1
1.1
Symptoms and physical ndings usually become apparent during the rst or early during the second decade of
life. The average age of onset is nine years of age,[2] and
the majority of individuals experience symptoms before
20 years of age. The disease may progress for several
years before eventually going into remission (abruptly
ceasing).[2]
1.2 Neurological
Neurological abnormalities are common. Roughly 45%
of people with ParryRomberg syndrome are also aficted with trigeminal neuralgia (severe pain in the tissues supplied by the ipsilateral trigeminal nerve, including the forehead, eye, cheek, nose, mouth and jaw) and/or
migraine (severe headaches that may be accompanied by
An axial CT scan of a 17-year-old girl with ParryRomberg syn- visual abnormalities, nausea and vomiting).[6][7]
drome, showing severe loss of subcutaneous tissue and muscle of
the right side of the face, with no apparent involvement of the
facial bones
10% of aected individuals develop a seizure disorder as part of the disease.[6] The seizures are typically
Jacksonian in nature (characterized by rapid spasms of a
muscle group that subsequently spread to adjacent muscles) and occur on the side contralateral to the aected
side of the face.[2] Half of these cases are associated with
abnormalities in both the gray and white matter of the
HISTORY
4.2 Surgical
3
Charles Henry Parry (1779 1860).[15] It was described a
second time in 1846 by Moritz Heinrich Romberg (1795
1873) and Eduard Heinrich Henoch (1820 1910).[16]
German neurologist Albert Eulenburg (1840 1917) was
the rst to use the descriptive title progressive hemifacial
atrophy in 1871.[17][18][19]
In culture
Additional Images
A 3D, soft tissue reconstruction of a CT scan of a
17 year old girl with Parry Romberg syndrome.
CT scan3D bone reconstruction of a 17 year old girl
with Parry Romberg syndrome.
See also
Hemifacial microsomia
List of cutaneous conditions
Trigeminal trophic lesion
10
References
12
11
Further reading
12
External links
EXTERNAL LINKS
13
13.1
ParryRomberg syndrome Source: http://en.wikipedia.org/wiki/Parry%E2%80%93Romberg_syndrome?oldid=662087183 Contributors: Alison, DragonySixtyseven, Arcadian, GregorB, Rjwilmsi, AED, SmackBot, RDBrown, Fuhghettaboutit, Gveret Tered, Orderinchaos, Cydebot, Thijs!bot, Epbr123, Headbomb, WhatamIdoing, Thildebr3, CommonsDelinker, Gonzalo M. Garcia, Newtgrrl, My Core
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13.2
Images
File:Parry_Romberg_Syndrome_CT_scan.jpg Source:
http://upload.wikimedia.org/wikipedia/commons/d/d4/Parry_Romberg_
Syndrome_CT_scan.jpg License: CC BY-SA 3.0 Contributors: Own work Original artist: Desherinka
13.3
Content license