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DEFINISI DEMAM
REFERAT ILEUS
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EVANS
SYNDROMEPENDAHUL
UAN
Pada tahun 1951,
Evans dan
rekannya
menjelaskan
sekelompok
pasien yangsecara
klinis ditandai
dengan imun
trombositopenia
dan autoimun
anemia
hemolitik (AIHA).
Anemia dan
trombositopenia
yang terjadi
bervariasi dalam
hal waktu
onsetdan durasi.
Terjadi remisi
spontan dan
eksaserbasi
umum, dan
beberapa
pasientersebut
mengalami
neutropenia.Evans
syndrome adalah
suatu kondisi yang
jarang ditandai
dengan
adanyakombinasi
imun
trobositopenia
(ITP) dan
autoimun
haemolytic
anemia baik
terjadibersamaan
atau sekuensial
dengan tes direk
antiglobulin (DAT)
positif tanpa
etiologiyang jelas.
Kondisi ini
biasanya
berlangsung
kronis dengan
karakteristik
terjadieksaserbasi
dan
remisi.Berdasarka
n review data
pasien dewasa
dengan
imunositopenia
dari tahun1950
samapi 1958
terdiri dari 369
kasus AIHA dan
367 kasus
trombositopeniah
anya 6 dari 766
pasien yang
menderita evans
syndrome. Tidak
ada predileksi seks
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