(asma ". C yop e!ipitate d. ? esh who(e "(ood *D. As his n# se yo# p epa e hea(th tea!hin% "e$o e he %oes home. It is impo tant that yo# (et the !hi(d "e esponsi"(e $o his disease. .hi!h o$ the $o((owin% hea(th tea!hin%s "est show this p in!ip(e2 a. Tea!h him set o$ (imitations to p e'ent "(eedin% episodes ". Tea!h him to a(e t his pediat i!ian in !ase o$ "(eedin% !. Tea!h him that his disease is in!# a"(e d. Tea!h him how to p e'ent t ansmission o$ his disease **. Eenna, an *; y/o is dia%nosed with I on de$i!ien!y anemia. She is !# ent(y ta)in% o a( i on s#pp(ements. The $o((owin% a e impo tant hea(th tea!hin% in ta)in% i on s#pp(ements E+CE,T: a. 36o# ha'e to ta)e yo# medi!ations "etween mea(s4 ". 36o# may ta)e o an%e <#i!e with it4 !. 3It may !a#se yo# stoo( to t# n "(a!)4 d. 3The ta"(ets may stain yo# teeth, "#t it1s on(y tempo a y4 *0. Fa (, an ; month o(d "oy, was " o#%ht to the O,: $o his e%#(a !he!)7#p. On yo# inte a!tion with the mothe , yo# (ea ned that she is !on!e ned that he "a"y mi%ht ha'e i on de$i!ien!y anemia. The $o((owin% a e app op iate hea(th tea!hin%s E+CE,T: a. 3Comme !ia( in$ant !e ea(s ha'e a hi%he i on !ontent than " east mi()4 ". 3Comme !ia((y p epa ed mi() is sti(( the pe $e!t $ood $o yo# "a"y4 !. 3.ei%ht %ain $o yo# !hi(d may not "e eA#a( with "ein% a Ghea(thy1 !hi(d4 d. 36o# may en!o#nte di$$i!#(ty in %i'in% $ood othe than what he eats, "#t yo# m#st "e $i m a"o#t it4

*5. /a"y Fa ( was "o n *0 ho# s a%o to a type O HIJ mothe . On yo# assessment, yo# noted that he is <a#ndi!ed. &e <a#ndi!e is most (i)e(y: a. No ma( hemo(ysis o$ his R/Cs ". A/O in!ompati"i(ity !. Rh in!ompati"i(ity d. Non o$ the a"o'e *4. A K*,D mothe app oa!hes yo# in the O,:, she te((s yo# that she1s !on!e ned a"o#t he p e%nan!y sin!e she is Rh H7J. .hi!h o$ the $o((owin% is the most app op iate hea(th tea!hin%2 a. 36o# sho#(d "e imm#ni9ed with RhoKAM today4 ". 36o# sho#(d "e imm#ni9ed with RhoKAM within @0 ho# s a$te de(i'e y4 !. 36o# sho#(d "e imm#ni9ed with RhoKAM within @0 ho# s "e$o e de(i'e y4 d. 36o# sho#(d "e imm#ni9ed with RhoKAM a$te the "i th o$ yo# 0nd !hi(d.4 *8. In patients with Tha(assemia, on o$ the p o"(ems is hemoside osis. .hi!h o$ the $o((owin% is the app op iate t eatment $o this p o"(em2 a. :e$e o-amine !. ,eni!i((in ". Sp(ene!tomy d. /(ood T ans$#sion *>. The diso de IT, is !ha a!te i9ed "y the $o((owin% E+CE,T: a. E-!essi'e dest #!tion o$ p(ate(ets !. /e(ie'ed to "e a#to7imm#ne ". ,ete!hiae "eneath the s)in d. A%e o$ onset is a o#nd ;7*0 y/o *@. A mothe , whose @y/o !hi(d is e!o'e in% $ om IT, a$te 0 mos t eatment, app oa!hes yo# and as)s $o ad'i!e. .hi!h o$ the $o((owin% is the most app op iate a. 3As (on% as his p(ate(et !o#nt is "e(ow 8D,DDD/mm5 yo# ha'e to est i!t he a!ti'ities4 ". 3She may pa ti!ipate in some a!ti'ities s#!h as hide and see)4 !. 3I$ she has pain, yo# may %i'e aspi in4 d. 3IT, is a(ways se($7(imitin%, so yo# ha'e nothin% to wo y a"o#t4 *;. A !hi(d with IT, is a"o#t to #nde %o sp(ene!tomy. .hi!h o$ the $o((owin% is an app op iate (on% te m mana%ement $o patients post7sp(ene!tomy2 a. Ki'e pne#mo!o!!a( and menin%o!o!!a( 'a!!inations post7op ". Ki'e pne#mo!o!!a( and menin%o!o!!a( 'a!!ination p e7op !. ,eni!i((in in<e!tions "e$o e his s!hed#(ed ope ation d. Feep patient in e'e se iso(ation whi(e #nde %oin% anti"ioti! the apy *B. A$te !he!)in% on a patient with :en%#e &emo ha%i! ?e'e , yo# noted the $o((owin% si%ns. .hi!h wo#(d "e yo# $i st p io ity2 a. /, o$ *DD/;D !. ,#(se ate o$ BB ". Non7"(an!hin% ash d. RR o$ 0* 0D. The p ima y pathophysio(o%i! e-p(anation o$ &eno!h7S!hon(ein Synd ome is: a. In! eased 'as!#(a pe mea"i(ity ". :est #!tion o$ the p(ate(ets !. ,(ate(ets a e ina!ti'ated "y a#to imm#no(o%i! me!hanisms d. The e is e-ha#stion o$ !oa%#(ation $a!to s !a#sin% spontaneo#s "(eedin% "#$ %" &A!'$( Write "#$ if it)s true and lea*e it +!AN, if false- Write your answers before the number 0*. &eno!h7S!hon(ein p# p# a is !a#sed "y a hype sensiti'ity ea!tion to a a((e %en. 00. I on de$i!ien!y anemia is !ommon amon% ado(es!ents main(y "e!a#se o$ dietin% $ads asso!iated with this a%e. 05. In hemophi(ia /, the e is a de$i!ien!y o$ $a!to +I. 04. ,atients with (e#)emia ha'e a "ette p o%nosis espe!ia((y i$ a e in the a%es "etween 07B y/o. 08. In patients with A/O in!ompati"i(ity, a !hi(d who is "(ood type / may ha'e a ea!tion i$ the mothe 1s "(ood type is O. 0>. The p o"(em in A/O in!ompati"i(ity is that the anti"odies $ om the "a"y a%%(#tinates the mothe 1s R/C 0@. &emophi(ia is a %eneti! disease whe ein a hemophi(i! $athe may t ansmit the disease to his son. 0;. In tha(assemia, the e is de$e!ti'e p od#!tion o$ the L7hemo%(o"in !a#sin% the disease. 0B. The main $o m o$ t eatment in patients with tha(assemia is (i$e7(on% "(ood t ans$#sion 5D. I$ the anemia de'e(ops s(ow(y o'e time, !hi(d en a e #s#a((y a"(e to adapt to the $a((in% hemo%(o"in (e'e(s. .A CHIN/ 0P$( .atch column A with column + Assessment findings +lood dyscrasias 5*. pa ieta( and $ onta( "ossin%, p ot #sion o$ A. &emophi(ia #ppe teeth, " oad and $(attened nose. /. :&? 50. pa((o , ano e-ia, $ati%#e easi(y C. I on :e$i!ien!y Anemia 55. (a %e a eas o$ asymmet i!a( e!!hymosis :. IT, p ominent o'e the (e%s. E. Tha(assemia 54. p o(on%ed "(eedin% anywhe e in the "ody, e-!essi'e " #isin%, hema th osis 58. <oint pain, HIJ to# niA#et test, $e'e s#dden onset KOO:LMCF

N103 Hematological Disorders Pediatric Nursing NAME:_______________________________ CLASS NO.__________ .A CHIN/ 0P$( .atch column A with column + Assessment findings +lood dyscrasias *. pa ieta( and $ onta( "ossin%, p ot #sion o$ A. :&? #ppe teeth, " oad and $(attened nose. /. &emophi(ia 0. pa((o , ano e-ia, $ati%#e easi(y C. Tha(assemia 5. (a %e a eas o$ asymmet i!a( e!!hymosis :. IT, p ominent o'e the (e%s. E. I on :e$i!ien!y Anemia 4. p o(on%ed "(eedin% anywhe e in the "ody, e-!essi'e " #isin%, hema th osis 8. <oint pain, HIJ to# niA#et test, $e'e s#dden onset .#! IP!$ CH%IC$( Write your answers before the number in CAPI A! letters :ante Lim, an *; y/o, was admitted "e!a#se o$ se'e e <oint pains. &e was a(so noted to ha'e easy " #isin%, and that he "(eeds easi(y and p o$#se(y when he %ets simp(e s! apes = !#ts. >. 6o# assessment is a. &emophi(ia !. IT, ". :en%#e ?e'e d. A th itis @. The main %oa( o$ !a e $o :ante is a. (owe the is) o$ "(eedin% ". p o'ide adeA#ate $(#ids to p e'ent sho!) !. p o'ide s#ppo t to patient and $ami(y d. p e'ent the sp ead o$ the disease ;. 6o# )now that his disease is t ansmitted %eneti!a((y th o#%h a. se-7(in)ed 6 !h omosome ". se-7(in)ed + !h omosome !. a#tosoma( e!essi'e t ait d. a#tosoma( dominant t ait B. To t eat his diso de , the $o((owin% is #sed E+CE,T: a. ?a!to CIII !. ? esh $ o9en p(asma ". C yop e!ipitate d. ? esh who(e "(ood *D. As his n# se yo# p epa e hea(th tea!hin% "e$o e he %oes home. It is impo tant that yo# (et the !hi(d "e esponsi"(e $o his disease. .hi!h o$ the $o((owin% hea(th tea!hin%s "est show this p in!ip(e2 a. Tea!h him set o$ (imitations to p e'ent "(eedin% episodes ". Tea!h him to a(e t his pediat i!ian in !ase o$ "(eedin% !. Tea!h him that his disease is in!# a"(e d. Tea!h him how to p e'ent t ansmission o$ his disease **. In patients with Tha(assemia, on o$ the p o"(ems is hemoside osis. .hi!h o$ the $o((owin% is the app op iate t eatment $o this p o"(em2 a. :e$e o-amine !. ,eni!i((in ". Sp(ene!tomy d. /(ood T ans$#sion *0. The diso de IT, is !ha a!te i9ed "y the $o((owin% E+CE,T: a. E-!essi'e dest #!tion o$ p(ate(ets !. /e(ie'ed to "e a#to7imm#ne ". ,ete!hiae "eneath the s)in d. A%e o$ onset is a o#nd ;7*0 y/o *5. A mothe , whose @y/o !hi(d is e!o'e in% $ om IT, a$te 0 mos t eatment, app oa!hes yo# and as)s $o ad'i!e. .hi!h o$ the $o((owin% is the most app op iate a. 3As (on% as his p(ate(et !o#nt is "e(ow 8D,DDD/mm5 yo# ha'e to est i!t he a!ti'ities4 ". 3She may pa ti!ipate in some a!ti'ities s#!h as hide and see)4 !. 3I$ she has pain, yo# may %i'e aspi in4 d. 3IT, is a(ways se($7(imitin%, so yo# ha'e nothin% to wo y a"o#t4 *4. A !hi(d with IT, is a"o#t to #nde %o sp(ene!tomy. .hi!h o$ the $o((owin% is an app op iate (on% te m mana%ement $o patients post7sp(ene!tomy2 a. Ki'e pne#mo!o!!a( and menin%o!o!!a( 'a!!inations post7op ". Ki'e pne#mo!o!!a( and menin%o!o!!a( 'a!!ination p e7op !. ,eni!i((in in<e!tions "e$o e his s!hed#(ed ope ation d. Feep patient in e'e se iso(ation whi(e #nde %oin% anti"ioti! the apy *8. A$te !he!)in% on a patient with :en%#e &emo ha%i! ?e'e , yo# noted the $o((owin% si%ns. .hi!h wo#(d "e yo# $i st p io ity2 a. /, o$ *DD/;D !. ,#(se ate o$ BB ". Non7"(an!hin% ash d. RR o$ 0* *>. The p ima y pathophysio(o%i! e-p(anation o$ &eno!h7S!hon(ein Synd ome is: a. In! eased 'as!#(a pe mea"i(ity ". :est #!tion o$ the p(ate(ets !. ,(ate(ets a e ina!ti'ated "y a#to imm#no(o%i! me!hanisms d. The e is e-ha#stion o$ !oa%#(ation $a!to s !a#sin% spontaneo#s "(eedin% *@. Eenna, an *; y/o is dia%nosed with I on de$i!ien!y anemia. She is !# ent(y ta)in% o a( i on s#pp(ements. The $o((owin% a e impo tant hea(th tea!hin% in ta)in% i on s#pp(ements E+CE,T: a. 36o# ha'e to ta)e yo# medi!ations "etween mea(s4 ". 36o# may ta)e o an%e <#i!e with it4 !. 3It may !a#se yo# stoo( to t# n "(a!)4 d. 3The ta"(ets may stain yo# teeth, "#t it1s on(y tempo a y4

*;. Fa (, an ; month o(d "oy, was " o#%ht to the O,: $o his e%#(a !he!)7#p. On yo# inte a!tion with the mothe , yo# (ea ned that she is !on!e ned that he "a"y mi%ht ha'e i on de$i!ien!y anemia. The $o((owin% a e app op iate hea(th tea!hin%s E+CE,T: a. 3Comme !ia( in$ant !e ea(s ha'e a hi%he i on !ontent than " east mi()4 ". 3Comme !ia((y p epa ed mi() is sti(( the pe $e!t $ood $o yo# "a"y4 !. 3.ei%ht %ain $o yo# !hi(d may not "e eA#a( with "ein% a Ghea(thy1 !hi(d4 d. 36o# may en!o#nte di$$i!#(ty in %i'in% $ood othe than what he eats, "#t yo# m#st "e $i m a"o#t it4 *B. /a"y Fa ( was "o n *0 ho# s a%o to a type O HIJ mothe . On yo# assessment, yo# noted that he is <a#ndi!ed. &e <a#ndi!e is most (i)e(y: a. No ma( hemo(ysis o$ his R/Cs ". A/O in!ompati"i(ity !. Rh in!ompati"i(ity d. Non o$ the a"o'e 0D. A K*,D mothe app oa!hes yo# in the O,:, she te((s yo# that she1s !on!e ned a"o#t he p e%nan!y sin!e she is Rh H7J. .hi!h o$ the $o((owin% is the most app op iate hea(th tea!hin%2 a. 36o# sho#(d "e imm#ni9ed with RhoKAM today4 ". 36o# sho#(d "e imm#ni9ed with RhoKAM within @0 ho# s a$te de(i'e y4 !. 36o# sho#(d "e imm#ni9ed with RhoKAM within @0 ho# s "e$o e de(i'e y4 d. 36o# sho#(d "e imm#ni9ed with RhoKAM a$te the "i th o$ yo# 0nd !hi(d. Ron, a 4 y/o was admitted in the pediat i! wa d "e!a#se o$ easy " #isin%. &e was %i'en a dia%nosis o$ a!#te (ympho!yti! (e#)emia. 0*. The symptoms o$ (e#)emia may "e asso!iated with the $o((owin% E+CE,T: a. E-!essi'e p o(i$e ation !. In'asion o$ 'as!#(a st #!t# es ". In$i(t ation o$ s# o#ndin% st #!t# es d. &ype $#n!tionin% ./C 00. Ron is a"o#t to #nde %o "one ma ow "iopsy. As the n# se assi%ned, yo# %i'e inst #!tions to the mothe and the !hi(d e%a din% the p o!ed# e. .hi!h o$ the $o((owin% statements he(ps in the assessment o$ the mothe 1s #nde standin% o$ the p o!ed# e2 a. 3they wi(( #se a (a %e need(e to %et "one ma ow $ om the "a!)4 ". 3the e is a p o"(em a"o#t in$e!tion d# in% the p o!ed# e4 !. 3a$te ta)in% some ma ow, they wi(( ep(a!e it with no ma( ma ow4 d. 3Ron m#st "e sedated d# in% the p o!ed# e4 05. To he(p the pa ents mana%e Ron1s sepa ation an-iety, yo# may s#%%est a. Lea'e the !hi(d a$te he is as(eep ". Sho ten the 'isits !. / in% his $a'o ite toys $ om home d. Te(( the !hi(d that they a e (ea'in% and when they wi(( et# n 04. Ron #nde went !hemothe apy. /e$o e he was dis!ha %ed, yo# %i'e yo# hea(th tea!hin% a"o#t Ron1s !ondition. 6o# wo#(d )now that $# the tea!hin% is ne!essa y when the mothe states: a. 3he needs to eat $ #its and 'e%eta"(es, $ esh $ om the sto e4 ". 3he needs to !ontin#e and "e !omp(iant with his $o((ow7#p4 !. 3i$ he has mi(d $e'e , we sho#(d ha'e him !he!)ed #p4 d. 3i$ he has mo#th so es, we ha'e to ha'e him !he!)ed #p4 08. ,ediat i! patients with (e#)emia a e p one to in$e!tion "e!a#se: a. ./C is easi(y hemo(y9ed. ". ./C a e $ew, and a e o#tn#m"e ed "y the in'adin% mi! oo %anism. !. ./C is immat# e, and is #na"(e to pha%o!ytose "a!te ia. d. R/Cs a e mi! o!yti! and hypo!h omi!. "#$ %" &A!'$( Write "#$ if it)s true and lea*e it +!AN, if false- Write your answers before the number 0>. The p o"(em in A/O in!ompati"i(ity is that the anti"odies $ om the "a"y a%%(#tinates the mothe 1s R/C 0@. &emophi(ia is a %eneti! disease whe ein a hemophi(i! $athe may t ansmit the disease to his son. 0;. In tha(assemia, the e is de$e!ti'e p od#!tion o$ the L7hemo%(o"in !a#sin% the disease. 0B. The main $o m o$ t eatment in patients with tha(assemia is (i$e7(on% "(ood t ans$#sion 5D. I$ the anemia de'e(ops s(ow(y o'e time, !hi(d en a e #s#a((y a"(e to adapt to the $a((in% hemo%(o"in (e'e(s. 5*. &eno!h7S!hon(ein p# p# a is !a#sed "y a hype sensiti'ity ea!tion to a a((e %en. 50. I on de$i!ien!y anemia is !ommon amon% ado(es!ents main(y "e!a#se o$ dietin% $ads asso!iated with this a%e. 55. In hemophi(ia /, the e is a de$i!ien!y o$ $a!to +I. 54. ,atients with (e#)emia ha'e a "ette p o%nosis espe!ia((y i$ a e in the a%es "etween 07B y/o. 58. In patients with A/O in!ompati"i(ity, a !hi(d who is "(ood type / may ha'e a ea!tion i$ the mothe 1s "(ood type is O. KOO:LMCF