DAFTAR ISI

KATA PENGANTAR ............................................................................................ ii

DAFTAR ISI .......................................................................................................... iii

DAFTAR GAMBAR ............................................................................................. iv

DAFTAR TABEL ................................................................................................... v

BAB I PENDAHULUAN ....................................................................................... 1

BAB II TINJAUAN PUSTAKA

2.1 EPIDERMOLISIS BULOSA

2.1.1 Definisi ................................................................................................. 3

2.1.2 Epidemiologi ........................................................................................ 3

2.1.3 Klasifikasi ........................................................................................... 4

2.1.4.Pathogenesis ........................................................................................ 5

2.1.5 Gejala Klinis ......................................................................................... 6

2.1.6 Pemeriksaan penunjang ...................................................................... 14

2.1.7 Diagnosis ............................................................................................ 15

2.1.8 Diagnosis Banding .............................................................................. 16

2.1.9. Penatalaksanaan ................................................................................. 17

2.1.10. Komplikasi ...................................................................................... 20
2.1.11. Prognosis ........................................................................................ 20
2.1.12. Kesimpulan ..................................................................................... 21
DAFTAR PUSTAKA .......................................................................................... 22

ii
 DAFTAR GAMBAR

Gambar 2.1. Susunan skematis taut dermoepidermal ...................................... 5

Gambar 2.2. Epidermolisis bulosa simplex subtipe Weber-Cockayne ............ 7
Gambar 2.3. Papul hiperkeratosis dan plak pada telapak tangan EBS
Koebner ........................................................................................................... 8
Gambar 2.4. Epidermolisis Bulosa Simpleks Tipe Downling-Mera dan
Gambaran mikroskop elektronnya pada bayi 18 bulan .................................... 9
Gambar 2.5. Bayi dengan EBJ subtipe Herlitz .............................................. 10
Gambar 2.6. Gigi pasien dengan EBJ Generalized non-Herlitz .................... 11
Gambar 2.7. Polisindaktil pada pasien dengan EBD ..................................... 12
Gambar 2.8. Lengan penderita sindrom BART ............................................. 13
Gambar 2.9. Sindrom Kindler dengan poikiloderma (kiri) dan bula (kanan)
........................................................................................................................ 14

iii
 DAFTAR TABEL

Tabel 1. Kalsifikasi epidermolisis bulosa berdasarkan the third internasional

consensus meeting on diagnosis and clasification of epidermolisis bullosa

.................................................................................................................................4

iv