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D50D89 Diseases of the blood and blood-forming organs and

certain disorders involving the immune mechanism


(D50D53) Nutritional anemias

(D50) Iron deficiency anaemia

o (D50.0) Iron deficiency anaemia secondary to blood loss (chronic)

o (D50.1) Sideropenic dysphagia

Kelly-Paterson syndrome

Plummer-Vinson syndrome

o (D50.8) Other iron deficiency anaemias

o (D50.9) Iron deficiency anaemia, unspecified

(D51) Vitamin B12 deficiency anaemia

o (D51.0) Vitamin B12 deficiency anaemia due to intrinsic factor deficiency

Pernicious anemia

o (D51.1) Vitamin B 12 deficiency anaemia due to selective vitamin B 12 malabsorption with


proteinuria

Megaloblastic hereditary anaemia

o (D51.2) Transcobalamin II deficiency

o (D51.3) Other dietary vitamin B 12 deficiency anaemia

o (D51.8) Other vitamin B 12 deficiency anaemias

o (D51.9) Vitamin B 12 deficiency anaemia, unspecified

(D52) Folate deficiency anaemia

o (D52.0) Dietary folate deficiency anaemia

Nutritional megaloblastic anaemia

o (D52.1) Drug-induced folate deficiency anaemia

o (D52.8) Other folate deficiency anaemias

o (D52.9) Folate deficiency anaemia, unspecified

(D53) Other nutritional anaemias


o (D53.0) Protein deficiency anaemia

o (D53.1) Other megaloblastic anaemias, not elsewhere classified

o (D53.2) Scorbutic anaemia

o (D53.8) Other specified nutritional anaemias

o (D53.9) Nutritional anaemia, unspecified

(D55D59) Haemolytic anaemias

(D55) Anaemia due to enzyme disorders

o (D55.0) Anaemia due to glucose-6-phosphate dehydrogenase (G6PD) deficiency

Favism

G6PD deficiency anaemia

o (D55.1) Anaemia due to other disorders of glutathione metabolism

o (D55.2) Anaemia due to disorders of glycolytic enzymes

hexokinase deficiency

pyruvate kinase deficiency

triose-phosphate isomerase deficiency

o (D55.3) Anaemia due to disorders of nucleotide metabolism

o (D55.8) Other anaemias due to enzyme disorders

o (D55.9) Anaemia due to enzyme disorder, unspecified

(D56) Thalassaemia

o (D56.0) Alpha thalassaemia

o (D56.1) Beta thalassaemia

o (D56.2) Delta-beta thalassaemia

o (D56.3) Thalassaemia trait

o (D56.4) Hereditary persistence of fetal haemoglobin (HPFH)

o (D56.8) Other thalassaemias

o (D56.9) Thalassaemia, unspecified

(D57) Sickle-cell disorders


o (D57.0) Sickle-cell anaemia with crisis

o (D57.1) Sickle-cell anaemia without crisis

o (D57.2) Double heterozygous sickling disorders

o (D57.3) Sickle-cell trait

o (D57.8) Other sickle-cell disorders

(D58) Other hereditary haemolytic anaemias

o (D58.0) Hereditary spherocytosis

Acholuric (familial) jaundice

Congenital (spherocytic) haemolytic icterus

Minkowski-Chauffard syndrome

o (D58.1) Hereditary elliptocytosis

Elliptocytosis (congenital)

Ovalocytosis (congenital)(hereditary)

o (D58.2) Other haemoglobinopathies

Abnormal haemoglobin NOS

Congenital Heinz body anaemia

Haemoglobinopathy NOS

Unstable haemoglobin haemolytic disease

o (D58.8) Other specified hereditary haemolytic anaemias

Stomatocytosis

(D59) Acquired haemolytic anaemia

o (D59.0) Drug-induced autoimmune haemolytic anaemia

o (D59.1) Other autoimmune haemolytic anaemias

Warm autoimmune hemolytic anemia

o (D59.2) Drug-induce nonautoimmune haemolytic anaemia

o (D59.3) Haemolytic-uraemic syndrome

o (D59.4) Other nonautoimmune haemolytic anaemias


Microangiopathic hemolytic anemia

o (D59.5) Paroxysmal nocturnal haemoglobinuria (Marchiafava-Micheli)

o (D59.6) Haemoglobinuria due to haemolysis from other external causes

paroxysmal cold haemoglobinuria

o (D59.8) Other acquired haemolytic anaemias

o (D59.9) Acquired haemolytic anaemia, unspecified

(D60D64) Aplastic and other anaemias

(D60) Acquired pure red cell aplasia (erythroblastopenia)

(D61) Other aplastic anaemias

o (D61.0) Constitutional aplastic anaemia

Blackfan-Diamond syndrome

Familial hypoplastic anaemia

Fanconi's anaemia

Pancytopenia with malformations

o (D61.1) Drug-induced aplastic anaemia

o (D61.2) Aplastic anaemia due to other external agents

o (D61.3) Idiopathic aplastic anaemia

o (D61.8) Other specified aplastic anaemias

o (D61.9) Aplastic anaemia, unspecified

Hypoplastic anaemia NOS

Medullary hypoplasia

Panmyelophthisis

(D62) Acute posthaemorrhagic anaemia

(D63) Anaemia in chronic diseases classified elsewhere

(D64) Other anaemias

o (D64.0) Hereditary sideroblastic anaemia

o (D64.1) Secondary sideroblastic anaemia due to disease


o (D64.2) Secondary sideroblastic anaemia due to drugs and toxins

o (D64.3) Other sideroblastic anaemias

o (D64.4) Congenital dyserythropoietic anaemia

o (D64.8) Other specified anaemias

o (D64.9) Anaemia, unspecified

(D65D69) Coagulation defects, purpura and other haemorrhagic conditions

(D65) Disseminated intravascular coagulation (defibrination syndrome)

o Afibrinogenaemia, acquired

o Consumption coagulopathy

o Diffuse or disseminated intravascular coagulation (DIC)

o Fibrinolytic haemorrhage, acquired

o Fibrinolytic purpura

o Purpura fulminans

(D66) Hereditary factor VIII deficiency

o Haemophilia A

(D67) Hereditary factor IX deficiency

o Christmas disease

o Haemophilia B

(D68) Other coagulation defects

o (D68.0) Von Willebrand's disease

o (D68.1) Hereditary factor XI deficiency

Haemophilia C

o (D68.2) Hereditary deficiency of other clotting factors

o (D68.3) Haemorrhagic disorder due to circulating anticoagulants

o (D68.4) Acquired coagulation factor deficiency

o (D68.8) Other specified coagulation defects

o (D68.9) Coagulation defect, unspecified


(D69) Purpura and other haemorrhagic conditions

o (D69.0) Allergic purpura

anaphylactoid purpura

Henoch-Schnlein purpura

o (D69.1) Qualitative platelet defects

Bernard-Soulier syndrome (giant platelet)

Glanzmann's disease

Grey platelet syndrome

Thromboasthenia (haemorrhagic)(hereditary)

Thrombocytopathy

o (D69.2) Other nonthrombocytopenic purpura

o (D69.3) Idiopathic thrombocytopenic purpura

Evans' syndrome

o (D69.4) Other primary thrombocytopenia

o (D69.5) Secondary thrombocytopenia

o (D69.6) Thrombocytopenia, unspecified

o (D69.8) Other specified haemorrhagic conditions

o (D69.9) Haemorrhagic condition, unspecified

(D70D77) Other diseases of blood and blood-forming organs

(D70) Agranulocytosis

o Agranulocytic angina

o Infantile genetic agranulocytosis

o Kostmann's disease

o Neutropenia, NOS

(D71) Functional disorders of polymorphonuclear neutrophils


o Cell membrane receptor complex (CR3) defect

o Chronic (childhood) granulomatous disease

o Congenital dysphagocytosis

o Progressive septic granulomatosis

(D72) Other disorders of white blood cells

o (D72.0) Genetic anomalies of leukocytes

Alder anomaly

May-Hegglin anomaly

Pelger-Hut anomaly

o (D72.1) Eosinophilia

o (D72.8) Other specified disorders of white blood cells

Leukaemoid reaction: lymphocytic, monocytic, myelocytic

Leukocytosis

Lymphocytosis (symptomatic)

Lymphopenia

Monocytosis (symptomatic)

Plasmacytosis

o (D72.9) Disorder of white blood cells, unspecified

(D73) Diseases of spleen

o (D73.0) Hyposplenism

o (D73.1) Hypersplenism

o (D73.2) Chronic congestive splenomegaly

o (D73.3) Abscess of spleen

o (D73.4) Cyst of spleen

o (D73.5) Infarction of spleen

o (D73.8) Other diseases of spleen

o (D73.9) Disease of spleen, unspecified


(D74) Methaemoglobinaemia

o (D74.0) Congenital methaemoglobinaemia

Congenital NADH-methaemoglobin reductase deficiency

Haemoglobin-M (Hb-M) disease

Methaemoglobinaemia, hereditary

o (D74.8) Other methaemoglobinaemias

Acquired methaemoglobinaemia (with sulfhaemoglobinaemia)

Toxic methaemoglobinaemia

o (D74.9) Methaemoglobinaemia, unspecified

(D75) Other diseases of blood and blood-forming organs

o (D75.0) Familial erythrocytosis

o (D75.1) Secondary polycythaemia

o (D75.2) Essential thrombocytosis

o (D75.8) Other specified diseases of blood and blood-forming organs

Basophilia

o (D75.9) Disease of blood and blood-forming organs, unspecified

(D76) Certain diseases involving lymphoreticular tissue and reticulohistiocytic system

o (D76.0) Langerhans' cell histiocytosis, not elsewhere classified

Eosinophilic granuloma

Hand-Schller-Christian disease

Histiocytosis X (chronic)

o (D76.1) Haemophagocytic lymphohistiocytosis

Familial haemophagocytic reticulosis

o (D76.2) Haemophagocytic syndrome, infection-associated

o (D76.3) Other histiocytosis syndromes

Reticulohistiocytoma (giant-cell)

Sinus histiocytosis with massive lymphadenopathy


Xanthogranuloma

(D77) Other disorders of blood and blood-forming organs in diseases classified elsewhere

(D80D89) Certain disorders involving the immune mechanism

(D80) Immunodeficiency with predominantly antibody defects

o (D80.0) Hereditary hypogammaglobulinaemia

Autosomal recessive agammaglobulinaemia (Swiss type)

X-linked agammaglobulinaemia (Bruton) (with growth hormone deficiency)

o (D80.1) Nonfamilial hypogammaglobulinaemia

Agammaglobulinaemia with immunoglobulin-bearing B-lymphocytes

Common variable agammaglobulinaemia (CVAgamma)

Hypogammaglobulinaemia NOS

o (D80.2) Selective deficiency of immunoglobulin A (IgA)

o (D80.3) Selective deficiency of immunoglobulin G (IgG) subclasses

o (D80.4) Selective deficiency of immunoglobulin M (IgM)

o (D80.5) Immunodeficiency with increased immunoglobulin M (IgM)

o (D80.6) Antibody deficiency with near-normal immunoglobulins or with


hyperimmunoglobulinaemia

o (D80.7) Transient hypogammaglobulinaemia of infancy

o (D80.8) Other immunodeficiencies with predominantly antibody defects

Kappa light chain deficiency

o (D80.8) Immunodeficiency with predominantly antibody defects, unspecified

(D81) Combined immunodeficiencies

o (D81.0) Severe combined immunodeficiency (SCID) with reticular dysgenesis

o (D81.1) Severe combined immunodeficiency (SCID) with low T-cell and B-cell numbers

o (D81.2) Severe combined immunodeficiency (SCID) with low or normal B-cell numbers

o (D81.3) Adenosine deaminase deficiency (ADA)

o (D81.4) Nezelof's syndrome


o (D81.5) Purine nucleoside phosphorylase deficiency (PNP)

o (D81.6) Major histocompatibility complex class I deficiency

Bare lymphocyte syndrome

o (D81.7) Major histocompatibility complex class II deficiency

o (D81.8) Other combined immunodeficiencies

Biotin-dependent carboxylase deficiency

o (D81.9) Combined immunodeficiency, unspecified

Severe combined immunodeficiency disorder (SCID) NOS

(D82) Immunodeficiency associated with other major defects

o (D82.0) Wiskott-Aldrich syndrome

Immunodeficiency with thrombocytopenia and eczema

o (D82.1) Di George's syndrome

o (D82.2) Immunodeficiency with short-limbed stature

o (D82.3) Immunodeficiency following hereditary defective response to Epstein-Barr virus

X-linked lymphoproliferative disease

o (D82.4) Hyperimmunoglobulin E syndrome (IgE)

(D83) Common variable immunodeficiency

(D84) Other immunodeficiencies

o (D84.0) Lymphocyte function antigen-1 (LFA-1) defect

o (D84.1) Defects in the complement system

C1 esterase inhibitor deficiency (C1-INH)

o (D84.8) Other specified immunodeficiencies

o (D84.9) Immunodeficiency, unspecified

(D86) Sarcoidosis

o (D86.0) Sarcoidosis of lung

o (D86.1) Sarcoidosis of lymph nodes

o (D86.2) Sarcoidosis of lung with sarcoidosis of lymph nodes


o (D86.3) Sarcoidosis of skin

o (D86.8) Sarcoidosis of other and combined sites

(D89) Other disorders involving the immune mechanism, not elsewhere classified

o (D89.0) Polyclonal hypergammaglobulinaemia

Benign hypergammaglobulinaemic purpura

Polyclonal gammopathy NOS

o (D89.1) Cryoglobulinaemia

o (D89.2) Hypergammaglobulinaemia, unspecified

o (D89.8) Other specified disorders involving the immune mechanism, not elsewhere classified

o (D89.9) Disorder involving the immune mechanism, unspecified

See also
List of ICD-10 codes

International Statistical Classification of Diseases and Related Health Problems

List of ICD-9 codes 140239: neoplasms

References

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