TUMORS
EPIDEMIOLOGI
SOFT TISSUE : NON EPITHELIAL TISSUES,
EXCEPT : BONE, CARTILAGINEOUS,
BRAIN & MENINGES,
HEMATOPOETIC CELL,
LYMPHOID
MOLECULAR ABNORMALITY
CITOGENETIC ABNORMALITIES
DISTRIBUTION
IT CAN OCCUR IN ANY SITE THROUGHOUT THE BODY
FIBROUS TUMORS
FIBROHISTIOCYTIC TUMORS
LIPOMATOUS TUMORS
SMOOTH MUSCLE TUMORS
SKELETAL MUSCLE TUMORS
TUMORS OF BLOOD AND LYMPH VESSEL
PERIVASCULAR TUMORS
SYNOVIAL TUMORS
NEURAL TUMORS
PARAGANGLIONIC TUMORS
EXTRASKELETAL CARTILAGINOUS AND OSSEUS TUMORS
PLURIPOTENTIAL MESENCHYMAL TUMORS
MISCELLANOUS TUMORS
UNCLASSIFIED TUMOR
FIBROUS TUMORS
FIBROSARCOMA
2 MAIN GROUPS : - THE ADULT TYPE
- INFANTILE TYPE
VERY UNCOMMON
ADULT FIBROSARCOMA : - 40 60 YEARS
- PAINFULL
- DEEP SEAT MASS
INFANTILE : 2 YEARS & OFTEN CONGENITAL
RECURREN AFTER EXCISION
HEMATOGEN METASTATIC PULMO
MORFOLOGY :
- SOLITER
- INFILTRATIF OR SIRCUMSCRIPTA
TUMORS OF FIBROUS ORIGIN
FIBROSARCOMA
Intermediate Tumors
Atypical fibroxanthoma
Dermatofibrosarcoma protuberans
Giant cell fibroblastoma
Flexiform fibrohistiocytic tumor
Angiomatoid fibrous histiocytoma
FIBROHISTIOSYTIC TUMORS
- SUB TYPE :
1. STORIFORM PLEOMORFIC : MOST COMMON
2. ANGIOMATOID : VASCULAR & TENDENCY YOUNGER
ADULT
3. INFLAMMATORIC
4. MIXOID
LIPOMATOUS TUMORS
Benign Tumors Intermediate Tumors
Lipoma Atypical lipoma
Cutaneous lipoma
Deep Lipoma Malignant Tumors
Multiple lipomas Liposarcoma
Angiolipoma
Spindle cell or pleomorphic
lipoma
Miolipoma
Angiomyolipoma
Chondroid lipoma
Hibernoma
Lipoblastoma or
lipoblastomatosis
Lipomatosis
LIPOMATOUS TUMORS
LIPOSARCOMA
LEIOMYOSARCOMA
MALIGNANT TUMOR
ANY LOCATION, MORE THAN HALF : RETROPERITONEAL OR
INTRAABDOMINAL SITES
CUTANEOUS LEIOMYOSARCOMAS : SMALL SOLITARY
EXTREMITY NODULES
RARE : ARISE IN LARGE VASCULAR STRUCTURE WITH
SYMPTOMS OF OBSTRUCTION TO THE NORMAL FLOW OF BLOOD
MORFOLOGY :
- TYPICAL CELL IS ELONGATED & HAS AN ABUNDANT CYTOPLASM
- MULTINUCLEATED GIANT CELLS
RHABDOMYOSARCOMA
Benign Tumors
Hemangioma
Malignant Tumors
Kaposis sarcoma
TUMORS OF BLOOD AND LYMPH VESSELS
KAPOSIS SARCOMA
T PRIMARY TUMOR
T0 NO EVIDENCE OF PRIMARY TUMOR
T1 TUMOR < 5 CM IN GREATEST DIMENSION
T1a SUPERFICIAL TUMOR
T1b DEEP TUMOR
T2 TUMOR > 5 CM IN GREATEST DIMENSION
T2a SUPERFICIAL TUMOR
T2b DEEP TUMOR
N REGIONAL LYMPH NODES
N0 NO REGIONAL LYMPH NODES METASTASIS
N1 REGIONAL LYMPH NODES METASTASIS
M DISTANT METASTASIS
M0 NO DISTANT METASTASIS
M1 DISTANT METASTASIS