PF dan Anamnesis :
Anamnesis:
Keluhan mimisan yang susah berhenti, gusi sering berdarah, memar kulit, lemas, letih, lesu
(gejala anemia), BB turun. Belum pernah mengalami hal serupa, terdapat riwayat ibu
hemofilia.
terdapat perdarahan kulit dan mukosa (dapat berupa memar) = autosomal dominan
Hemartrosis (perdarahan persendian) dan perdarahan intramuskular = autosomal
resesif
varian X-linked recesive : tanpa gejala
Sinusitis berulang
Sakit kepala
diare kronis
PF
Vital Sign : hipertensi, takikardi
Jaundice
Ecchymoses
Oral Candidiasis
Oral hematoma
Asites
Pharingitis
Pneumonia
Lymphadenopati
Perdarahan pada saluran cerna dan epistaksis (75% pasien)
Menorrhagia
Ptekia (jarang terjadi)
Komplikasi : anemia, nyeri dan pembengkakan (bila perdarahan bersifat abnormal
pada jar. lunak atau persendian)
sumber :
Gurenlian, RDH, MS, PhD, AFAAOM, J., & M. Pierce, RDH, BS, J. (2015). Treating
Patients with Blood Clotting Disorder: Von Willebrand disease. Retrieved 8 May 2021,
from https://dimensionsofdentalhygiene.com/article/treating-patients-with-von-willebrand-
disease/
Echahdi, H., El Hasbaoui, B., El Khorassani, M., Agadr, A., & Khattab, M. (2017). Von
Willebrand's disease: case report and review of literature. The Pan African medical
journal, 27, 147. https://doi.org/10.11604/pamj.2017.27.147.12248
Winiati, E. (1993). Gejala Klinik dan Pemeriksaan Laboratorik Von Willebrand's. Jurnal
Kedokteran Gigi Universitas Indonesia, 1(1), 1-4. Retrieved from
http://www.jdentistry.ui.ac.id/index.php/JDI/article/view/929/830
Laffan, M. A., Lester, W., O'Donnell, J. S., Will, A., Tait, R. C., Goodeve, A., Millar, C. M.,
& Keeling, D. M. (2014). The diagnosis and management of von Willebrand disease: a
United Kingdom Haemophilia Centre Doctors Organization guideline approved by the
British Committee for Standards in Haematology. British journal of haematology, 167(4),
453–465. https://doi.org/10.1111/bjh.13064