Intestinal atresia :duodenal, jejunal & ileal Intestinal malrotation with volvulus Meconium ileus Neonatal necrotising enterocolitis(NNEC) Hirschprungs disease Anorectal malformations
MEDICAL CAUSES
NEONATAL SEPSIS MATERNAL HYPOTHYROIDISM MATERNAL DIABETES MELLITUS
EPILEPTIC DRUGS)
INTESTINAL ATRESIA
DUODENAL ATRESIA
25-50% of all intestinal atresias Complete stenosis of second part of duodenum at the
level of ampulla of vater Defective fusion of foregut and midgut with failure to recanalise lumen after solid phase of int. develop in 4th &5th weeks of gestation. Associated with downs syndrome & maternal polyhydramnios.
3 TYPES
MUCOSAL BLOCK
TIGHT BAND FIBROSAL
ladds band in case of malrotation Associated anomalies-malrotation, esophageal atresia,CHD, anorectal malformations
Clinical features
jaundice bilious vomiting dehydration growth retardation
Diagnosis:
BABYGRAM: double bubble sign with absence of air in the distal part
Duodenal atresia
TREATMENT
PRE OPERATIVE PREPRATION
correction of fluid & stabilising patient nasogastric or orogastric decompression evaluate for other congenital anomalies Surgical: duodenoduodenostomy Gastrotomy tube or transanastomotic nasojejunal tube for feeding is needed as prolonged post operative ileus is the usual problem
20% membraneous or mucousal atresia TYPE 2 35% fibrous atresia TYPE 3A 35% compelete single atresia TYPE 3B 5% compelete jejunal atresia with coiled ileum(APPLE PEAL) TYPE 4 5% Multiple segments of atresia
TREATMENT
ILEAL\JEJUNAL ATRESIA Stabilise & correct fluid electrolyte balance Prophylactic antibiotics Surgery: resection of dilated proximal bowel with end to end anastomosis In simple mucosal diaphragm- jejunoplasty or ileoplasty with partial excision of web
MECONIUM ILEUS
90% cases associated with cystic fibrosis Thick meconium get collected in
Clinical features
bilious vomiting
respiratory dysfunction high salt in the sweat Exocrine pancreatic insufficiency
Diagnosis:
Plain x ray- calcified meconium pellets with multiple air fluid levels which appear as soap bubbles (NEUHAUSER SIGN)
TREATMENT
In uncomplicated, hyperosmolar contrast media like
gastrografin wash out inspissated meconium Plug is releived by direct enteral irrigation with Nacetyl cysteine following enterotomy. In complicated cases: CHIMNEY ENTEROSTOMY BISHOP KOOP operation SANTULLI operation
SANTULLI OPERATION
Distal ileum is brought as ileostomy and proximal part is sutured to distal bowel
development
CLINICAL FEATURES
presents in 1st yr of life with acute or chronic
Diagnosis
Upper git contrast studies(malrotation),
Barium enema-
TREATMENT
Resuscitation & urgent surgery needed to untwist volvulus, Ladds procedure widen the base of small bowel mesentry, straighten duodenum and position the bowel in a non rotated position Appendicectomy to be done
NECROTISING ENTEROCOLITIS
NECROTISING ENTEROCOLITIS
Rapidly progressing extensive bowel necrosis,
infection & perforation. Common site is terminal ileum,caecum, ascending colon Etiology unknown Predisposing factors- prematurity & pulmonary disorders.
CLINICAL FEATURE
Abd distention
Bloody stools
TREATMENT
MEDICAL THERAPY:
BROAD SPECTRUM ANTIBIOTICS, NASOGASTRIC ASPIRATION