DAFTAR ISI.........................................................................................................................
BAB 1 PENDAHULUAN
1.1
Latar Belakang
......................................................................................
1.2
Rumusan Masalah.......................................................................................
1.3
Tujuan .........................................................................................................
1.4
Manfaat .......................................................................................................
Definisi.........................................................................................................
2.1.1 Talasemia..........................................................................................
2.1.2 Hemoglobin.......................................................................................
2.2 Epidemiologi.................................................................................................
2.3 Etiologi, Patogenesis dan Patofisiologi.........................................................
6
7
2.4 Klasifikasi Talasemia....................................................................................
2.4.1 Talasemia Alfa....................................................................................
2.4.2 Talasemia Beta..................................................................................
2.4.3 Talasemia Tranfusion Dependent.....................................................
2.4.4 Talasemia Non Tranfusion Dependent.............................................
2.5 Tanda dan Gejala Klinis..............................................................................
2.5.1 Talasemia Beta.................................................................................
2.5.2 Karier Talasemia Beta......................................................................
2.5.3 Homozigot Talasemia 0..................................................................
2.5.4 HbH disease (Talasemia /+).......................................................
2.5.5 Karier Talasemia Alfa.......................................................................
2.5.6 Karier Talasemia Alfa Silent.............................................................
2.6 Diagnosa Banding......................................................................................
2.7 Komplikasi..................................................................................................
2.8 Prognosis...................................................................................................
BAB 3 DIAGNOSIS DAN TATALAKSANA
3.1
Diagnosis ..................................................................................................
3.2
Tatalaksana................................................................................................
Kesimpulan................................................................................................
4.2
Saran.........................................................................................................
DAFTAR PUSTAKA.........................................................................................................